Samiksha Jaiswal (Editor)

International Classification of Diseases for Oncology

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The International Classification of Diseases for Oncology (ICD-O) is a domain-specific extension of the International Statistical Classification of Diseases and Related Health Problems for tumor diseases. This classification is widely used by cancer registries.

Contents

It is currently in its third revision (ICD-O-3). ICD-10 includes a list of morphology codes. They stem from ICD-O second edition (ICD-O-2) that was valid at the time of publication.

Axes

The classification has two axes: topography and morphology.

Morphology

The morphology axis is for the shape and structure of the tumor.

This axis has particular importance because the Systematized Nomenclature of Medicine ("SNOMED") has adopted the ICD-O classification of morphology. SNOMED has been changing continuously, and several different versions of SNOMED are in use. Accordingly, mapping of ICD-O codes to SNOMED requires careful assessment of whether entities are indeed true matches.

Topography

The topography axis is for of the tumor's site in the body. It is standardized with the C section of ICD-10.

There were no changes in the topography axis between ICD-O-2 and ICD-O-3.

See List of ICD-10 codes#(C00–C97) Malignant Neoplasms for examples.

5th Digit Behaviour Code for Neoplasms

  • /0 Benign
  • /1 Uncertain whether benign or malignant
  • Borderline malignancy
  • Low malignant potential
  • Uncertain malignant potential
  • /2 Carcinoma in situ
  • Intraepithelial
  • Noninfiltrating
  • Noninvasive
  • /3 Malignant, primary site
  • /6 Malignant, metastatic site
  • Malignant, secondary site
  • /9 Malignant, uncertain whether primary or metastatic site
  • 800 Neoplasms, NOS

    M8000/0 Neoplasm, benign

  • Tumor, benign
  • Unclassified tumor, benign
  • M8000/1 Neoplasm, uncertain whether benign or malignant

  • Neoplasm, NOS
  • Tumor, NOS
  • Unclassified tumor, uncertain whether benign or malignant
  • Unclassified tumor, borderline malignancy
  • M8000/3 Neoplasm, malignant

  • Tumor, malignant, NOS
  • Malignancy
  • Cancer
  • Unclassified tumor, malignant
  • Blastoma, NOS
  • M8000/6 Neoplasm, metastatic

  • Neoplasm, metastatic
  • Tumor, metastatic
  • Tumor, secondary
  • Tumor embolus
  • M8000/9 Neoplasm, malignant, uncertain whether primary or metastatic

  • Unclassified tumor, malignant, uncertain whether primary or metastatic
  • M8001/0 Tumor cells, benign

    M8001/1 Tumor cells, uncertain whether benign or malignant

  • Tumor cells, NOS
  • M8001/3 Tumor cells, malignant

    M8002/3 Malignant tumor, small cell type

    M8003/3 Malignant tumor, giant cell type

    M8004/3 Malignant tumor, spindle cell type

  • Malignant tumor, fusiform cell type
  • M8005/0 Clear cell tumor, NOS

    M8005/3 Malignant tumor, clear cell type

    801–804 Epithelial Neoplasms, NOS

  • M8010/0 Epithelial tumor, benign
  • M8010/2 Carcinoma in situ, NOS
  • Intraepithelial carcinoma, NOS
  • M8010/3 Carcinoma, NOS
  • Epithelial tumor, malignant
  • M8010/6 Carcinoma, metastatic, NOS
  • Secondary carcinoma
  • M8010/9 Carcinomatosis
  • M8011/0 Epithelioma, benign
  • M8011/3 Epithelioma, malignant
  • Epithelioma, NOS
  • M8012/3 Large cell carcinoma, NOS
  • M8013/3 Large cell neuroendocrine carcinoma
  • M8014/3 Large cell carcinoma with rhabdoid phenotype
  • M8015/3 Glassy cell carcinoma
  • M8020/3 Carcinoma, undifferentiated, NOS
  • M8021/3 Carcinoma, anaplastic, NOS
  • M8022/3 Pleomorphic carcinoma
  • M8030/3 Giant cell and spindle cell carcinoma
  • M8031/3 Giant cell carcinoma
  • M8032/3 Spindle cell carcinoma, NOS
  • M8033/3 Pseudosarcomatous carcinoma
  • Sarcomatoid carcinoma
  • M8034/3 Polygonal cell carcinoma
  • M8035/3 Carcinoma with osteoclast-like giant cells
  • M8040/0 Tumorlet, benign
  • M8040/1 Tumorlet, NOS
  • M8041/3 Small cell carcinoma, NOS
  • Reserve cell carcinoma
  • Round cell carcinoma
  • Small cell neuroendocrine carcinoma
  • M8042/3 Oat cell carcinoma (C34._)
  • M8043/3 Small cell carcinoma, fusiform cell
  • M8044/3 Small cell carcinoma, intermediate cell
  • M8045/3 Combined small cell carcinoma
  • Mixed small cell carcinoma
  • Combined small cell-large cell carcinoma
  • Combined small cell-adenocarcinoma
  • Combined small cell-squamous cell carcinoma
  • M8046/3 Non-small cell carcinoma (C34._)
  • 805-808 Squamous Cell Neoplasms

  • M8050/0 Papilloma, NOS (except papilloma of bladder M8120/1)
  • M8050/2 Papillary carcinoma in situ
  • M8050/3 Papillary carcinoma, NOS
  • M8051/0 Verrucous papilloma
  • M8051/3 Verrucous carcinoma, NOS
  • Condylomatous carcinoma
  • Verrucous squamous cell carcinoma
  • Verrucous epidermoid carcinoma
  • Warty carcinoma
  • M8052/0 Squamous cell papilloma, NOS
  • Squamous papilloma
  • Keratotic papilloma
  • M8052/2 Papillary squamous cell carcinoma, non-invasive
  • Papillary squamous cell carcinoma in situ
  • M8052/3 Papillary squamous cell carcinoma
  • Papillary epidermoid carcinoma
  • M8053/0 Squamous cell papilloma, inverted
  • M8060/0 Squamous papillomatosis
  • Papillomatosis, NOS
  • M8070/2 Squamous cell carcinoma in situ, NOS
  • Epidermoid carcinoma in situ, NOS
  • Intraepidermal carcinoma, NOS
  • Intraepithelial squamous cell carcinoma
  • M8070/3 Squamous cell carcinoma, NOS
  • Epidermoid carcinoma, NOS
  • Squamous carcinoma
  • Squamous cell epithelioma
  • M8070/6 Squamous cell carcinoma, metastatic, NOS
  • M8071/3 Squamous cell carcinoma, keratinizing, NOS
  • Squamous cell carcinoma, large cell, keratinizing
  • Epidermoid carcinoma, keratinizing
  • M8072/3 Squamous cell carcinoma, large cell, nonkeratinizing, NOS
  • Squamous cell carcinoma, non keratinizing, NOS
  • Epidermoid carcinoma, large cell, nonkeratinizing
  • M8073/3 Squamous cell carcinoma, small cell, nonkeratinizing
  • Epidermoid carcinoma, small cell, nonkeratinizing
  • M8074/3 Squamous cell carcinoma, spindle cell
  • Epidermoid carcinoma, spindle cell
  • Squamous cell carcinoma, sarcomatoid
  • M8075/3 Squamous cell carcinoma, adenoid
  • Squamous cell carcinoma, pseudoglandular
  • Squamous cell carcinoma, acantholytic
  • M8076/2 Squamous cell carcinoma in situ with questionable stromal invasion
  • Epidermoid carcinoma in situ with questionable stromal invasion
  • M8076/3 Squamous cell carcinoma, microinvasive
  • M8077/2 Squamous intraepithelial neoplasia, grade III
  • Cervical intraepithelial neoplasia, grade III (C53._)
  • CIN III, NOS (C53._)
  • CIN III with severe dysplasia (C53._)
  • Vaginal intraepithelial neoplasia, grade III (C52._)
  • VAIN III (C52._)
  • Vulvar intraepithelial neoplasia, grade III (C51._)
  • VIN III (C51._)
  • Anal intraepithelial neoplasia, grade III (C21.1)
  • AIN III (C21.1)
  • M8078/3 Squamous cell carcinoma with horn formation
  • M8080/2 Queyrat erythroplasia (C60._)
  • M8081/2 Bowen disease (C44._)
  • Intraepidermal squamous cell carcinoma, Bowen type (C44._)
  • M8082/3 Lymphoepithelial carcinoma
  • Lymphoepithelioma
  • Lymphoepithelioma-like carcinoma
  • Schmincke tumor (C11._)
  • M8083/3 Basaloid squamous cell carcinoma
  • M8084/3 Squamous cell carcinoma, clear cell type
  • 809-811 Basal cell Neoplasms

  • M8090/1 Basal cell tumor (C44._)
  • (M8090/3) Basal cell carcinoma, NOS (C44._)
  • Basal cell epithelioma
  • Rodent ulcer
  • Pigmented basal cell carcinoma
  • M8091/3 Multifocal superficial basal cell carcinoma (C44._)
  • Multicentric basal cell carcinoma
  • M8092/3 Infriltrating basal cell carcinoma, NOS (C44._)
  • Infiltrating basal cell carcinoma, non-sclerosing
  • Infiltrating basal cell carcinoma, sclerosing
  • Basal cell carcinoma, morpheic
  • Basal cell carcinoma, desmoplastic type
  • M8093/3 Basal cell carcinoma, fibroepithelial (C44._)
  • Fibroepithelioma of Pinkus type
  • Fibroepithelial basal cell carcinoma, Pinkus type
  • Pinkus tumor
  • Fibroepithelioma, NOS
  • M8094/3 Basosquamous carcinoma (C44._)
  • Mixed basal-squamous cell carcinoma
  • M8095/3 Metatypical carcinoma
  • M8096/0 Intraepidermal epithelioma of Jadassohn (C44._)
  • M8097/3 Basal cell carcinoma, nodular (C44._)
  • Basal cell carcinoma, micronodular
  • M8098/3 Adenoid basal carcinoma (C53._)
  • M8100/0 Trichoepithelioma (C44._)
  • Brooke tumor
  • Epithelioma adenoides cysticum
  • M8101/0 Trichofolliculoma (C44._)
  • M8102/0 Trichilemmoma (C44._)
  • M8102/3 Trichilemmocarcinoma (C44._)
  • Trichilemmal carcinoma
  • M8103/0 Pilar tumor (C44._)
  • Proliferating trichilemmal cyst
  • Proliferating trichilemmal tumor
  • M8110/0 Pilomatrixoma, NOS (C44._)
  • Calcifying epithelioma of Malherbe
  • Pilomatricoma, NOS
  • M8110/3 Pilomatrix carcinoma (C44._)
  • Pilomatrixoma, malignant
  • Pilomatricoma, malignant
  • Matrical carcinoma
  • 812-813 Transitional cell Papillomas And Carcinomas

  • M8120/0 Transitional cell papilloma, benign
  • Transitional papilloma
  • M8120/1 Urothelial papilloma, NOS
  • Papilloma of baldder (C67._)
  • Transitional cell papilloma, NOS
  • M8120/2 Transitional cell carcinoma in situ
  • Urothelial carcinoma in situ
  • M8120/3 Transitional cell carcinoma, NOS
  • Urothelial carcinoma, NOS
  • Transitional carcinoma
  • M8121/0 Schneiderian papilloma, NOS (C30.0, C31._)
  • Sinonasal papilloma, NOS
  • Sinonasal papilloma, exophytic
  • Sinonasal papilloma, fungiform
  • Transitional cell papilloma, inverted, benign
  • Transitional papilloma, inverted, benign
  • M8121/1 Transitional cell papilloma, inverted, NOS
  • Transitional papilloma, inverted, NOS
  • Schneiderian papilloma, inverted
  • Columnar cell papilloma
  • Cylindrical cell papilloma
  • Oncocytic Schneiderian papilloma
  • M8121/3 Schneiderian carcinoma (C30.0, C31._)
  • Cylindrical cell carcinoma
  • M8122/3 Transitional cell carcinoma, spindle cell
  • Transitional cell carcinoma, sarcomatoid
  • M8123/3 Basaloid carcinoma
  • M8124/3 Cloacogenic carcinoma (C21.2)
  • M8130/1 Papillary transitional cell neoplasm of low malignant potential (C67._)
  • Papillary urothelial neoplasm of low malignant potential
  • M8130/2 Papillary transitional cell carcinoma, non-invasive (C67._)
  • Papillary urothelial carcinoma, non-invasive
  • M8130/3 Papillary transitional cell carcinoma (C67._)
  • Papillary urothelial carcinoma
  • M8131/3 Transitional cell carcinoma, micropapillary ( C67._)
  • 814–838 Adenomas And Adenocarcinomas

  • (M8140/0) Adenoma, NOS
  • M8140/1 Atypical adenoma
  • Bronchial adenoma, NOS (C34._)
  • M8140/2 Adenocarcinoma in situ, NOS
  • (M8140/3) Adenocarcinoma, NOS
  • M8140/6 Adenocarcinoma, metastatic, NOS
  • M8141/3 Scirrhous adenocarcinoma
  • Scirrhous carcinoma
  • Carcinoma with productive fibrosis
  • (M8142/3) Linitis plastica (C16._)
  • M8143/3 Superficial spreading adenocarcinoma
  • M8144/3 Adenocarcinoma, intestinal type (C16._)
  • Carcinoma, intestinal type
  • M8145/3 Carcinoma, diffuse type (C16._)
  • Adenocarcinoma, diffuse type
  • M8146/0 Monomorphic adenoma
  • M8147/0 Basal cell adenoma
  • M8147/3 Basal cell adenocarcinoma
  • M8148/2 Glandular intraepithelial neoplasia, grade III
  • Prostatic intraepithelial neoplasia, grade III (C61.9)
  • PIN III
  • M8149/0 Canalicular adenoma
  • M8150/0 Islet cell adenoma (C25._)
  • Islet cell tumor, benign
  • Nesidioblastoma
  • Islet cell adeomatosis
  • M8150/1 Islet cell tumor, NOS (C25._)
  • M8150/3 Islet cell carcinoma (C25._)
  • Islet cell adenocarcinoma
  • (M8151/0) Insulinoma, NOS (C25._)
  • Beta cell adenoma
  • M8151/3 Insulinoma, malignant (C25._)
  • Beta cell tumor, malginant
  • (M8152/0) Glucagonoma, NOS (C25._)
  • Alpha cell tumor, NOS
  • M8152/3 Glucagonoma, malignant (C25._)
  • Alpha cell tumor, malignant
  • (M8153/1) Gastrinoma, NOS
  • G cell tumor, NOS
  • Gastrin cell tumor
  • M8153/3 Gastinoma, malignant
  • G cell tumor, malignant
  • Gastrin cell tumor, malignant
  • M8154/3 Mixed islet cell and exocrine adenocarcinoma (C25._)
  • Mixed acinar-endocrine carcinoma
  • Mixed ductal-endocrine carcinoma
  • M8155/1 Vipoma, NOS
  • (M8155/3) Vipoma, malignant
  • M8156/1 Somatostatinoma, NOS
  • Somatostatin cell tumor, NOS
  • M8156/3 Somatostatinoma, malignant
  • somatostatin cell tumor, malignant
  • M8157/1 Enteroglucagonoma, NOS
  • M8157/3 Enteroglucagonoma, malignant
  • M8160/0 Bile duct adenoma (C22.1, C24.0)
  • Cholangioma
  • (M8160/3) Cholangiocarcinoma (C22.1, C24.0)
  • Bile duct carcinoma
  • Bile duct adenocarcinoma
  • M8161/0 (C22.1, C24.0)
  • M8161/3 Bile duct cystadenocarcinoma (C22.1, C24.0)
  • M8162/3 Klatskin tumor (C22.1, C24.0)
  • M8170/0 Liver cell adenoma (C22.0)
  • (M8170/3) Hepatocellular carcinoma, NOS (C22.0)
  • Liver cell carcinoma
  • Hepatocarcinoma
  • Hepatoma, malignant
  • Hepatoma, NOS
  • M8171/3 Hepatocellular carcinoma, fibrolamellar (C22.0)
  • M8172/3 Hepatocellular carcinoma, scirrhous (C22.0)
  • Sclerosing hepatic carcinoma
  • M8173/3 Hepatocellular carcinoma, spindle cell variant (C22.0)
  • Hepatocellular carcinoma, sarcomatoid
  • M8174/3 Hepatocellular carcinoma, clear cell type (C22.0)
  • M8175/3 Hepatocellular carcinoma, pleomorphic type
  • M8180/3 Combined hepatocellular carcinoma and cholangiocarcinoma (C22.0)
  • Mixed hepatocellular and bilde duct carcinoma
  • Hepatocholangiocarcinoma
  • M8190/0 Trabecular adenoma
  • M8190/3 Trabecular adenocarcinoma
  • Trabecular carcinoma
  • M8191/0 Embryonal adenoma
  • M8200/0 Eccrine dermal cylindroma (C44._)
  • Turban tumor
  • Cylindroma of skin
  • (M8200/3) Adenoid cystic carcinoma
  • Adenocystic carcinoma
  • Cylindroma, NOS (except cylindroma of skin M8200/0)
  • Adenocarcinoma, cylindroid
  • Bronchial adenoma, cylindroid (C34._)
  • M8201/2 Cribiform carcinoma in situ (C50._)
  • Ductal carcinoma in situ, cribiform type
  • M8201/3 Cribiform carcinoma, NOS
  • Ductal carcinoma, cribiform type
  • M8202/0 Microcystic adenoma (C25._)
  • M8204/0 Lactating adenoma
  • M8210/0 Adenomatous polyp, NOS
  • Polypoid adenoma
  • M8210/2 Adenocarcinoma in situ in adenomatous polyp
  • Adenocarcinoma in situ in tublar adenoma
  • Carcinoma in situ in adeomatous polyp
  • Adenocarcinoma in situ in polypoid adenoma
  • Adenocarcinoma in situ in a polyp, NOS
  • Carcinoma in situ in a polyp, NOS
  • M8210/3 Adenocarcinoma in adeonmatous polyp
  • Adenocarcinoma in tubular adenoma
  • Carcinoma in adeomatous polyp
  • Adenocarcinoma in polypoid adenoma
  • Adenocarcinoma in a polyp, NOS
  • Carcinoma in a polyp, NOS
  • M8211/0 Tubular adenoma, NOS
  • M8211/3 Tubular adenocarcinoma
  • Tubular carcinoma
  • M8212/0 Flat adenoma
  • M8213/0 Serrated adenoma (C18._)
  • Mixed adenomatous and hyperplastic polyp
  • M8214/3 Parietal cell carcinoma (C16._)
  • Parietal cell adenocarcinoma
  • M8215/3 Adenocarcinoma of anal glands (C21.1)
  • Adenocarcinoma of anal ducts
  • M8220/0 Adenomatous polyposis coli (C18._)
  • Familial polyposis coli
  • Adenomatosis, NOS
  • M8220/3 Adenocarcinoma in adenomatous polyposis
  • M8221/0 Multiple adenomatous polyps
  • M8221/3 Adenocarcinoma in multiple adenomatous polyps
  • M8230/2 Ductal carcinoma in situ, solid type (C50._)
  • Intraductal carcinoma, solid type
  • M8230/3 Solid carcinoma, NOS
  • Solid carcinoma with mucin formation
  • Solid adenocarcinoma with mucin formation
  • M8231/3 Carcinoma simplex
  • (M8240/1) Carcinoid tumor of uncertain malignant potential
  • Carcinoid tumor, NOS, of appendix (C18.1)
  • Carcinoid, NOS, of appendix
  • Carcinoid tumor, argentaffin, NOS
  • Argentaffinoma, NOS
  • M8240/3 Carcinoid tumor, NOS (except of appendix M8240/1)
  • Carcinoid, NOS (except of appendix)
  • Typical carcinoid
  • Bronchial adenoma, carcinoid
  • M8241/3 Enterochromaffin cell carcinoid
  • Carcinoid tumor, argentaffin, malignant
  • Argentaffinoma, malignant
  • EC cell carcinoid
  • Serotonin producing carcinoid
  • M8242/1 Enterochromaffin-like cell carcinoid, NOS
  • ECL cell carcinoid, NOS
  • M8242/3 Enterochromaffin-like cell tumor, malignant
  • ECL cell carcinoid, malignant
  • M8243/3 Goblet cell carcinoid
  • Mucocarcinoid tumor
  • Mucinous carcinoid
  • M8244/3 Composite carcinoid
  • Combined carcinoid and adenocarcinoma
  • Mixed carcinoid-adenocarcinoma
  • M8245/1 Tubular carcinoid
  • M8245/3 Adenocarcinoid tumor
  • M8246/3 Neuroendocrine carcinoma, NOS
  • M8247/3 Merkel cell carcinoma (C44._)
  • Merkel cell tumor
  • Primary cutaneous neuroendocrine carcinoma
  • M8248/1 Apudoma
  • M8249/3 Atypical carcinoid tumor
  • M8250/1 Pulmonary adenomatosis (C34._)
  • M8250/3 Bronchiolo-alveolar adenocarcinoma, NOS (C34._)
  • Bronchiolo-alveolar carcinoma, NOS
  • Bronchiolar adenocarcinoma
  • Bronchiolar carcinoma
  • Alveolar cell carcinoma
  • M8251/0 Alveolar adenoma (C34._)
  • M8251/3 Alveolar adenocarcinoma (C34._)
  • Alveolar carcinoma
  • M8252/3 Bronchiolo-alveolar carcinoma, non-mucinous (C34._)
  • Bronchiolo-alveolar carcinoma, Clara cell
  • Bronchiolo-alveolar carcinoma, type II pneumocyte
  • M8253/3 Bronchiolo-alveolar carcinoma, mucinous (C32._)
  • Bronchiolo-alveolar carcinoma, goblet cell type
  • M8254/3 Bronchiolo-alveolar carcinoma, mixed mucinous and non-mucinous (C34._)
  • Bronchiolo-alveolar carcinoma, Clara cell and goblet cell type
  • Bronchiolo-alveolar carcinoma, type II pneumocyte and goblet cell type
  • Bronchiolo-alveolar carcinoma, indeterminate type
  • M8255/3 Adenocarcinoma combined with mixed subtypes
  • Adenomcarcinoma combined with other types of carcinoma
  • M8260/0 Papillary adenoma, NOS
  • Glandular papilloma
  • M8260/3 Papillary adenocarcinoma, NOS
  • Papillary carcinoma of thyroid (C73.9)
  • Papillary renal cell carcinoma (C64.9)
  • M8261/0 Villous adenoma, NOS
  • Villous papilloma
  • M8261/2 Adenocarcinoma in situ in villous adenoma
  • M8261/3 Adenocarcinoma in villous adenoma
  • M8262/3 Villous adenocarcinoma
  • M8263/0 Tubulovillous adenoma, NOS
  • villoglandular adenoma
  • Papillotubular adenoma
  • M8263/2 Adenocarcinoma in situ in tubulovillous adenoma
  • M8263/3 Adenocarcinoma in tubulovillous adenoma
  • Papillotubular adenocarcinoma
  • Tubulopapillary adenocarcinoma
  • M8264/0 Papillomatosis, glandular
  • Biliary papillomatosis (C22.1, C24.0)
  • M8270/0 Chromophobe adenoma (C75.1)
  • M8270/3 Chromophobe carcinoma (C75.1)
  • Chromophobe adenocarcinoma
  • (M8271/0) Prolactinoma (C75.1)
  • M8272/0 Pituitary adenoma, NOS (C75.1)
  • M8272/3 Pituitary carcinoma, NOS (C75.1)
  • M8280/0 Acidophil adenoma (C75.1)
  • Eosinophil adenoma
  • M8280/3 Acidophil carcinoma (C75.1)
  • Acidophil adenocarcinoma
  • Eosinophil carcinoma
  • Eosinophil adenocarcinoma
  • M8281/0 Mixed acidophil-basophil adenoma (C75.1)
  • (M8290/0) Oxyphilic adenoma
  • Oncocytic adenoma
  • Oncocytoma
  • Hurthle cell adenoma(C73.9)
  • Hurthle cell tumor
  • Follicular adenoma, oxyphilic cell (C73.9)
  • M8290/3 Oxyphilic adenocarcinoma
  • Oncocytic carcinoma
  • Oncocytic adenocarcinoma
  • Hurthlecell carcinoma (C73.9)
  • Hurthle cell adenocarcinoma
  • Follicular carcinoma, oxyphilic cell (C73.9)
  • M8300/0 Basophil adenoma (C75.1)
  • Mucoid cell adenoma
  • M8300/3 Basophil carcinoma (C75.1)
  • Basophil adenocarcinoma
  • Mucoid cell adenocarcinoma
  • M8310/0 Clear cell adenoma
  • M8310/3 Clear cell adenocarcinoma, NOS
  • Clear cell carcinoma
  • Clear cell adenocarcinoma, mesonephroid
  • M8311/1 Hypernephroid tumor
  • (M8312/3) Renal cell carcinoma, NOS (C64.9)
  • Renal cell adenocarcinoma
  • Grawitz tumor
  • Hypernephroma
  • M8313/0 Clear cell adenofibroma (C56.9)
  • clear cell cystadenofibroma
  • M8313/1 Clear cell adenofibroma of borderline malignancy
  • Clear cell cystadenofibroma of borderline malignancy
  • M8313/3 Clear cell adenocarcinofibroma (C56.9)
  • Clear cell cystadenocarcinofibroma
  • M8314/3 Lipid-rich carcinoma (C50._)
  • M8315/3 Glycogen-rich carcinoma
  • M8316/3 Cyst-associated renal cell carcinoma (C64.9)
  • M8317/3 Renal cell carcinoma, chromophobe type (C64.9)
  • Chromophobe cell renal carcinoma
  • M8318/3 Renal cell carcinoma, sarcomatoid (C64.9)
  • Renal cell carcinoma, spindle cell
  • M8319/3 collecting duct carcinoma (C64.9)
  • Bellini duct carcinoma
  • Renal carcinoma, collecting duct type
  • M8320/3 Granular cell carcinoma
  • Granular cell adenocarcinoma
  • M8321/0 Chief cell adenoma (C75.0)
  • M8322/0 Water-clear cell adenoma (C75.0)
  • M8322/3 Water-clear cell adenocarcinoma (C75.0)
  • Water-celar cell carcinoma
  • M8323/0 Mixed cell adenoma
  • M8323/3 Mixed cell adenocarcinoma
  • M8324/0 Lipoadenoma
  • Adenolipoma
  • M8325/0 Metanephric adenoma (C64.9)
  • M8330/0 Follicular adenoma (C73.9)
  • M8330/1 Atypical follicular adenoma (C73.9)
  • M8330/3 Follicular adenocarcinoma, NOS (C73.9)
  • Follicular carcinoma, NOS
  • M8331/3 Follicular adenocarcinoma, well differentiated (C73.9)
  • Follicular carcinoma, well differentiated
  • M8332/3 Follicular adenocarcinoma, trabecular (C73.9)
  • Follicular carcinoma, trabecular
  • Follicular adenocarcinoma, moderately differentiated
  • FOlloicular carcinoma, moderatedly differentiated
  • M8333/0 Microfollicular adenoma, NOS (C73.9)
  • Fetal adenoma
  • M8333/3 Fetal adenocarcinoma
  • M8334/0 Macrofollicular adenoma (C73.9)
  • Colloid adenoma
  • M8335/3 Follicular carcinoma, minimally invasive (C73.9)
  • Follicular carcinoma, encapsulated
  • M8336/0 Hyalinizing trabecular adenoma (C73.9)
  • (M8337/3)Insular carcinoma (C73.9)
  • M8340/3 Papillary carcinoma, follicular variant (C73.9)
  • Papillary adenocarcinoma, follicular variant
  • Papillary and follicular adenocarcinoma
  • Papillary and follicular carcinoma
  • M8341/3 Papillary microcarcinoma (C73.9)
  • M8342/3 Papillary carcinoma, oxyphilic cell (C73.9)
  • M8343/3 Papillary carcinoma, encapsulated (C73.9)
  • M8344/3 Papillary carcinoma, columnar cell (C73.9)
  • Papillary carcinoma, tall cell
  • M8345/3 Medullary carcinoma with amyloid stroma (C73.9)
  • Parafollicular cell carcinoma
  • C cell carcinoma
  • M8346/3 Mixed medullary-follicular carcinoma (C73.9)
  • M8347/3 Mixed medullary-papillary carcinoma (C73.9)
  • M8350/3 Nonencapsulated sclerosing carcinoma (c73.9)
  • Nonencapsulated sclerosing adenocarcinoma
  • Nonencapsulated sclerosing tumor
  • Papillary carcinoma, diffuse sclerosing
  • M8360/1 Multiple endocrine adenomas
  • Endocrine adenomatosis
  • M8361/0 Juxtaglomerular tumor (C64.9)
  • Reninoma
  • M8370/0 Adrenal cortical adenoma, NOS (C74.0)
  • Adrenal cortical tumor, benign
  • Adrenal cortical tumor, NOS
  • M8370/3 Adrenal cortical carcinoma (C74.0)
  • Adrenal cortical adenocarcinoma
  • Adrenal cortical tumor, malignant
  • M8371/0 Adrenal cortical adenoma, compact cell (C74.0)
  • M8372/0 Adrenal cortical adenoma, pigmented (C74.0)
  • Black adenoma
  • Pigmented adenoma
  • M8373/0 Adrenal cortical adenoma, clear cell (C74.0)
  • M8374/0 Adrenal cortical adenoma, glomerulosa cell (C74.0)
  • M8375/0 Adrenal cortical adenoma, mixed cell (C74.0)
  • (M8380/0) Endometrioid adenoma, NOS
  • Endometrioid cystadenoma, NOS
  • M8380/1 Endometrioid adenoma, borderline malignancy
  • Endometrioid cystadenoma, borderline malignancy
  • Endometrioid tumor of low malignant potential
  • Atypical proliferative endometrioid tumor
  • M8380/3 Endometrioid adenocarcinoma, NOS
  • Endometrioid carcinoma, NOS
  • Endometrioid cystadenocarcinoma
  • M8381/0 Endometrioid adenofibroma, NOS
  • Endometrioid cystadenofibroma, NOS
  • M8381/1 Endometrioid adenofibroma, borderline malignancy
  • Endometrioid cystadenofibroma, borderline malignancy
  • M8381/3 Endometriod adenofibroma, malignant
  • Endometrioid cystadenofibroma, malignant
  • M8382/3 Endometrioid adenocarcinoma, secretory variant
  • M8383/3 Endometrioid adenocarcinoma, ciliated cell variant
  • M8384/3 Adenocarcinoma, endocervical type
  • 839–842 Adnexal And Skin appendage Neoplasms

    M8390/0 Skin appendage adenoma (C44._)

  • Skin appendage tumor, benign
  • Adnexal tumor, benign
  • M8390/3 Skin appendage carcinoma (C44._)

  • Adnexal carcinoma
  • M8391/0 Follicular fibroma (C44._)

  • Trichodiscoma
  • Fibrofolliculoma
  • Perifollicular fibroma
  • M8392/0 Syringofibroadenoma (C44._)

    M8400/0 Sweat gland adenoma (C44._)

  • Sweat gland tumor, benign
  • Hidradenoma, NOS
  • Syringadenoma, NOS
  • M8400/1 Sweat gland tumor, NOS (C44._)

    M8400/3 Sweat gland adenocarcinoma (C44._)

  • Sweat gland carcinoma
  • Sweat gland tumor, malignant
  • M8401/0 Apocrine adenoma

  • Apocrine cystadenoma
  • M8401/3 Apocrine adenocarcinoma

    M8402/0 Nodular hidradenoma (C44._)

  • Eccrine acrospiroma
  • Clear cell hidradenoma
  • M8402/3 Nodular hidradenoma, malignant (C44._)

  • Hidradenocarcinoma
  • M8403/0 Eccrine spiradenoma (C44._)

  • Spiradenoma, NOS
  • M8403/3 Malignant eccrine spiradenoma (C44._) M8404/0 Hidrocystoma (C44._)

  • Eccrine cystadenoma
  • M8405/0 Papillary hidradenoma

  • Hidradenoma papilliferum
  • M8406/0 Papillary syringadenoma (C44._)

  • Papillary syringocystadenoma
  • Syringocystadenoma papilliferum
  • M8407/0 Syringoma, NOS (C44._)

    M8407/3 Sclerosing sweat duct carcinoma (C44._)

  • Syringomatous carcinoma
  • Microcystic adnexal carcinoma
  • M8408/0 Eccrine papillary adenoma (C44._)

    M8408/1 Aggressive digital papillary adenoma (C44._)

    M8408/3 Eccrine papillary adenocarcinoma (C44._)

  • Digital papillary adenocarcinoma
  • M8409/0 Eccrine poroma (C44._)

    M8410/0 Sebaceous adnoma (C44._)

    M8410/3 Sebaceous adenocarcinoma (C44._)

  • Sebaceous carcinoma
  • M8413/3 Eccrine adenocarcinoma (C44._)

    M8420/0 Ceruminous adenoma (C44.2)

    M8420/3 Ceruminous adenocarcinioma (C44.2)

  • Ceruminous carcinoma
  • 843 Mucoepidermoid Neoplasms

    M8430/1 Mucoepidermoid tumor

    M8430/3 Mucoepidermoid carcinoma

    844–849 Cystic, Mucinous And Serous Neoplasms

    M8440/0 Cystadenoma, NOS

  • Cystoma, NOS
  • M8440/3 Cystadenocarcinoma, NOS

    M8441/0 Serous cystadenoma, NOS

  • Serous cystoma
  • Serous microcystic adenoma
  • M8441/3 Serous cystadenocarcinoma, NOS (C56.9)

  • Serous adenocarcinoma, NOS
  • Serous carcinoma, NOS
  • M8442/1 Serous cystadenoma, borderline malignancy (C56.9)

  • Serous tumor, NOS, of low malignant potential
  • Atypical proliferating serous tumor
  • M8443/0 Clear cell cystadenoma (C56.9)

    M8444/1 Clear cell cystic tumor of borderline malignancy (C56.9)

  • Atypical proliferating clear cell tumor
  • M8450/0 Papillary cystadenoma, NOS (C56.9)

    M8450/3 Papillary cystadenocarcinoma, NOS (C56.9)

  • Papillocystic adenocarcinoma
  • M8451/1 Papillary cystadenoma, borderline malignancy (C56.9)

    M8452/1 Solid pseudo papillary tumor (C25._)

  • Papillary cystic tumor
  • Solid and papillary epithelial neoplasm
  • Solid and cystic tumor
  • M8452/3 Solid pseudopapillary carcinoma (C25._)

    M8453/0 Intraductal papillary-mucinous adenoma (C25._)

    M8453/1 Intraductal papillary-mucinous tumor with moderate dysplasia (C25._)

    M8453/2 Intraductal papillary-mucinous carcinoma, non-invasive (C25._)

    M8453/3 Intraductal papillary-mucinous carcinoma invasive (C25._)

    M8454/0 Cystic tumor of atrio-ventricular node (C38.0)

    M8460/0 Papillary serous cystadenoma, NOS (C56.9)

    M8460/3 Papillary serous cystadenocarcinoma (C56.9)

  • Papillary serous adenocarcinoma
  • Micropapillary serous carcinoma
  • M8461/0 Serous surface papilloma (C56.9)

    M8461/3 Serous surface papillary carcinoma (C56.9)

  • Primary serous papillary carcinoma of peritoneum (C48.1)
  • M8462/1 Serous papillary cystic tumor of borderline malignancy (C56.9)

  • Papillary serous cystadenoma, borderline malignancy
  • Papillary serous tumor of low malignant potential
  • Atypical proliferative papillary serous tumor
  • M8463/1 Serous surface papillary tumor of borderline malignancy (C56.9)

    M8470/0 Mucinous cystadenoma, NOS (C56.9)

  • Mucinous cystoma
  • Pseudomucinous cystadenoma, NOS
  • M8470/1 Mucinous cystic tumor with moderate dysplasia (C25._)

    M8470/2 Mucinous cystadenocarcinoma, non-invasive (C25._)

    M8470/3 Mucinous cystadenocarcinoma/ NOS (C56.9)

  • Pseudomucinous adenocarcinoma
  • Pseudomucinous cystadenocarcinoma, NOS
  • M8471/0 Papillary mucinous cystadenoma, NOS (C56.9)

  • Papillary pseudomucinous cystadenoma, NOS
  • M8471/3 papillary mucinous cystadenocarcinoma (C56.9)

  • Papillary pseudomucinous cystadenocarcinoma
  • M8472/1 Mucinous cystic tumor of borderline malignancy (C56.9)

  • Mucinous cystadenoma, borderline malignancy
  • Pseudomucinous cystadenoma, borderline malignancy
  • Mucinous tumor, NOS, of low malignant potential
  • Atypical proliferative mucinous tumor
  • M8473/1 Papillary mucinous cystadenoma, borderline malignancy (C56.9)

  • Papillary pseudomucinous cystadenoma borderline malignancy
  • Papillary mucinous tumor of low malignant potential
  • M8480/0 Mucinous adenoma

    M8480/3 Mucinous adenocarcinoma

  • Mucinous carcinoma
  • Colloid adenocarcinoma
  • Colloid carcinoma
  • Gelatinous adenocarcinoma
  • Gelatinous carcinoma
  • Mucoid adenocarcinoma
  • Mucoid carcinoma
  • Mucous adenocarcinoma
  • Mucous carcinoma
  • Pseudomyxoma peritonei with unknown primary site (C80.9)
  • M8480/6 Pseudomyxoma peritonei

    M8481/3 Mucin-producing adenocarcinoma

  • Mucin-producing carcinoma
  • Mucin-secreting adenocarcinoma
  • Mucin-secreting carcinoma
  • M8482/3 Mucinous adenocarcinoma, endocervical type

    M8490/3 Signet ring cell carcinoma

  • Signet ring cell adenocarcinoma
  • M8490/6 Metastatic signet ring cell carcinoma

  • Krukenberg tumor
  • 850–854 Ductal, Lobular And Medullary Neoplasms

    M8500/2 Intraductal carcinoma, noninfiltrating, NOS

  • Intraductal adenocarcinoma, noninfiltrating, NOS
  • Intraductal carcinoma, NOS
  • Ductal carcinoma in situ, NOS (C50._)
  • DCIS, NOS
  • Ductal intraepithelial neoplasia 3
  • DIN 3
  • M8500/3 Infiltrating duct carcinoma, NOS (C50._)

  • Infiltrating duct adenocarcinoma
  • Duct adenocarcinoma, NOS
  • Duct carcinoma, NOS
  • Duct cell carcinoma
  • Ductal carcinoma, NOS
  • M8501/2 Comedocarcinoma, noninfiltrating (C50._)

  • Ductal carcinoma in situ, comedo type
  • DCIS, comedo type
  • M8501/3 Comedocarcinoma, NOS (C50._)

    M8502/3 Secretory carcinoma of breast (C50._)

  • Juvenile carcinoma of breast
  • M8503/0 Intraductal papilloma

  • Duct adenoma, NOS
  • Ductal papilloma
  • M8503/2 Noninfiltrating intraductal papillary adenocarcinoma (C50._)

  • Noninfiltrating intraductal papillary carcinoma
  • Intraductal papillary adenocarcinoma, NOS
  • Intraductal papillary carcinoma, NOS
  • Ductal carcinoma in situ, papillary
  • DCIS, papillary
  • M8503/3 Intraductal papillary adenocarcinoma with invasion (C50._)

  • Infiltrating papillary adenocarcinoma
  • Infiltrating and papillary adenocarcinoma
  • M8504/0 Intracystic papillary adenoma

  • Intracystic papilloma
  • M8504/2 Noninfiltrating intracystic carcinoma

    M8504/3 Intracystic carcinoma, NOS

  • Intracystic papillary adenocarcinoma
  • M8505/0 Intraductal papillomatosis, NOS

  • Diffuse intraductal papillomatosis
  • M8506/0 Adenoma of nipple (C50._)

  • Subareolar duct papillomatosis
  • M8507/2 Intraductal micropapillary carcinoma (C50._)

  • Ductal carcinoma in situ, micropapillary
  • Intraductal carcinoma, clinging
  • M8508/3 Cystic hypersecretory carcinoma (C50._)

    M8510/3 Medullary carcinoma, NOS

  • Medullary adenocarcinoma
  • M8512/3 Medullary carcinoma with lymphoid stroma

    M8513/3 Atypical medullary carcinoma (C50._)

    M8514/3 Duct carcinoma, desmoplastic type

    M8520/2 Lobular carcinoma in situ, NOS (C50._)

  • Lobular carcinoma, noninfiltrating
  • LCIS, NOS
  • M8520/3 Lobular carcinoma, NOS (C50._)

  • Lobular adenocarcinoma
  • Infiltrating lobular carcinoma, NOS
  • M8521/3 Infiltrating ductular carcinoma (C50._)

    M8522/2 Intraductal carcinoma and lobular carcinoma in situ (C50._)

    M8522/3 Infiltrating duct and lobular carcinoma (C50._)

  • Lobular and ductal carcinoma
  • Infiltrating duct and lobular carcinoma in situ
  • Intraductal and lobular carcinoma
  • Infiltrating lobular carcinoma and ductal carcinoma in situ
  • M8523/3 Infiltrating duct mixed with other types of carcinoma (C50._)

  • Infiltrating duct and cribiform carcinoma
  • Infiltrating duct and mucinous carcinoma
  • Infiltrating duct and tubular carcinoma
  • Infiltrating duct and colloid carcinoma
  • M8524/3 Infiltrating lobular mixed with other types of carcinoma (C50._)

    M8525/3 Polymorphous low grade adenocarcinoma

  • Terminal duct adenocarcinoma
  • M8530/3 Inflammatory carcinoma (C50._)

  • Inflammatory adenocarcinoma
  • M8540/3 Paget disease, mammary (C50._)

  • Paget disease of breast
  • M8541/3 Paget disease and infiltrating duct carcinoma of breast (C50._)

    M8542/3 Paget disease, extramammary (except paget disease of bone)

    M8543/3 Paget disease and intraductal carcinoma of breast (C50._)

    8550 Acinar cell neoplasms

    M8550/0 Acinar cell adenoma

  • Acinar adenoma
  • Acinic cell adenoma
  • M8550/1 Acinar cell tumor

  • Acinic cell tumor
  • M8550/3 Acinar cell carcinoma

  • Acinic cell adenocarcinoma
  • Acinar adenocarcinoma
  • Acinar carcinoma
  • M8551/3 Acinar cell cystadenocarcinoma

    856–857 Complex epithelial neoplasms

    M8560/0 Mixed squamous cell and glandular papilloma

    M8560/3 Adenosquamous carcinoma

  • Mixed adenocarcinoma and squamous cell carcinoma
  • Mixed adenocarcionma and epidermoid carcinoma
  • M8561/0 Adenolymphoma (C07._, C08._)

  • Warthin's tumor
  • Papillary cystadenoma lymphomatosum
  • M8562/3 Epithelial-myoepithelial carcinoma

    M8570/3 Adenocarcinoma with squamous metaplasia

  • Adenoacanthoma
  • M8571/3 Adenocarcinoma with cartilaginous and osseus metaplasia

  • Adenocarcinoma with cartilaginous metaplasia
  • Adenocarcinoma with osseous metaplasia
  • M8572/3 Adenocarcinoma with spindle cell metaplasia

    M8573/3 Adenocarcinoma with apocrine metaplasia

  • Carcinoma with apocrine metaplasia
  • M8574/3 Adenocarcinoma with neuroendocrine differentiation

  • Carcinoma with neuroendocrine differentiation
  • M8575/3 Metaplastic carcinoma, NOS

    M8576/3 Hepatoid adenocarcinoma

  • Hepatoid carcinoma
  • 858 Thymic Epithelial Neoplasms

  • M8580/0 Thymoma, benign (C37.9)
  • M8580/1 Thymoma, NOS (C37.9)
  • M8580/3 Thymoma, malignant, NOS (C37.9)
  • M8581/1 Thymoma, type A, NOS (C37.9)
  • Thymoma, spindle cell, NOS
  • Thymoma, medullary, NOS
  • M8581/3 Thymoma, type A, malignant (C37.9)

  • Thymoma, spindle cell, malignant
  • Thymoma, medullary, malignant
  • M8582/1 Thymoma, type AB, NOS (C37.9)

  • Thymoma, mixed type, NOS
  • M8582/3 thymoma, type AB, malignant (C37.9)

  • Thymoma, mixed type, malignant
  • M8583/1 Thymoma, type B1, NOS (C37.9)

  • Thymoma, lymphocyte-rich, NOS
  • Thymoma, lymphocytic, NOS
  • Thymoma, predominantly cortical, NOS
  • Thymoma, organoid, NOS
  • M8583/3 Thymoma, type B1, malignant (C37.9)

  • Thymoma, lymphocyte-rich, malignant
  • Thymoma, lymphocytic, malignant
  • Thymoma, predominantly cortical, malignant
  • Thymoma, organoid, malignant
  • M8584/1 Thymoma, type B2, NOS (C37.9)

  • Thymoma, cortical, NOS
  • M8584/3 Thymoma, type B2, malignant (C37.9)

  • Thymoma, cortical, malignant
  • M8585/1 Thymoma, type B3, NOS (C37.9)

  • Thymoma, epithelial, NOS
  • Thymoma, atypical, NOS
  • M8585/3 Thymoma, type B3, malignant (C37.9)

  • Thymoma, epithelial, malignant
  • Thymoma, atypical, malignant
  • Well differentiated thymic carcinoma
  • M8586/3 Thymic carcinoma, NOS (C37.9)

  • Thymoma, type C
  • M8587/0 Ectopic hamartomatous thymoma

    M8588/3 Spindle epithelial tumor with thymus-like element

  • Spindle epithelial tumor with thymus-like differentiation
  • SETTLE
  • M8589/3 Carcinoma showing thymus-like element

  • Carcinoma showing thymus-like differentiation
  • CASTLE
  • 859–867 Specialized gonadal neoplasms

    M8590/1 Sex cord-stromal tumor, NOS

  • Sex cord/gonadal stromal tumor, NOS
  • Testicular/ovarian stromal tumor
  • M8591/1 Sex cord-gonadal stromal tumor, incompletely differentiated

    M8592/1 Sex cord-gonadal stromal tumor, mixed forms

    M8593/1 Stromal tumor with minor sex cord elements

    M8600/0 Thecoma, NOS

  • Theca cell tumor
  • M8600/3 Thecoma, malignant

    M8601/0 Thecoma, luteinized

    M8602/0 Sclerosing stromal tumor

    M8610/0 Luteoma, NOS

  • Luteinoma
  • M8620/1) Granulosa cell tumor, NOS

  • , adult type
  • M8620/3 Granulosa cell tumor, malignant

  • Granulosa cell carcinoma
  • Granulosa cell tumor, sarcomatoid
  • M8621/1 Granulosa cell-theca cell tumor

  • Theca cell-granulosa cell tumor
  • M8622/1 Granulosa cell tumor, juvenile

    M8623/1 Sex cord tumor with annular tubules

    M8630/1 Androblastoma/Arrhenoblastoma, benign

    M8630/1 Androblastoma/Arrhenoblastoma, NOS

    M8630/3 Androblastoma/Arrhenoblastoma, malignant

    M8631/0 Sertoli-Leydig cell tumor, well differentiated

    M8631/1 Sertoli-Leydig cell tumor of intermediate differentiation

  • Sertoli-Leydig cell tumor, NOS
  • M8631/3 Sertoli-Leydig cell tumor, poorly differentiated

  • Sertoli-Leydig cell tumor, sarcomatoid
  • M8632/1 Gynandroblastoma

    M8633/1 Sertoli-Leydig cell tumor, retiform

    M8634/1 Sertoli-Leydig cell tumor, intermediate differentiation, with heterologous elements

  • retiform, with heterologous elements
  • M8634/3 Sertoli-Leydig cell tumor, poorly differentiated, with heterologous elements

    M8640/1 Sertoli tumor, NOS

  • Pick tubular adenoma
  • Sertoli cell adenoma
  • Tubular androblastoma, NOS
  • Testicular adenoma
  • M8640/3 Sertoli cell carcinoma (C62._)

    M8641/0 Sertoli cell tumor with lipid storage

  • Folliculome lipidique (C56.9)
  • Tubular androblastoma with lipid storage
  • Lipid-rich Sertoli cell tumor
  • M8642/1 large cell calcifying Sertoli cell tumor

    M8650/0 Leydig cell tumor, bening (C62._)

    M8650/3 Leydig cell tumor, malignant

  • Interstitial cell tumor, malignant
  • M8660/0 Hilus cell tumor (C56.9)

  • Hilar cell tumor
  • M8670/0 Lipid cell tumor of ovary (C56.9)

  • Lipoid cell tumor of ovary
  • Steroid cell tumor, NOS
  • Masculinovoblastoma
  • M8670/3 Steroid cell tumor, malignant

    M8641/0 Adrenal rest tumor

    868–871 Paragangliomas And Glomus tumors

    M8680/0 Paraganglioma, benign

    M8680/1 Paraganglioma, NOS

    M8680/3 paraganglioma, malignant

    M8681/1 Sympathetic paraganglioma

    M8682/1 Parasympathetic paraganglioma

    M8683/0 Gangliocytic paraganglioma (C17.0)

    M8690/1 Glomus jugulare tumor, NOS (C75.5)

  • Jugular/jugulotympanic paranglioma
  • M8691/1 Aortic body tumor (C75.5)

  • Aortic/aorticopulmonary paraganglioma
  • M8692/1 Carotid body tumor/paraganglioma (C75.4)

    M8693/1 Extra-adrenal paraganglioma, NOS

  • Nonchromaffin paraganglioma, NOS
  • Chemodectoma
  • M8693/3 Extra-adrenal paraganglioma, malignant

  • Nonchromaffin paraganglioma, malignant
  • M8700/0 Pheochromocytoma, NOS (C74.1)

  • Adrenal medullary/chromaffin paraganglioma
  • Chromaffin tumor
  • Chromaffinoma
  • M8700/3 Pheochromocytoma, malignant (C74.1)

  • Adrenal medullary paraganglioma, malignant
  • Pheochromoblastoma
  • M8710/3 Glomangiosarcoma

  • Glomoid sarcoma
  • M8711/0 Glomus tumor, NOS

    M8711/3 Glomus tumor, Malignant

    M8712/0 Glomangioma

    M8713/0 Glomangiomyoma

    872–879 Nevi And Melanomas

    M8720/0 Pigmented nevus, NOS

  • Melanocytic nevus
  • Nevus, NOS
  • Hairy nevus
  • M8720/2 Melanoma in situ

    M8720/3 Malignant melanoma, NOS (except juvenile melanoma M8770/0)

  • Melanoma, NOS
  • M8721/3 Nodular melanoma

    M8722/0 Balloon cell nevus

    M8722/3 Balloon cell melanoma

    M8723/0 Halo nevus

  • Regressing nevus
  • M8723/3 Malignant melanoma, regressing

    M8725/0 Neuronevus

    M8726/0 Magnocellular nevus (C69.4)

  • Melanocytoma, eyeball
  • Melanocytoma, NOS
  • M8727/0 Dysplastic nevus

    M8727/0 dysplastic nevus

    M8728/0 Diffuse melanocytosis

    M8728/1 Meningeal melanocytoma (C70.9)

    M8728/3 Meningeal melanomatosis (C70.9)

    M8730/0 Nonpigmented nevus

  • Achromic nevus
  • M8740/0 Junctional nevus, NOS

  • Intraepidermal nevus
  • M8740/3 Malignant melanoma in junctional nevus

    M8741/2 Precancerous melanosis, NOS

    M8741/3 Malignant melanoma in precancerous melanosis

    M8742/3 Lentigo maligna melanoma

  • Hutchinson melanotic freckle
  • M8743/3 Superficial spreading melanoma

    M8744/3 Acral lentiginous melanoma, malignant

    M8745/3 * Desmoplastic melanoma, malignant

  • Neurotropic melanoma, malignant
  • Melanoma, desmoplastic, amelanotic
  • M8746/3 Mucosal lentiginous melanoma

    M8750/0 Intradermal nevus

  • Dermal nevus
  • M8760/0 compound nevus

  • Dermal and epidermal nevus
  • M8761/0 Small congenital nevus

    M8761/1 Giant pigmented nevus, NOS

  • Intermediate and giant congenital nevus
  • M8761/3 Malignant melanoma in giant pigmented nevus/congenital melanocytic nevus

    M78762/1 Proliferative dermal lesion in congenital nevus

    M8770/0 Epithelioid and spindle cell nevus

  • Juvenile nevus
  • Juvenile melanoma
  • Spitz nevus
  • Pigmented spindle cell nevus of Reed
  • M8770/3 Mixed epithelioid and spindle cell melanoma

    M8771/0 Epithelioid cell nevus

    M8771/3 Epithelioid cell melanoma

    M8772/0 spindle cell nevus, NOS

    M8772/3 Spindle cell melanoma, NOS

    M8773/3 Spindle cell melanoma, type A

    M8774/3 Spindle cell melanoma, type B

    M8780/0 Blue nevus, NOS

  • Jadassohn blue nevus
  • M8780/3 blue nevus, malignant

    M8790/0 Cellular blue nevus

    880 Soft tissue Tumors And Sarcomas, NOS

    M8800/0 Soft tissue tumor, benign

    M8800/3 Sarcoma, NOS

  • Soft tissue sarcoma
  • Soft tissue/mesenchymal tumor, malignant
  • M8800/9 Sarcomatosis, NOS

    M8801/3 Spindle cell sarcoma

    M8802/3 Giant cell sarcoma (except of bone M9250/3)

  • Pleomorphic cell sarcoma
  • M8803/3 Small cell sarcoma

  • Round cell sarcoma
  • M8804/3 Epithelioid sarcoma

  • Epithelioid cell sarcoma
  • M8805/3 Undifferentiated sarcoma

    M8806/3 Desmoplastic small round cell tumor

    881–883 Fibromatous neoplasms

    M8810/0 Fibroma, NOS

    M8810/1 Cellular fibroma (C56.9)

    M8810/3 Fibrosarcoma, NOS

    M8811/0 Fibromyxoma

  • Myxoid fibroma
  • Myxofibroma, nos
  • M8811/3 Fibromyxosarcoma

    M8812/0 Periosteal fibroma (C40._, C41._)

  • Periosteal sarcoma, NOS
  • M8813/0 Fascial fibroma

    M8813/3 Fascial fibrosarcoma

    M8814/3 Infantile fibrosarcoma

  • Congenital fibrosarcoma
  • M8815/0 Solitary fibrous tumor

  • Localized fibrous tumor
  • M8815/3 Solitary fibrous tumor, malignant

    M8820/0 Elastofibroma

    M8821/1 Aggressive fibromatosis

  • Extra-abdominal desmoid
  • Desmoid, NOS
  • Invasive fibroma
  • M8822/1 Abdominal fibromatosis

  • Abdominal desmoid
  • Mesenteric fibromatosis (C48.1)
  • Retroperitoneal fibromatosis (C48.0)
  • M8823/0 Desmoplastic fibroma

    M8824/0 Myofibroma

    M8824/1 Myofibromatosis

  • Congenital generalized fibromatosis
  • Infantile myofibromatosis
  • M8825/0 Myofibroblastoma

    M8825/1 Myofibroblastic tumor, nos

  • Inflammatory myofibroblastic tumor
  • M8826/0 Angiomyofibroblastoma

    M8827/1 Myobfibroblastic tumor, peribronchial (C34._)

  • congenital peribronchial myofibroblastic tumor
  • M8830/0 Benign fibrous histiocytoma

  • Fibrous histiocytoma, NOS
  • Fibroxanthoma, NOS
  • Xantofibroma
  • M8830/1 Atypical fibrous histiocytoma

  • Atypical fibroxanthoma
  • M8830/3 Malignant fibrous histiocytoma

  • Fibroxanthoma, malignant
  • M8831/0 Histiocytoma, NOS

  • Deep histiocytoma
  • Juvenile histiocytoma
  • Reticulohistiocytoma
  • M8832/0 Dermatofibroma, NOS (C44._)

  • Sclerosing hemangioma
  • Cutaneous histiocytoma
  • Subepidermal nodular fibrosis
  • Dermatofibroma lenticulare
  • M8832/3 Dermatofibrosarcoma, NOS (C44._)

  • Dermatofibrosarcoma protuberans, NOS
  • M8833/3 Pigmented dermatofibrosarcoma protuberans

  • Bednar tumor
  • M8834/1 Giant cell fibroblastoma

    M8835/1 Plexiform fibrohistiocytic tumor

    M8836/1 Angiomatoid fibrous histiocytoma

    884 Myxomatous neoplasms

    M8840/0 Myxoma, NOS

    M8840/3 Myxosarcoma

    M8841/1 Angiomyxoma

  • Aggressive angiomyxoma
  • M8842/0 Ossifying fibromyxoid tumor

    885–888 Lipomatous neoplasms

    M8850/0 Lipoma, NOS

    M8850/1 Atypical lipoma

  • Superficial well differentiated liposarcoma
  • Well differentiated liposarcoma of superficial soft tissue
  • M8850/3 Liposarcoma, NOS

  • Fibroliposarcoma
  • M8851/0 Fibrolipoma

    M8851/3 Liposarcoma, well differentiated

  • Liposarcoma, differentiated
  • Lipoma-like liposarcoma
  • Sclerosing liposarcoma
  • Inflammatory liposarcoma
  • M8852/0 Fibromyxolipoma

  • Myxolipoma
  • M8852/3 Myxoid liposarcoma

  • Myxoliposarcoma
  • M8853/3 Round cell liposarcoma

    M8854/0 Pleomorphic lipoma

    M8854/3 Pleomorphic liposarcoma

    M8855/3 Mixed liposarcoma

    M8856/0 Intramuscular lipoma

  • Infiltrating lipoma/angiolipoma
  • M8857/0 Spindle cell lipoma

    M8857/3 Fibroblastic liposarcoma

    M8858/3 Dedifferentiated liposarcoma

    M8860/0 Angiomyolipoma

    M8861/0 Angiolipoma, NOS

    M8862/0 Chondroid lipoma

    M8870/0 Myelolipoma

    M8880/0 Hibernoma

  • Fetal fat cell lipoma
  • Brown fat tumor
  • M8881/0 Lipoblastomatosis

  • Fetal lipoma, NOS
  • Fetal lipomatosis
  • Lipoblastoma
  • 889–892 Myomatous neoplasms

    M8890/0 Leiomyoma, NOS

  • Fibroid uterus (C55.9)
  • Fibromyoma
  • Leiomyofibroma
  • Plexiform leiomyoma
  • Lipoleiomyoma
  • M8890/1 Leiomyomatosis, NOS

  • Intravascular leiomyomatosis
  • M8890/3 Leiomyosarcoma, NOS

    M8891/0 Epithelioid leiomyoma

  • Leiomyoblastoma
  • M8891/3 Epithelioid leiomyosarcoma

    M8892/0 Cellular leiomyoma

    M8893/0 Bizarre leiomyoma

  • Symplastic/atypical/pleomorphic leiomyoma
  • M8894/0 Angiomyoma

  • Vascular leiomyoma
  • Angioleiomyoma
  • M8894/3 Angiomyosarcoma

    M8895/0 Myoma

    M8895/3 Myosarcoma

    M8896/3 Myxoid leiomyosarcoma

    M8897/1 Smooth muscle tumor of uncertain malignant potential

  • Smooth muscle tumor, NOS
  • M8898/1 Metastasizing leiomyoma

    M8900/0 Rhabdomyoma, NOS

    M8900/3 Rhabdomyosarcoma, NOS

  • Rhabdosarcoma
  • M8901/3 Pleomorphic rhabdomyosarcoma, adult type

  • Pleomorphic rhabdomyosarcoma, NOS
  • M8902/3 Mixed type rhabdomyosarcoma

  • Mixed embryonal rhabdomyosarcoma and alveolar rhabdomyosarcoma
  • M8903/0 Fetal rhabdomyoma

    M8904/0 Adult rhabdomyoma

  • Glycogenic rhabdomyoma
  • M8905/0 Genital rhabdomyoma

    M8910/3 Embryonal rhabdomyosarcoma, NOS

  • Embryonal rhabdomyosarcoma, pleomorphic
  • Sarcoma botryoides
  • Botryoid sarcoma
  • M8912/3 Spindle cell rhabdomyosarcoma

    M8920/3 Alveolar rhabdomyosarcoma

    M8921/3 Rhabdomyosarcoma with ganglionic differentiation

  • Ectomesenchymoma
  • 893–899 Complex Mixed And Stromal Neoplasms

    M8930/0 Endometrial stromal nodule

    M8930/3 Endometrial stromal sarcoma, NOS

  • Endometrial sarcoma, NOS
  • Endometrial stromal sarcoma, high grade
  • M8931/3 Endometrial stromal sarcoma, low grade

  • Endolymphatic stromal myosis
  • Endometrial stromatosis
  • Stromal endometriosis
  • Stromal myosis, NOS
  • M8932/0 Adenomyoma

  • Atypical polypoid adenomyoma
  • M8933/3 Adenosarcoma

    M8934/3 Carcinofibroma

    M8935/0 Stromal tumor, benign

    M9835/1 Stromal tumor, NOS

    M8935/3 Stromal sarcoma, NOS

    M8936/0 Gastrointestinal stromal tumor, benign

  • GIST, benign
  • M8936/1 Gastrointestinal stromal tumor, NOS

  • GIST, NOS/uncertain malignant potential
  • Gastrointestinal autonomic nerve tumor (GANT)
  • Gastrointestinal pacemaker cell tumor
  • M8936/3 Gastrointestinal stromal sarcoma

  • GIST, malignant
  • M8940/0 Pleomorphic adenoma

  • Mixed tumor, NOS
  • Mixed tumor, salivary gland type, NOS
  • Chondroid syringoma
  • M8940/3 Mixed tumor, malignant, NOS

  • Mixed tumor, malignant, NOS
  • Mixed tumor, salivary gland type, malignant
  • Malignant chondroid syringoma
  • M8941/3 Carcinoma in pleomorphic adenoma

    M8950/3 Mullerian mixed tumor

    M8951/3 Mesodermal mixed tumor

    M8959/0 Benign cystic nephroma

    M8959/1 Cystic partially differentiated nephroblastoma

    M8959/3 Malignant cystic nephroma

  • Malignant multilocular cystic nephroma
  • M8960/1 Mesoblastic nephroma

    M8960/3 Nephroblastoma, NOS

  • Wilms's tumor
  • Nephroma, NOS
  • M8963/3 malignant rhabdoid tumor

  • Rhabdoid sarcoma
  • Rhabdoid tumor, NOS
  • M8964/3 Clear cell sarcoma of kidney

    M8965/0 Nephrogenic adenofibroma

    M8966/0 Renomedullary interstitial cell tumor

  • Renomedullary fibroma
  • M8967/0 Ossifying renal tumor

    M8970/3 Hepatoblastoma

  • Embryonal hepatoma
  • M8971/3 Pancreatoblastoma

    M8972/3 Pulmonary blastoma

  • Pneumoblastoma
  • M8973/3 Pleuropulmonary blastoma

    M8974/1 Sialoblastoma

    M8980/3 Carcinosarcoma, NOS

    M8981/3 Carcinosarcoma, embryonal

    M8982/0 Myoepithelioma

  • Myoepithelial tumor
  • Myoepithelial adenoma
  • M8982/3 Malignant myoepithelioma

  • Myoepithelial carcinoma
  • M8983/0 Adenomyoepithelioma

    M8990/0 Mesencymoma, benign

    M8990/1 Mesenchymoma, NOS

  • Mixed mesenchymal tumor
  • M8990/3 Mesenchymoma, malignant

  • Mixed mesenchymal sarcoma
  • M8991/3 Embryonal sarcoma

    9000–9030) Fibroepithelial Neoplasms

    M9000/0 Brenner tumor, NOS

    M9000/1 Brenner tumor, borderline malignancy

  • Brenner tumor, proliferating
  • M9000/3 Brenner tumor, malignant

    M9010/0 Fibroadenoma, NOS

    M9011/0 Intracanalicular fibroadenoma

    M9012/0 Pericanalicular fibroadenoma

    M9013/0 Adenofibroma, NOS

  • Cystadenofibroma, NOS
  • Papillary adenofibroma
  • M9014/0 Serous adenofibroma, NOS

  • Serous cystadenofibroma, NOS
  • M9014/1 Serous adenofibroma of borderline malignancy

  • Serous cystadenofibroma of borderline malignancy
  • M9014/3 Serous adenocarcinofibroma

  • Malignant serous adenofibroma
  • Serous cystadenocarcinofibroma
  • Malignant serous cystadenofibroma
  • M9015/0 Mucinous adenofibroma, NOS

  • Mucinous cystadenofibroma, NOS
  • M9015/1 Mucinous adenofibroma of borderline malignancy

  • Mucinous cystadenofibroma of borderline malignancy
  • M9015/3 Mucinous adenocarcinofibroma

  • Malignant mucinous adenofibroma
  • Mucinous cystadenocarcinofibroma
  • Malignant mucinous cystadenofibroma
  • M9016/0 Gian fibroadenoma

    M9020/0 Phyllodes tumor, benign

  • Cystosarcoma phyllodes, benign
  • M9020/1 Phyllodes tumor, borderline

  • Cystosarcoma phyllodes, NOS
  • Phyllodes tumor, NOS
  • M9020/3 Phyllodes tumor, malignant

  • Cystosarcoma phyllodes, malignant
  • M9030/0 Juvenile fibroadenoma

    904 Synovial-Like Neoplasms

    M9040/0 Synovioma, benign

    M9040/3 Synovial sarcoma, NOS

  • Synovioma, NOS
  • Synovioma, malignant
  • M9041/3 Synovial sarcoma, spindle cell

  • Synovial sarcoma, monophasic fibrous
  • M9042/3 Synovial sarcoma, epithelioid cell

    M9043/3 Synovial sarcoma, biphasic

    M9044/3 Clear cell sarcoma, NOS (except of kiney M9864/3)

  • Clear cell sarcoma, of tendons and aponeuroses
  • Melanoma, malignant, of soft parts
  • 905 Mesothelial Neoplasms

    M9050/0 Mesothelioma, benign

    M9050/3 Mesothelioma, malignant or NOS

    M9051/0 Fibrous mesothelioma, benign

    M9051/3 Fibrous mesothelioma, malignant or NOS

  • Spindled mesothelioma
  • Sarcomatoid mesothelioma
  • Desmoplastic mesothelioma
  • M9052/0 Epithelioid mesothelioma, benign

  • Well differentiated papillary mesothelioma, benign
  • mesothelial papilloma
  • M9052/3 Epithelioid mesothelioma, malignant or NOS

    M9053/3 Mesothelioma, biphasic, malignant or NOS

    M9054/0 Adenomatoid tumor, NOS

    M9055/0 Multicystic mesothelioma, benign

  • Cystic mesothelioma, benign
  • M9055/1 cystic mesothelioma, NOS

    906–909 Germ cell Neoplasms

    M9060/3 Dysgerminoma

    M9061/3 Seminoma, NOS

    M9062/3 Seminoma, anaplastic

  • Seminoma with high mitotic index
  • M9063/3 Spermatocytic seminoma

  • Spermatocytoma
  • M9064/2 Intratubular malignant germ cells

  • Intratubular germ cell neoplasia
  • M9064/3 Germinoma

  • Germ cell tumor, NOS
  • M9065/3 Germ cell tumor, nonseminomatous

    M9070/3 Embryonal carcinoma, NOS

  • Embryonal adenocarcinoma
  • M9071/3 Yolk sac tumor

  • Endodermal sinus tumor
  • Polyvesicular vitelline tumor
  • Orchioblastoma
  • Embryonal carcinoma, infantile
  • Hepatoid yolk sac tumor
  • M9072/3 Polyembryoma

  • Embryonal carcinoma, polyembryonal type
  • M9073/1 Gonadoblastoma

  • Gonocytoma
  • M9080/0 Teratoma, benign

  • Adult cystic teratoma
  • Adult/cystic teratoma, NOS
  • Teratoma, differentiated
  • Mature teratoma
  • M9080/1 Teratoma, NOS

  • Solid teratoma
  • M9080/3 Teratoma, malignant, NOS

  • Embryonal teratoma
  • Teratoblastoma, malignant
  • Immature teratoma, malignant or NOS
  • M9081/3 Teratocarcinoma

  • Mixed embryonal carcinoma and teratoma
  • M9082/3 malignant teratoma, undifferentiated

  • Malignant teratoma, anaplastic
  • M9083/3 Malignant teratoma, intermediate

    M9084/0 Dermoid cyst, NOS

  • Dermoid, NOS
  • M9084/3 Teratoma with malignant transformation

  • Dermoid cyst with malignant transformation or with secondary tumor
  • M9085/3 mixed germ cell tumor

  • Mixed teratoma and seminoma
  • M9090/0 Struma ovarii, NOS

    M9090/3 Struma ovarii, malignant

    M9091/1 Strumal carcinoid

  • Struma ovarii and carcinoid
  • 910 Trophoblastic neoplasms

    M9100/0 Hydatidifrom mole, NOS

  • Hydatid mole
  • Complete hydatidiform mole
  • M9100/1 Invasive hydatidiform mole

  • Chorioadenoma /destruens
  • Chorioadenoma
  • Invasive mole, NOS
  • Malignant hydatidiform mole
  • M9100/3 Choriocarcinoma, NOS

  • Chorionepithelioma
  • Chorioepithelioma
  • M9101/3 Choriocarcinoma combined with other germ cell elements

  • combined with teratoma
  • combined with embryonal carcinoma
  • M9102/3 Malignant teratoma, trophoblastic

    M9103/0 Partial hydatidiform mole

    M9104/1 Placental site trophoblastic tumor

    M9105/3 Trophoblastic tumor, epithelioid

    911 Mesonephromas

    M9110/0 Mesonephroma, benign

  • Mesonephric adenoma
  • Wolffian duct adenoma
  • M9110/1 Mesonephric tumor, NOS

  • Wolffian duct tumor
  • M9110/3 Mesonephroma, malignant

  • Mesonephric adenocarcinoma
  • Mesonephroma, NOS
  • Wolffian duct carcinoma
  • 912–916 Blood vessel tumors

    M9120/0 Hemangioma, NOS

  • Angioma, NOS
  • Chorioangioma
  • M9120/3 Hemangiosarcoma

  • Angiosarcoma
  • M9121/0 Cavernous hemangioma

    M9122/0 Venous hemangioma

    M9123/0 Racemose hemangioma

  • Arteriovenous hemangioma
  • M9124/3 Kupffer cell sarcoma

    M9125/0 Epithelioid hemangioma

  • Histiocytoid hemangioma
  • M9130/0 Hemangioendothelioma, benign

    M9130/1 Hemangioendothelioma, NOS

  • Angioendothelioma
  • Kaposiform hemangioendothelioma
  • M9130/3 Hemangioendothelioma, malignant

  • Hemangioendothelial sarcoma
  • M9131/0 Capillary hemangioma

  • Hemangioma simplex
  • Infantile/plexiform/juvenile hemangioma
  • M9132/0 Intramuscular hemangioma

    M9133/1 Epithelioid hemangioendothelioma, NOS

    M9133/3 Epithelioid hemangioendothelioma, malignant

  • Intravascular bronchial alveolar tumor
  • M9135/1 Endovascular papillary angioendothelioma

  • Dabska tumor
  • M9136/1 Spindle cell hemangioendothelioma

  • Spindle cell angioendothelioma
  • M9140/3 Kaposi's sarcoma

  • Multiple hemorrhagic sarcoma
  • M9141/0 Angiokeratoma

    M9142/0 Verrucous keratotic hemangioma

    M9150/0 Hemangiopericytoma, benign

    M9150/1 Hemangiopericytoma, NOS

  • Hemangiopericytic meningioma
  • M9150/3 Hemangiopericytoma, malignant

    M9160/0 angiofibroma, NOS

  • Juvenile angiofibroma
  • Fibrous papule of nose
  • Involuting nevus
  • Giant cell or cellular angiofibroma
  • M9161/0 Acquired tufted hemangioma

    M9161/1 Hemangioblastoma

  • Angioblastoma
  • M9150/0 Hemangiopericytoma, benign

    M9150/1 Hemangiopericytoma, NOS

    917 Lymphatic vessel tumors

    M9170/0 Lymphangioma, NOS

  • Lymphangioendothelioma, NOS
  • M9170/3 Lymphangiosarcoma

  • Lymphangioendothelial sarcoma
  • Lymphangioendothelioma, malignant
  • M9171/0 Capillary lymphangioma

    M9172/0 Cavernous lymphangioma

    M9173/0 Cystic lymphangioma

  • Hygroma, NOS
  • Cystic Hygroma
  • M9174/0 Lymphangiomyoma

    M9174/1 Lymphangiomyomatosis

  • Lymphangioleiomyomatosis
  • M9175/0 Hemolymphangioma

    918–924 Osseous And Chondromatous neoplasms

    M9180/0 Osteoma, NOS

    M9180/3 Osteosarcoma, NOS

  • Osteogenic sarcoma, NOS
  • Osteochondrosarcoma
  • Osteoblastic sarcoma
  • M9181/3 Chondroblastic osteosarcoma

    M9182/3 Fibroblastic osteosarcoma

  • Osteofibrosarcoma
  • M9183/3 Telangeictatic osteosarcoma

    M9184/3 Osteosarcoma in Paget disease of bone

    M9185/3 Small cell osteosarcoma

  • Round cell osteosarcoma
  • M9186/3 Central osteosarcoma

  • Conventional central osteosarcoma
  • Medullary osteo sarcoma
  • M9187/3 Intraosseous well differentiated osteosarcoma

  • Intraosseous low grade osteosarcoma
  • M9191/0 Osteoid osteoma, NOS

    M9192/3 Parosteal osteosarcoma

  • Juxtacortical osteosarcoma
  • M9193/3 Periosteal osteosarcoma

    M9194/3 High grade surface osteosarcoma

    M9195/3 Intracortical osteosarcoma

    M9200/0 Osteoblastmoa, NOS

  • Giant osteoid ostemoa
  • M9200/1 Aggressive osetoblastoma

    M9210/0 Osteochondroma

  • Cartilagionus exostosis
  • Cartilaginous exostosis
  • Ecchondroma
  • M9210/1 Osteochondromatosis, NOS

  • Ecchondrosis
  • M9220/0 Chondroma, NOS

  • Enchondroma
  • M9220/1 Condromatosis, NOS

    M9220/3 Chondrosarcoma, NOS

  • Fibrochondrosarcoma
  • M9221/0 Juxtacortical chondroma

  • Periosteal chondroma
  • M9221/3 Juxtacortical chondrosarcoma

  • Periosteal chondrosarcoma
  • M9230/0 Chondroblastoma, NOS

  • Chondromatous giant cell tumor
  • Codman tumor
  • M9230/3 Chondroblastoma, malignant

    M9231/3 Myxoid chondrosarcoma

    M9240/3 Mesenchymal chondrosarcoma

    M9241/0 Chondromyxoid fibroma

    M9242/3 Clear cell chondrosarcoma

    M9243/3 Dedifferentiated chondrosarcoma

    925 Giant cell tumors

    M9250/1 giant cell tumor of bone, NOS

  • Osteoclastoma, NOS
  • M9250/3 Giant cell tumor of bone, malignant

  • Osteoclastoma, malignant
  • Giant cell sarcoma of bone
  • M9251/1 Giant cell tumor of soft parts, NOS

    M9251/3 Malignant giant cell tumor of soft parts

    M9252/0 Tenosynovial giant cell tumor

  • Fibrous histiocytoma of tendon sheath
  • Giant cell tumor of tendon sheath
  • M9252/3 Malignant tenosynovial giant cell tumoe

  • Giant cell tumor of tendon sheath, malignant
  • 926 Miscellaneous bone tumors (C40._, C41._)

    M9260/3 Ewing's sarcoma/tumor

    M9261/3 Adamantinoma of long bones

    M9262/0 Ossifying fibroma

  • Fibro-osteoma
  • Osteofibroma
  • 927–934 Odontogenic tumors C41._)

    M9270/0 Odontogenic tumor, benign

    M9270/1 Odontogenic tumor, NOS

    M9270/3 Odontogenic tumor, malignant

  • Odontogenic carcinoma/sarcoma
  • Primary intraosseus or ameloblastic carcinoma
  • M9271/0 Ameloblastic fibrodentinoma

  • Dentinoma
  • M9272/0 Cementoma, NOS

  • Periapical cemental dysplasia or cemento-osseus dysplasia
  • M9273/0 Cementoblastoma, benign

    M9274/0 Cementifying fibroma

  • Cemento-ossifying fibroma
  • M9275/0 Gigantiform cementoma

  • Florid osseus dysplasia
  • M9280/0 Odontoma, NOS

    M9281/0 Compound odontoma

    M9282/0 Complex odontoma

    M9290/0 Ameloblastic fibro-odontoma

  • Fibroameloblastic odontoma
  • M9290/3 Ameloblastic odontosarcoma

  • Ameloblastic fibrodentinosarcoma or fibro-odontosarcoma
  • M9300/0 Adenomatoid odontogenic tumor

  • Adenomeloblastoma
  • M9301/0 Calcifying odontogenic cyst

    M9302/0 Odontogenic ghost cell tumor

    M9310/0 Ameloblastoma, NOS

  • Adamantinoma, NOS (except of long bones M9261/3)
  • M9310/3 Ameloblastoma, malignant

  • Adamantinoma, NOS (except of long bones M9261/3)
  • M9311/0 Odontoameloblastoma

    M9312/0 Squamous odontogenic tumor

    M9320/0 Odontogenic myxoma

  • Odontogenic myxofibroma
  • M9321/0 Central odontogenic fibroma

  • Odontogenic fibroma, NOS
  • M9322/0 Peripheral odontogenic fibroma

    M9330/0 Ameloblastic fibroma

    M9330/3 Ameloblastic fibrosarcoma

  • Ameloblastic sarcoma
  • Odontogenic fibrosarcoma
  • M9340/0 Calcifying epithelial odontogenic tumor

  • Pindbord gumor
  • M9341/1 clear cell odontogenic tumor

    M9342/3 Odontogenic carcinosarcoma

    935–937 Miscellaneous tumors

    M9350/1 Craniopharyngioma

  • Rathke pouch tumor
  • M9351/1 Craniopharyngioma, adamantinomatous

    M9352/1 Craniopharyngioma, papillary

    M9360/1 Pinealoma

    M9361/1 Pineocytoma

    M9362/3 Pineoblastoma

  • Mixed pineal tumor
  • Mixed pineocytoma-pineoblastoma
  • Pineal parenchymal tumor of intermediate differentiation
  • Transitional pineal tumor
  • M9363/0 Melanotic neuroectodermal tumor

  • Retinal anlage tumor
  • Melanoameloblastoma
  • Melanotic progonoma
  • M9364/3 Peripheral neuroectodermal tumor

  • Neuroectodermal tumor, NOS
  • Peripheral primitive neuroectodermal tumor, NOS (PPNET)

    M9365/3 Askin Tumor

    M9370/3 Chordoma, NOS

    M9371/3 Chondroid chordoma

    M9372/3 Dedifferentiated chorcoma

    M9373/0 Parachordoma

    938–948 Gliomas

    M9380/3 Glioma, malignant

  • Glioma, NOS (except nasal glioma, not neoplastic)
  • M9381/3 Gliomatosis cerebri

    M9382/3 Mixed glioma

  • oligoastrocytoma
  • Anaplastic oligoastrocytoma
  • M9383/1 Subepyndymoma

  • Subependymal glioma
  • Subependymal astrocytoma, NOS
  • Mixed subendymoma-ependymoma
  • M9384/1 Subependymal giant cell astrocytoma

    M9390/0 Choroid plexus papilloma, NOS

    M9390/1 Atypical choroid plexus papilloma

    M9390/3 Choroid plexus carcinoma

  • Choroid plexus papilloma, anaplastic or malignant
  • M9391/3 Ependymoma, NOS

  • Epithelial / cellular / clear cell / tanycytic ependymoma
  • M9392/3 Ependymoma, anaplastic

  • Ependymoblastoma
  • M9393/3 Papillary ependymoma

    M9394/1 Myxopapillary ependymoma

    M9400/3 Astrocytoma, NOS

  • Astrocytic glioma
  • Astroglioma
  • Diffuse astrocytoma
  • Astrocytoma, low grade
  • Diffuse astocytoma, low grade
  • Cystic astrocytoma
  • M9401/3 Astrocytoma, anaplastic

    M9410/3 Protoplasmic astrocytoma

    M9411/3 Gemistocytic astrocytoma

  • Gemistocytoma
  • M9412/1 Desmoplastic infantile astrocytoma or ganglioglioma

    M9413/0 dysembryoplastic neuroepithelial tumor

    M9420/3 Fibrillary astrocytoma

  • Fibrous astrocytoma
  • M9421/1 Pilocytic astrocytoma

  • Piloid or Juvenile astrocytoma
  • Spongioblastoma, NOS
  • M9423/3 Polar spongioblastoma

  • Spongioblastoma polare
  • Primitive polar spongioblastoma
  • M9424/3 Pleomorphic xanthoastrocytoma

    M9430/3 Astroblastoma

    M9440/3 Glioblastoma, NOS

  • Glioblastoma multiforme
  • Spongioblastoma multiforme
  • M9441/3 Giant cell glioblastoma

  • Monstrocellular sarcoma
  • M9442/1 gliofibroma

    M9442/3 gliosarcoma

  • Glioblastoma with sarcomatous component
  • M9444/1 Chordoid glioma

  • Chordoid glioma of third ventricle
  • M9450/3 Oligodendroglioma, NOS

    M9451/3 Oligodendroglioma, anaplastic

    M9460/3 Oligodendroblastoma

    M9470/3 Medullablastoma, NOS

  • Melanotic medulloblastoma
  • M9471/3 Desmoplastic nodular medulloblastoma

  • Desmoplastic medulloblastoma
  • Circumscribed arachnoidal cerebellar sarcoma
  • M9472/3 Medullomyoblastoma

    M9473/3 Primitive neuroectodermal tumor, NOS

  • PNET, NOS
  • Central primitive neuroectodermal tumor, NOS (CPNET)
  • Supratentorial PNET
  • M9474/3 large cell medulloblastoma

    M9480/3 Cerebellar sarcoma, NOS

    949–952 Neuroepitheliomatous neoplasms

    M9490/0 Ganglioneuroma

    M9490/3 Ganglioneuroblastoma

    M9491/0 Ganglioneuromatosis

    M9492/0 Gangliocytoma

    M9493/0 Dysplastic gangliocytoma of cerebellum (Lhermitte-Duclos)

    M9500/3 Neuroblastoma, NOS

  • Sympathicoblastoma
  • Central neuroblastoma
  • M9501/0 Medulloepithelioma, benign

  • Diktyoma, benign
  • M9501/3 Medulloepithelioma, NOS

  • Diktyoma, malignant
  • M9502/0 Teratoid medulloepithelioma, benign

    M9502/3 Teratoid medulloepithelioma

    M9503/3 Neuroepithelioma, NOS

    M9504/3 Spongioneuroblastoma

    M9505/1 Ganglioglioma, NOS

    M9505/3 Ganglioglioma, anaplastic

    M9506/1 Central neurocytoma

  • Neurocytoma
  • Cerebellar liponeurocytoma
  • Lipomatous medulloblastoma
  • Neurolipocytoma
  • Medullocytoma
  • M9507/0 Pacinian tumor

    M9508/3 Atypical teratoid/rhabdoid tumor

    M9510/0 Retinocytoma

    M9510/3 Retinoblastoma, NOS

    M9511/3 Retinoblastoma, differentiated

    M9512/3 Retinoblastoma, undifferentiated

    M9513/3 Retinoblastoma, diffuse

    M9514/1 Retinoblastoma, spontaneously regressed

    M9520/3 Olfactory neurogenic tumor

    M9521/3 Olfactory neurocytoma

  • Esthesioneurocytoma
  • M9522/3 Olfactory neuroblastoma

  • Esthesioneuroblastoma
  • M9523/3 Olfactory neuroepithelioma

  • Esthesio neuroepithelioma
  • 953 Meningiomas

    M9530/0 Meningioma, NOS

  • Microcystic
  • Secretory
  • Lymphoplasmacyte-rich
  • Metaplastic
  • M9530/1 Meningiomatosis, NOS

  • Diffuse
  • Multiple meningiomas
  • M9530/3 Meningioma, malignant

  • Anaplastic
  • Leptomeningeal sarcoma
  • Meningeal sarcoma
  • Meningothelial sarcoma
  • M9531/0 Meningothelial meningioma

  • Endotheliomatous meningioma
  • Syncytial meningioma
  • M9532/0 Fibrous meningioma

  • Fibroblastic meningioma
  • M9533/0 Psammomatous meningioma

    M9534/0 Angiomatous meningioma

    M9537/0 Transitional meningioma

    M9538/1 Clear cell meningioma

  • Chordoid
  • M9538/3 Papillary meningioma

  • Rhabdoid
  • M9539/1 Atypical meningioma

    M9539/3 Meningeal sarcomatosis

    954–957 Nerve sheath tumors

    M9540/0 Neurofibroma, NOS

    M9540/1 Neurofibromatosis, NOS

  • Multiple neurofibromatosis
  • Von Recklinghausen disease (except of bone)
  • M9540/3 Malignant peripheral nerve sheath tumor

  • MPNST, NOS
  • MPNST with glandular differentiation
  • Epithelioid
  • with mesenchymal differentiation
  • Melanotic
  • Melanotic psammomatous
  • M9541/0 Melanotic neurofibroma

    M9550/0 Plexiform neurofibroma

  • Plexiform neuroma
  • M9560/0 Neurilemoma, NOS

  • Schwannoma, NOS
  • Neurinoma
  • Acoustic neuroma
  • Pigmented or melanotic schwannoma
  • Plexiform / cellular / degenerated / ancient / psammomatous
  • M9560/1 Neurinomatosis

    M9561/3 Malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation

  • MPNST with rhabdomyoblastic differentiation
  • Triton tumor, malignant
  • Malignant schwannoma with rhabdomyoblastic differentiation
  • M9562/0 Neurothekeoma

  • Nerve sheath myxoma
  • M9570/0 Neuroma, NOS

    M9571/0 Perineurioma, NOS

  • Intraneural perineurioma
  • Soft tissue perineurioma
  • M9571/3 Perineurioma, malignant

  • Perineural MPNST
  • M9560/0 Schwannoma, NOS

    M9560/0 Neurinoma

    M9560/0 Acoustic neuroma

    M9570/0 Neuroma, NOS

    958 Granular cell tumors and Alveolar soft part sarcoma

    M9580/0 Granular cell tumor/myoblastoma, NOS

    M9580/3 Granular cell tumor/myoblastoma, malignant

    M9581/3 Alveolar soft part sarcoma

    M9582/0 Granular cell tumor of the sellar region (C75.1)

    959 Malignant lymphoma, NOS, Or diffuse

    M9590/3 Malignant Lymphoma, NOS

  • Lymphoma, NOS
  • Microglioma (C71._)
  • M9591/3 Malignant lymphoma, non-Hodgkin, NOS

  • Non-Hodgkin's lymphoma, NOS
  • B cell lymphoma, NOS
  • Malignant lymphoma, non-cleaved cell, NOS
  • Malignant lymphoma, diffuse, NOS
  • Malignant lymphoma, lymphocytic, intermediate differentiation, nodular
  • Malignant lymphoma, small cell, noncleaved, diffuse
  • Malignant lymphoma, undifferentiated cell, non-Burkitt
  • Malignant lymphoma, undifferentiated cell type, NOS
  • Lymphosarcoma, NOS
  • Lymphosarcoma, diffuse
  • Reticulum cell sarcoma, NOS
  • Reticulum cell sarcoma, diffuse
  • Reticulosarcoma, NOS
  • Reticulosarcoma, diffuse
  • Malignant lymphoma, small cleaved cell, diffuse
  • Malignant lymphoma, lymphocytic, poorly differentiated, diffuse
  • Malignant lymphoma, small cleaved cell, NOS
  • Malignant lymphoma, cleaved cell, NOS
  • M9596/3 Composite Hodgkin and non-Hodgkin lymphoma

    965–966 Hodgkin Lymphoma

    M9650/3 Hodgkin lymphoma, NOS

  • Hodgkin's disease, NOS
  • Malignant lymphoma, Hodgkin
  • M9651/3 Hodgkin lymphoma, lymphocyte rich

  • Lymphocyte-rich classical Hodgkin lymphoma
  • Hodgkin disease, lymphocyte predominance, NOS
  • Hodgkin disease, lymphocytic-histiocytic predominance
  • Hodgkin disease, lymphocyte predominance, diffuse
  • M9652/3 Mixed cellularity classical Hodgkin lymphoma, NOS

  • Hodgkin lymphoma, mixed cellularity, NOS
  • M9653/3 Lymphocyte-depleted classical Hodgkin lymphoma, NOS

    M9654/3 Hodgkin lymphoma, lymphocyte depletion, diffuse fibrosis

    M9655/3 Hodgkin lymphoma, lymphocyte depletion, reticular

    M9659/3 Nodular lymphocyte predominant Hodgkin lymphoma

  • Hodgkin lymphoma, lymphocyte predominance, nodular
  • Hodgkin paragranuloma, NOS
  • Hodgkin paragranuloma, nodular
  • M9661/3 Hodgkin granuloma

    M9662/3 Hodgkin sarcoma

    M9663/3 Nodular sclerosis classical Hodgkin lymphoma

  • Hodgkin lymphoma, nodular sclerosis, NOS
  • M9664/3 Hodgkin lymphoma, nodular sclerosis, cellular phase

  • Classical Hodgkin lymphoma, nodular sclerosis, cellular phase
  • M9665/3 Hodgkin lymphoma, nodular sclerosis, grade 1

  • Classical Hodgkin lymphoma, nodular sclerosis grade 1
  • Hodgkin disease, nodular sclerosis, lymphocyte predominance
  • Hodgkin disease, nodular sclerosis, mixed cellularity
  • M9667/3 Hodgkin lymphoma, nodular sclerosis, grade 2

  • Classical Hodgkin lymphoma, nodular sclerosis, grade 2
  • Hodgkin disease, nodular sclerosis, lymphocyte depletion
  • Hodgkin disease, nodular sclerosis, syncytial variant
  • 967-969 Mature B-cell Lymphomas

    M9670/3 Malignant lymphoma, small B lymphocytic, NOS (see also M9823/3)

  • Small lymphocytic lymphoma
  • Malignant lymphoma, small lymphocytic, NOS
  • Malignant lymphoma, lymphocytic, well differentiated, diffuse
  • Malignant lymphoma, lymphocytic, NOS
  • Malignant lymphoma, lymphocytic, diffuse, NOS
  • Malignant lymphoma, small cell, NOS
  • Malignant lymphoma, small lymphocytic, diffuse
  • Malignant lymphoma, small cell diffuse
  • M9671/3 Malignant lymphoma, lymphoplasmacytic (see also M9761/3)

  • Lymphoplasmacytic lymphoma
  • Malignant lymphoma, lymphoplasmacytoid
  • Immunocytoma
  • Malignant lymphoma, plasmacytoid
  • Plasmacytic lymphoma
  • M9673/3 Mantle cell lymphoma

  • Includes all variants: blastic, pleomorphic, small cell
  • Mantle zone lymphoma
  • Malignant zone lymphoma
  • Malignant lymphoma, lymphocytic, intermediate differentiation, diffuse
  • Malignant lymphoma, centrocytic
  • Malignant lymphomatous polyposis
  • M9675/3 Malignant lymphoma, mixed small and large cell, diffuse (see also M9690/3)

  • Malignant lymphoma, mixed lymphocytic-histiocytic, diffuse
  • Malignant lymphoma, mixed cell type, diffuse
  • Malignant lymphoma, centroblastic-centrocytic,NOS
  • Malignant lymphoma, centroblastic-centrocytic, diffuse
  • M9678/3 Primary effusion lymphoma

    M9679/3 Mediastinal large B-cell lymphoma (C38.3)

  • Mediastinal (thymic) large cell lymphoma
  • M9680/3 Malignant lymphoma, large B-cell, diffuse, NOS

  • Diffuse large B-cell lymphoma, NOS
  • Malignant lymphoma, large cell, NOS
  • Malignant lymphoma, large B-cell, NOS
  • Malignant lymphoma, histiocytic, NOS
  • Malignant lymphoma, histiocytic, diffuse
  • Malignant lymphoma, large cell, cleaved and noncleaved
  • Malignant lymphoma, large cell, diffuse, NOS
  • Malignant lymphoma, large cleaved cell, NOS
  • Malignant lymphoma, large cell, cleaved, NOS
  • Malignant lymphoma, large cell, noncleaved, diffuse or NOS
  • Malignant lymphoma, large B-cell, diffuse, centroblastic, NOS
  • Malignant lymphoma, large B-cell, centroblastic, NOS or diffuse
  • Intravascular large B-cell lymphoma
  • Angioendotheliomatosis
  • Angiotropic lymphoma
  • T-cell rich large B-cell lymphoma
  • Histiocyte-rich large B-cell lymphoma
  • Anaplastic large B-cell lymphoma
  • M9684/3 Malignant lymphoma, large B-cell, diffuse, immunoblastic, NOS

  • Malignant lymphoma, immunoblastic, NOS
  • Immunoblastic sarcoma
  • Malignant lymphoma, large cell, immunoblastic
  • Plasmablastic lymphoma
  • M9687/3 Burkitt lymphoma, NOS (see also M9826/3)

  • Includes all variants
  • Malignant lymphoma, undifferentiated
  • Malignant lymphoma, small noncleaved
  • Burkitt-like lymphoma
  • M9689/3 Splenic marginal zone lymphoma

  • Splenic marginal zone B-cell lymphoma
  • Splenic lymphoma with villous lymphocytes
  • M9690/3 Follicular lymphoma, NOS (see also M9675/3)

  • Malignant lymphoma, follicular/follicle center, NOS
  • M9691/3 Follicular lymphoma, grade 2

  • Follicular lymphoma, small cleaved cell
  • M9698/3 Follicular lymphoma, grade 3

  • Malignant lymphoma, large cell/centroblastic, follicular, NOS
  • M9699/3 Marginal zone B-cell lymphoma, NOS

  • Marginal zone lymphoma, NOS
  • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue (MALT-lymphoma)
  • BALT lymphoma
  • SALT lymphoma
  • Monocytoid b-cell lymphoma
  • Nodal marginal zone lymphoma
  • Nodal marginal zone B-cell lymphoma
  • 970–971 Mature T- and NK-cell Lymphomas

    M9700/3 Mycosis fungoides

  • Pagetoid reticulosis
  • M9701/3 Sezary syndrome

  • Sezary disease
  • M9702/3 Mature T-cell lymphoma, NOS

  • Peripheral T-cell lymphoma, NOS
  • T-cell lymphoma, NOS
  • Peripheral T-cell lymphoma, pleomorphic small/medium/large cell/T-zone lymphoma
  • Lymphoepithelioid lymphoma
  • Lennert lymphoma
  • M9705/3 Angioimmunoblastic T-cell lymphoma

  • Peripheral T-cell lymphoma, AILD (Angioimmunoblastic lymphadenopathy with dysproteinemia)
  • M9708/3 Subcutaneous panniculitis-like T-cell lymphoma

    M9709/3 Cutaneous T-cell lymphoma, NOS (C44._)

  • Cutaneous lymphoma, NOS
  • M9714/3 Anaplastic large cell lymphoma, T cell and Null cell type

  • Anaplastic large cell lymphoma, CD30+/NOS
  • M9716/3 Hepatosplenic (gamma-delta) cell lymphoma

  • Hepatosplenic T-cell lymphoma
  • M9717/3 Intestinal T-cell lymphoma

  • Enteropathy type T-cell lymphoma
  • M9718/3 Primary cutaneous CD 30+ T-cell lymphoproliferative disorder (C44._)

  • Lymphomatoid papulosis
  • Primary cutaneous anaplastic large cell lymphoma
  • Primary cutaneous CD30+ large T-cell lymphoma
  • M9719/3 NK/T-cell lymphoma, nasal and nasal type

  • Extranodal NK/T cell lymphoma, nasal type
  • T/NK-cell lymphoma
  • 972 Precursor Cell Lymphoblastic Lymphoma

    M9727/3 Precursor cell lymphoblastic lymphoma, NOS (see also M9835/3)

  • Blastic NK cell lymphoma
  • Malignant lymphoma, lymphoblastic, NOS
  • M9728/3 Precursor B-cell lymphoblastic Lymphoma (see also M9836/3)

    M9729/3 Precursor T-cell lymphoblastic Lymphoma (see also M9837/3)

    973 Plasma cell tumors

    M9731/3 Plasmacytoma, NOS

  • Extramedullary plasmacytoma
  • Solitary plasmacytoma of bone (C40._, C41._)
  • Solitary myeloma
  • Solitary plasmacytoma
  • M9732/3 Multiple myeloma (C42.1)

  • Plasma cell myeloma
  • Myeloma, NOS
  • Myelomatosis
  • M9733/3 Plasma cell leukemia (C42.1)

  • Plasmacytic leukemia
  • M9734/3 Plasmacytoma, extramedullary (not occurring in bone)

  • Extraosseous plasmacytoma
  • 974 Mast cell Tumors

    M9740/1 Mastocytoma, NOS or Extracutaneous mastocytoma

  • Mast cell tumor, NOS
  • M9740/3 Mast cell sarcoma

  • Malignant mast cell tumor
  • Malignant mastocytoma
  • M9741/3 Malignant mastocytosis

  • Systemic tissue mast cell disease
  • Aggressive systemic mastocytosis or Systemic mastocytosis with associated clonal, hematological non-mast cell lineage disease
  • M9742/3 Mast cell leukemia (C42.1)

    975 Neoplasms of Histiocytes and Accessory Lymphoid Cells

    M9750/3 Malignant histiocytosis

    M9751/1 Langerhans cell histiocytosis, NOS

    M9752/1 Langerhans cell histiocytosis, unifocal

  • Langerhans cell granulomatosis, unifocal
  • Langerhans cell histiocytosis, mono-ostotic
  • Eosinophilic granuloma
  • M9753/1 Langerhans cell histiocytosis, multifocal

  • Langerhans cell histiocytosis, poly-ostotic
  • M9754/3 Langerhans cell histiocytosis, disseminated

  • Langerhans cell histiocytosis, generalized
  • Letterer-Siwe disease
  • Acute progressive histiocytosis X
  • M9755/3 Histiocytic sarcoma

  • True histiocytic lymphoma
  • M9756/3 Langerhans cell sarcoma

    M9757/3 Dendritic cell sarcoma, NOS

  • Interdigitating dendritic cell sarcoma/tumor
  • M9758/3 Follicular dendritic cell sarcoma/tumor

    976 Immunoproliferative diseases

    M9760/3 Immunoproliferative disease, NOS

    M9761/3 Waldenstrom macroglobulinemia (C42.0) (see also M9671/3)

    M9762/3 Heavy chain disease, NOS

  • Alpha heavy chain disease
  • Mu heavy chain disease
  • Gamma heavy chain disease
  • Franklin disease
  • M9764/3 Immunoproliferative small intestinal disease (C17._)

  • Mediterranean lymphoma
  • M9765/1 Monoclonal gammopathy of undetermined significance

  • MGUS
  • Monoclonal gammopathy, NOS
  • (M9766/1) Angiocentric immunoproliferative lesion

  • LYmphoid granulomatosis
  • Lymphomatoid granulomatosis
  • M9767/1 Angioimmunoblastic lymphadenopathy

    M9768/1 T-gamma lymphoproliferative disease

    M9769/1 Immunoglobulin deposition disease

  • Systemic light chain disease
  • Primary amyloidosis
  • 980) Leukemias, NOS

    M9800/3 Leukemia, NOS

    M9801/3 Acute leukemia, NOS

  • Blast cell leukemia
  • Undifferentiated leukemia
  • Stem cell leukemia
  • M9805/3 Acute biphenotypic leukemia

  • Acute leukemia of ambiguous lineage
  • Acute mixed lineage leukemia
  • Acute bilineal leukemia
  • (982–983) Lymphoid leukemias (C42.1)

    M9820/3 Lymphoid leukemia, NOS

  • Lymphocytic leukemia, NOS
  • Lymphatic leukemia, NOS
  • M9823/3 B-cell chronic lymphocytic leukemia/small lymphocytic lymphoma (see also M9670/3)

  • Chronic lymphocytic leukemia, B-cell type (includes all variants of BCLL)
  • Chronic lymphocytic leukemia
  • Chronic lymphoid leukemia
  • Chronic lymphatic leukemia
  • M9826/3 Burkitt cell Leukemia (see also M9687/3)

  • Acute lymphoblastic leukemia, mature B-cell type
  • M9827/3 Adult T-cell leukemia/lymphoma (HTLV-1 positive) includes all variants

  • Adult T-cell lymphoma/leukemia
  • M9831/1 T-cell large granular lymphocytic leukemia

  • T-cell large granular lymphocytosis
  • NK-cell large granular lymphocytic leukemia
  • Large granular lymphocytosis, NOS
  • M9832/3 Prolymphocytic leukemia, NOS

    M9833/3 B-cell prolymphocytic leukemia

    M9834/3 T-cell prolymphocytic leukemia

    M9835/3 Precursor cell lymphoblastic leukemia, NOS (see also M9727/3)

  • Precursor cell lymphoblastic leukemia, not phenotyped
  • Acute lymphoblastic leukemia, NOS (see also M9727/3)
  • Acute lymphoblastic leukemia, precursor-cell type
  • Acute lymphoblastic leukemia-lymphoma, NOS
  • Acute lymphocytic leukemia
  • Acute lymphoid leukemia
  • Acute lymphatic leukemia
  • Acute lymphoblastic leukemia, L2 type, NOS
  • FAB L2
  • M9836/3 Precursor B lymphoblastic leukemia (see also M9728/3)

  • Pro-B ALL
  • Common precursor B ALL
  • Pre-B ALL
  • Pre-pre-B ALL
  • Common ALL
  • c-ALL
  • M9837/3 Precursor T lymphoblastic leukemia (see also M9729/3)

  • Pro-T ALL
  • Pre-T ALL
  • Cortical T ALL
  • Mature T ALL
  • 984-993 Myeloid Leukemias (C42.1)

    (9840–9849) Erythroleukemias (FAB-M6)

    M9840/3 Acute myeloid leukemia, M6 type

  • Acute erythroid leukemia
  • Erythroleukemia
  • FAB M6
  • AML M6
  • Erythremic myelosis, NOS
  • (9850–9859) Lymphosarcoma cell leukemia (9860–9869) Myeloid (Granulocytic) Leukemias

    M9860/3 Myeloid leukemia, NOS

  • Non-lymphocytic leukemia, NOS
  • Granulocytic leukemia, NOS
  • Myelogenous leukemia, NOS
  • Myelomonocytic leukemia, NOS
  • Myelocytic leukemia, NOS
  • Eosinophilic leukemia
  • Monocytic leukemia, NOS
  • M9861/3 Acute myeloid leukemia, NOS (FAB or WHO type not specified (see also M9930/3)

  • Acute myelogenous leukemia
  • Acute non-lymphocytic leukemia
  • Acute granulocytic leukemia
  • Acute myelogenous leukemia
  • Acute myelocytic leukemia
  • M9863/3 Chronic myeloid leukemia, NOS

  • Chronic myelogenous leukemia, NOS
  • Chronic granulocytic leukemia, NOS
  • Chronic myelocytic leukemia, NOS
  • M9866/3 Acute promyelocytic leukemia t(15;17)(q22;q11-12) * Acute promyelocytic leukemia, PML/RAR-alpha

  • Acute myeloid leukemia, t(15:17(q22;q11-12)
  • Acute promyelocytic leukemia, NOS
  • FAB-M3 (includes all variants)

  • Acute promyelocytic leukemia (AML with t(15;17)(q22;q12), PML-RARa and variants)
  • M9867/3) Acute myelomonocytic leukemia

  • Acute myelomonocytic leukemia
  • FAB-M4
  • M9870/3 Basophilic leukemia or Acute basophilic leukemia

    M9871/3 Acute myeloid leukemia with abnormal marrow eosinophils (includes all variants)

  • AML with inv(16)(p13q22) or t(16;16)(p13;q22), CBFb/MYH11 (FAB M4Eo)
  • M9872/3 Acute myeloid leukemia, minimally differentiated (FAB type M0)

  • Acute myeloblastic leukemia]
  • M9873/3 Acute myeloid leukemia, without maturation (FAB type M1)

    M9874/3 Acute myeloid leukemia, with maturation (FAB M2), NOS

    M9875/3 Chronic myelogenous leukemia BCR/ABL positive

  • Philadelphia chromosome (Ph1 positive)
  • t(9;22)(q34;q11)
  • Chronic granulocytic leukemia (BCR/ABL positive)/(Ph1 positive)/t(9;22)(q34;q11)
  • M9876/3 Atypical chronic myelogenous leukemia BCR/ABL negative

  • Atypical chronic myeloid leukemia (BCR/ABL negative)/(Ph1 negative)
  • M9891/3 Acute monoblastic and monocytic leukemia

  • Monoblastic leukemia, NOS
  • FAB M5 (includes all variants)
  • M9895/3 Acute myeloid leukemia multilineage dysplasia

  • AML with/without prior myelodysplastic syndrome
  • M9896/3 AML with t(8;21)(q22;q22), AML1/ETO

  • FAB M2 with t(8;21)(q22;q22), AML1/ETO
  • M9897/3 AML with 11q23 (MLL) abnormalities

  • AML, MLL
  • M9910/3 Acute megakaryoblastic leukemia, NOS

  • Megakaryocytic leukemia
  • (FAB-M7)
  • M9920/3 Acute myeloid leukemia and myelodysplastic syndrome, therapy related, NOS Therapy-related acute myeloid leukemia, alkylating agent/epipodophyllotoxin related

    M9930/3 Chloroma or Myeloid sarcoma (see also M9861/3)

  • Granulocytic sarcoma
  • M9931/3) Acute panmyelosis with myelofibrosis (C42.1)

  • Acute panmyelosis, NOS
  • Acute myelofibrosis
  • Acute myelosclerosis, NOS
  • 994 Other Leukemias (C42.1)

    M9940/3 Hairy cell leukemia (C42.1)

  • Hairy cell leukemia variant
  • Leukemic reticuloendotheliosis
  • M9945/3 Chronic myelomonocytic, leukemia, NOS

  • Type 1
  • Type 2
  • M9946/3 Juvenile myelomonocytic leukemia

    M9948/3 Aggressive NK cell leukemia

    995-996 Chronic Myeloproliferative Disorders (C42.1)

    M9950/3 Polycythemia vera

  • Polycythemia rubra vera
  • Proliferative polycythemia
  • M9960/1 Chronic Myeloproliferative disease, NOS

    M9961/3 Myelosclerosis with myeloid metaplasia

  • Chronic idiopathic myelofibrosis
  • Myelofibrosis as a result of myeloproliferative disease
  • Agnogenic myeloid metaplasia
  • Megakaryocytic myelosclerosis
  • Myelofibrosis with myeloid metaplasia
  • M9962/3 Essential thrombocytemia

  • Idiopathic thrombocythemia
  • Essential/idiopathic hemorrhagic thrombocythemia
  • M9963/3 Chronic neutrophilic leukemia

    M9964/3 Chronic eosinophilic leukemia / hypereosinophilic syndrome

    997 Other Haematologic Disorders

    M9970/1 Lymphoproliferative disease/disorder, NOS

  • Post-transplant lymphoproliferative disorder, pleomorphic
  • M9775/1 Myeloproliferative disease, NOS

  • Chronic Myeloproliferative disease, unclassifiable
  • Myelodysplastic / myeloproliferative diseases, unclassifiable
  • 998 Myelodysplastic syndrome (C42.1)

    M9980/3 Chronic myelomonocytic leukemia or Refractory anemia

    M9982/3 Refractory anemia with ringed sideroblasts

  • with sideroblasts
  • M9983/3 Refractory anemia with excess blasts

  • RAEB
  • RAEB I
  • RAEB II
  • M9985/3 Refractory cytopenia with multilineage dysplasia

    M9986/3 Myelodysplastic syndrome associated with isolated del(5q) chromosome abnormality

    M9989/3 Myelodysplastic syndrome, NOS

    References

    International Classification of Diseases for Oncology Wikipedia


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