The classification has two axes: topography and morphology.
The morphology axis is for the shape and structure of the tumor.
This axis has particular importance because the Systematized Nomenclature of Medicine ("SNOMED") has adopted the ICD-O classification of morphology. SNOMED has been changing continuously, and several different versions of SNOMED are in use. Accordingly, mapping of ICD-O codes to SNOMED requires careful assessment of whether entities are indeed true matches.
The topography axis is for of the tumor's site in the body. It is standardized with the C section of ICD-10.
There were no changes in the topography axis between ICD-O-2 and ICD-O-3.
See List of ICD-10 codes#(C00–C97) Malignant Neoplasms for examples.
/0 Benign/1 Uncertain whether benign or malignantBorderline malignancyLow malignant potentialUncertain malignant potential/2 Carcinoma in situIntraepithelialNoninfiltratingNoninvasive/3 Malignant, primary site/6 Malignant, metastatic siteMalignant, secondary site/9 Malignant, uncertain whether primary or metastatic siteM8000/0 Neoplasm, benign
Tumor, benignUnclassified tumor, benignM8000/1 Neoplasm, uncertain whether benign or malignant
Neoplasm, NOSTumor, NOSUnclassified tumor, uncertain whether benign or malignantUnclassified tumor, borderline malignancyM8000/3 Neoplasm, malignant
Tumor, malignant, NOSMalignancyCancerUnclassified tumor, malignantBlastoma, NOSM8000/6 Neoplasm, metastatic
Neoplasm, metastaticTumor, metastaticTumor, secondaryTumor embolusM8000/9 Neoplasm, malignant, uncertain whether primary or metastatic
Unclassified tumor, malignant, uncertain whether primary or metastaticM8001/0 Tumor cells, benign
M8001/1 Tumor cells, uncertain whether benign or malignant
Tumor cells, NOSM8001/3 Tumor cells, malignant
M8002/3 Malignant tumor, small cell type
M8003/3 Malignant tumor, giant cell type
M8004/3 Malignant tumor, spindle cell type
Malignant tumor, fusiform cell typeM8005/0 Clear cell tumor, NOS
M8005/3 Malignant tumor, clear cell type
M8010/0 Epithelial tumor, benignM8010/2 Carcinoma in situ, NOSIntraepithelial carcinoma, NOSM8010/3 Carcinoma, NOSEpithelial tumor, malignantM8010/6 Carcinoma, metastatic, NOSSecondary carcinomaM8010/9 CarcinomatosisM8011/0 Epithelioma, benignM8011/3 Epithelioma, malignantEpithelioma, NOSM8012/3 Large cell carcinoma, NOSM8013/3 Large cell neuroendocrine carcinomaM8014/3 Large cell carcinoma with rhabdoid phenotypeM8015/3 Glassy cell carcinomaM8020/3 Carcinoma, undifferentiated, NOSM8021/3 Carcinoma, anaplastic, NOSM8022/3 Pleomorphic carcinomaM8030/3 Giant cell and spindle cell carcinomaM8031/3 Giant cell carcinomaM8032/3 Spindle cell carcinoma, NOSM8033/3 Pseudosarcomatous carcinomaSarcomatoid carcinomaM8034/3 Polygonal cell carcinomaM8035/3 Carcinoma with osteoclast-like giant cellsM8040/0 Tumorlet, benignM8040/1 Tumorlet, NOSM8041/3 Small cell carcinoma, NOSReserve cell carcinomaRound cell carcinomaSmall cell neuroendocrine carcinomaM8042/3 Oat cell carcinoma (C34._)M8043/3 Small cell carcinoma, fusiform cellM8044/3 Small cell carcinoma, intermediate cellM8045/3 Combined small cell carcinomaMixed small cell carcinomaCombined small cell-large cell carcinomaCombined small cell-adenocarcinomaCombined small cell-squamous cell carcinomaM8046/3 Non-small cell carcinoma (C34._)M8050/0 Papilloma, NOS (except papilloma of bladder M8120/1)M8050/2 Papillary carcinoma in situM8050/3 Papillary carcinoma, NOSM8051/0 Verrucous papillomaM8051/3 Verrucous carcinoma, NOSCondylomatous carcinomaVerrucous squamous cell carcinomaVerrucous epidermoid carcinomaWarty carcinomaM8052/0 Squamous cell papilloma, NOSSquamous papillomaKeratotic papillomaM8052/2 Papillary squamous cell carcinoma, non-invasivePapillary squamous cell carcinoma in situM8052/3 Papillary squamous cell carcinomaPapillary epidermoid carcinomaM8053/0 Squamous cell papilloma, invertedM8060/0 Squamous papillomatosisPapillomatosis, NOSM8070/2 Squamous cell carcinoma in situ, NOSEpidermoid carcinoma in situ, NOSIntraepidermal carcinoma, NOSIntraepithelial squamous cell carcinomaM8070/3 Squamous cell carcinoma, NOSEpidermoid carcinoma, NOSSquamous carcinomaSquamous cell epitheliomaM8070/6 Squamous cell carcinoma, metastatic, NOSM8071/3 Squamous cell carcinoma, keratinizing, NOSSquamous cell carcinoma, large cell, keratinizingEpidermoid carcinoma, keratinizingM8072/3 Squamous cell carcinoma, large cell, nonkeratinizing, NOSSquamous cell carcinoma, non keratinizing, NOSEpidermoid carcinoma, large cell, nonkeratinizingM8073/3 Squamous cell carcinoma, small cell, nonkeratinizingEpidermoid carcinoma, small cell, nonkeratinizingM8074/3 Squamous cell carcinoma, spindle cellEpidermoid carcinoma, spindle cellSquamous cell carcinoma, sarcomatoidM8075/3 Squamous cell carcinoma, adenoidSquamous cell carcinoma, pseudoglandularSquamous cell carcinoma, acantholyticM8076/2 Squamous cell carcinoma in situ with questionable stromal invasionEpidermoid carcinoma in situ with questionable stromal invasionM8076/3 Squamous cell carcinoma, microinvasiveM8077/2 Squamous intraepithelial neoplasia, grade IIICervical intraepithelial neoplasia, grade III (C53._)CIN III, NOS (C53._)CIN III with severe dysplasia (C53._)Vaginal intraepithelial neoplasia, grade III (C52._)VAIN III (C52._)Vulvar intraepithelial neoplasia, grade III (C51._)VIN III (C51._)Anal intraepithelial neoplasia, grade III (C21.1)AIN III (C21.1)M8078/3 Squamous cell carcinoma with horn formationM8080/2 Queyrat erythroplasia (C60._)M8081/2 Bowen disease (C44._)Intraepidermal squamous cell carcinoma, Bowen type (C44._)M8082/3 Lymphoepithelial carcinomaLymphoepitheliomaLymphoepithelioma-like carcinomaSchmincke tumor (C11._)M8083/3 Basaloid squamous cell carcinomaM8084/3 Squamous cell carcinoma, clear cell typeM8090/1 Basal cell tumor (C44._)(M8090/3) Basal cell carcinoma, NOS (C44._)Basal cell epitheliomaRodent ulcerPigmented basal cell carcinomaM8091/3 Multifocal superficial basal cell carcinoma (C44._)Multicentric basal cell carcinomaM8092/3 Infriltrating basal cell carcinoma, NOS (C44._)Infiltrating basal cell carcinoma, non-sclerosingInfiltrating basal cell carcinoma, sclerosingBasal cell carcinoma, morpheicBasal cell carcinoma, desmoplastic typeM8093/3 Basal cell carcinoma, fibroepithelial (C44._)Fibroepithelioma of Pinkus typeFibroepithelial basal cell carcinoma, Pinkus typePinkus tumorFibroepithelioma, NOSM8094/3 Basosquamous carcinoma (C44._)Mixed basal-squamous cell carcinomaM8095/3 Metatypical carcinomaM8096/0 Intraepidermal epithelioma of Jadassohn (C44._)M8097/3 Basal cell carcinoma, nodular (C44._)Basal cell carcinoma, micronodularM8098/3 Adenoid basal carcinoma (C53._)M8100/0 Trichoepithelioma (C44._)Brooke tumorEpithelioma adenoides cysticumM8101/0 Trichofolliculoma (C44._)M8102/0 Trichilemmoma (C44._)M8102/3 Trichilemmocarcinoma (C44._)Trichilemmal carcinomaM8103/0 Pilar tumor (C44._)Proliferating trichilemmal cystProliferating trichilemmal tumorM8110/0 Pilomatrixoma, NOS (C44._)Calcifying epithelioma of MalherbePilomatricoma, NOSM8110/3 Pilomatrix carcinoma (C44._)Pilomatrixoma, malignantPilomatricoma, malignantMatrical carcinoma812-813 Transitional cell Papillomas And Carcinomas
M8120/0 Transitional cell papilloma, benignTransitional papillomaM8120/1 Urothelial papilloma, NOSPapilloma of baldder (C67._)Transitional cell papilloma, NOSM8120/2 Transitional cell carcinoma in situUrothelial carcinoma in situM8120/3 Transitional cell carcinoma, NOSUrothelial carcinoma, NOSTransitional carcinomaM8121/0 Schneiderian papilloma, NOS (C30.0, C31._)Sinonasal papilloma, NOSSinonasal papilloma, exophyticSinonasal papilloma, fungiformTransitional cell papilloma, inverted, benignTransitional papilloma, inverted, benignM8121/1 Transitional cell papilloma, inverted, NOSTransitional papilloma, inverted, NOSSchneiderian papilloma, invertedColumnar cell papillomaCylindrical cell papillomaOncocytic Schneiderian papillomaM8121/3 Schneiderian carcinoma (C30.0, C31._)Cylindrical cell carcinomaM8122/3 Transitional cell carcinoma, spindle cellTransitional cell carcinoma, sarcomatoidM8123/3 Basaloid carcinomaM8124/3 Cloacogenic carcinoma (C21.2)M8130/1 Papillary transitional cell neoplasm of low malignant potential (C67._)Papillary urothelial neoplasm of low malignant potentialM8130/2 Papillary transitional cell carcinoma, non-invasive (C67._)Papillary urothelial carcinoma, non-invasiveM8130/3 Papillary transitional cell carcinoma (C67._)Papillary urothelial carcinomaM8131/3 Transitional cell carcinoma, micropapillary ( C67._)814–838 Adenomas And Adenocarcinomas
(M8140/0) Adenoma, NOSM8140/1 Atypical adenomaBronchial adenoma, NOS (C34._)M8140/2 Adenocarcinoma in situ, NOS(M8140/3) Adenocarcinoma, NOSM8140/6 Adenocarcinoma, metastatic, NOSM8141/3 Scirrhous adenocarcinomaScirrhous carcinomaCarcinoma with productive fibrosis(M8142/3) Linitis plastica (C16._)M8143/3 Superficial spreading adenocarcinomaM8144/3 Adenocarcinoma, intestinal type (C16._)Carcinoma, intestinal typeM8145/3 Carcinoma, diffuse type (C16._)Adenocarcinoma, diffuse typeM8146/0 Monomorphic adenomaM8147/0 Basal cell adenomaM8147/3 Basal cell adenocarcinomaM8148/2 Glandular intraepithelial neoplasia, grade IIIProstatic intraepithelial neoplasia, grade III (C61.9)PIN IIIM8149/0 Canalicular adenomaM8150/0 Islet cell adenoma (C25._)Islet cell tumor, benignNesidioblastomaIslet cell adeomatosisM8150/1 Islet cell tumor, NOS (C25._)M8150/3 Islet cell carcinoma (C25._)Islet cell adenocarcinoma(M8151/0) Insulinoma, NOS (C25._)Beta cell adenomaM8151/3 Insulinoma, malignant (C25._)Beta cell tumor, malginant(M8152/0) Glucagonoma, NOS (C25._)Alpha cell tumor, NOSM8152/3 Glucagonoma, malignant (C25._)Alpha cell tumor, malignant(M8153/1) Gastrinoma, NOSG cell tumor, NOSGastrin cell tumorM8153/3 Gastinoma, malignantG cell tumor, malignantGastrin cell tumor, malignantM8154/3 Mixed islet cell and exocrine adenocarcinoma (C25._)Mixed acinar-endocrine carcinomaMixed ductal-endocrine carcinomaM8155/1 Vipoma, NOS(M8155/3) Vipoma, malignantM8156/1 Somatostatinoma, NOSSomatostatin cell tumor, NOSM8156/3 Somatostatinoma, malignantsomatostatin cell tumor, malignantM8157/1 Enteroglucagonoma, NOSM8157/3 Enteroglucagonoma, malignantM8160/0 Bile duct adenoma (C22.1, C24.0)Cholangioma(M8160/3) Cholangiocarcinoma (C22.1, C24.0)Bile duct carcinomaBile duct adenocarcinomaM8161/0 (C22.1, C24.0)M8161/3 Bile duct cystadenocarcinoma (C22.1, C24.0)M8162/3 Klatskin tumor (C22.1, C24.0)M8170/0 Liver cell adenoma (C22.0)(M8170/3) Hepatocellular carcinoma, NOS (C22.0)Liver cell carcinomaHepatocarcinomaHepatoma, malignantHepatoma, NOSM8171/3 Hepatocellular carcinoma, fibrolamellar (C22.0)M8172/3 Hepatocellular carcinoma, scirrhous (C22.0)Sclerosing hepatic carcinomaM8173/3 Hepatocellular carcinoma, spindle cell variant (C22.0)Hepatocellular carcinoma, sarcomatoidM8174/3 Hepatocellular carcinoma, clear cell type (C22.0)M8175/3 Hepatocellular carcinoma, pleomorphic typeM8180/3 Combined hepatocellular carcinoma and cholangiocarcinoma (C22.0)Mixed hepatocellular and bilde duct carcinomaHepatocholangiocarcinomaM8190/0 Trabecular adenomaM8190/3 Trabecular adenocarcinomaTrabecular carcinomaM8191/0 Embryonal adenomaM8200/0 Eccrine dermal cylindroma (C44._)Turban tumorCylindroma of skin(M8200/3) Adenoid cystic carcinomaAdenocystic carcinomaCylindroma, NOS (except cylindroma of skin M8200/0)Adenocarcinoma, cylindroidBronchial adenoma, cylindroid (C34._)M8201/2 Cribiform carcinoma in situ (C50._)Ductal carcinoma in situ, cribiform typeM8201/3 Cribiform carcinoma, NOSDuctal carcinoma, cribiform typeM8202/0 Microcystic adenoma (C25._)M8204/0 Lactating adenomaM8210/0 Adenomatous polyp, NOSPolypoid adenomaM8210/2 Adenocarcinoma in situ in adenomatous polypAdenocarcinoma in situ in tublar adenomaCarcinoma in situ in adeomatous polypAdenocarcinoma in situ in polypoid adenomaAdenocarcinoma in situ in a polyp, NOSCarcinoma in situ in a polyp, NOSM8210/3 Adenocarcinoma in adeonmatous polypAdenocarcinoma in tubular adenomaCarcinoma in adeomatous polypAdenocarcinoma in polypoid adenomaAdenocarcinoma in a polyp, NOSCarcinoma in a polyp, NOSM8211/0 Tubular adenoma, NOSM8211/3 Tubular adenocarcinomaTubular carcinomaM8212/0 Flat adenomaM8213/0 Serrated adenoma (C18._)Mixed adenomatous and hyperplastic polypM8214/3 Parietal cell carcinoma (C16._)Parietal cell adenocarcinomaM8215/3 Adenocarcinoma of anal glands (C21.1)Adenocarcinoma of anal ductsM8220/0 Adenomatous polyposis coli (C18._)Familial polyposis coliAdenomatosis, NOSM8220/3 Adenocarcinoma in adenomatous polyposisM8221/0 Multiple adenomatous polypsM8221/3 Adenocarcinoma in multiple adenomatous polypsM8230/2 Ductal carcinoma in situ, solid type (C50._)Intraductal carcinoma, solid typeM8230/3 Solid carcinoma, NOSSolid carcinoma with mucin formationSolid adenocarcinoma with mucin formationM8231/3 Carcinoma simplex(M8240/1) Carcinoid tumor of uncertain malignant potentialCarcinoid tumor, NOS, of appendix (C18.1)Carcinoid, NOS, of appendixCarcinoid tumor, argentaffin, NOSArgentaffinoma, NOSM8240/3 Carcinoid tumor, NOS (except of appendix M8240/1)Carcinoid, NOS (except of appendix)Typical carcinoidBronchial adenoma, carcinoidM8241/3 Enterochromaffin cell carcinoidCarcinoid tumor, argentaffin, malignantArgentaffinoma, malignantEC cell carcinoidSerotonin producing carcinoidM8242/1 Enterochromaffin-like cell carcinoid, NOSECL cell carcinoid, NOSM8242/3 Enterochromaffin-like cell tumor, malignantECL cell carcinoid, malignantM8243/3 Goblet cell carcinoidMucocarcinoid tumorMucinous carcinoidM8244/3 Composite carcinoidCombined carcinoid and adenocarcinomaMixed carcinoid-adenocarcinomaM8245/1 Tubular carcinoidM8245/3 Adenocarcinoid tumorM8246/3 Neuroendocrine carcinoma, NOSM8247/3 Merkel cell carcinoma (C44._)Merkel cell tumorPrimary cutaneous neuroendocrine carcinomaM8248/1 ApudomaM8249/3 Atypical carcinoid tumorM8250/1 Pulmonary adenomatosis (C34._)M8250/3 Bronchiolo-alveolar adenocarcinoma, NOS (C34._)Bronchiolo-alveolar carcinoma, NOSBronchiolar adenocarcinomaBronchiolar carcinomaAlveolar cell carcinomaM8251/0 Alveolar adenoma (C34._)M8251/3 Alveolar adenocarcinoma (C34._)Alveolar carcinomaM8252/3 Bronchiolo-alveolar carcinoma, non-mucinous (C34._)Bronchiolo-alveolar carcinoma, Clara cellBronchiolo-alveolar carcinoma, type II pneumocyteM8253/3 Bronchiolo-alveolar carcinoma, mucinous (C32._)Bronchiolo-alveolar carcinoma, goblet cell typeM8254/3 Bronchiolo-alveolar carcinoma, mixed mucinous and non-mucinous (C34._)Bronchiolo-alveolar carcinoma, Clara cell and goblet cell typeBronchiolo-alveolar carcinoma, type II pneumocyte and goblet cell typeBronchiolo-alveolar carcinoma, indeterminate typeM8255/3 Adenocarcinoma combined with mixed subtypesAdenomcarcinoma combined with other types of carcinomaM8260/0 Papillary adenoma, NOSGlandular papillomaM8260/3 Papillary adenocarcinoma, NOSPapillary carcinoma of thyroid (C73.9)Papillary renal cell carcinoma (C64.9)M8261/0 Villous adenoma, NOSVillous papillomaM8261/2 Adenocarcinoma in situ in villous adenomaM8261/3 Adenocarcinoma in villous adenomaM8262/3 Villous adenocarcinomaM8263/0 Tubulovillous adenoma, NOSvilloglandular adenomaPapillotubular adenomaM8263/2 Adenocarcinoma in situ in tubulovillous adenomaM8263/3 Adenocarcinoma in tubulovillous adenomaPapillotubular adenocarcinomaTubulopapillary adenocarcinomaM8264/0 Papillomatosis, glandularBiliary papillomatosis (C22.1, C24.0)M8270/0 Chromophobe adenoma (C75.1)M8270/3 Chromophobe carcinoma (C75.1)Chromophobe adenocarcinoma(M8271/0) Prolactinoma (C75.1)M8272/0 Pituitary adenoma, NOS (C75.1)M8272/3 Pituitary carcinoma, NOS (C75.1)M8280/0 Acidophil adenoma (C75.1)Eosinophil adenomaM8280/3 Acidophil carcinoma (C75.1)Acidophil adenocarcinomaEosinophil carcinomaEosinophil adenocarcinomaM8281/0 Mixed acidophil-basophil adenoma (C75.1)(M8290/0) Oxyphilic adenomaOncocytic adenomaOncocytomaHurthle cell adenoma(C73.9)Hurthle cell tumorFollicular adenoma, oxyphilic cell (C73.9)M8290/3 Oxyphilic adenocarcinomaOncocytic carcinomaOncocytic adenocarcinomaHurthlecell carcinoma (C73.9)Hurthle cell adenocarcinomaFollicular carcinoma, oxyphilic cell (C73.9)M8300/0 Basophil adenoma (C75.1)Mucoid cell adenomaM8300/3 Basophil carcinoma (C75.1)Basophil adenocarcinomaMucoid cell adenocarcinomaM8310/0 Clear cell adenomaM8310/3 Clear cell adenocarcinoma, NOSClear cell carcinomaClear cell adenocarcinoma, mesonephroidM8311/1 Hypernephroid tumor(M8312/3) Renal cell carcinoma, NOS (C64.9)Renal cell adenocarcinomaGrawitz tumorHypernephromaM8313/0 Clear cell adenofibroma (C56.9)clear cell cystadenofibromaM8313/1 Clear cell adenofibroma of borderline malignancyClear cell cystadenofibroma of borderline malignancyM8313/3 Clear cell adenocarcinofibroma (C56.9)Clear cell cystadenocarcinofibromaM8314/3 Lipid-rich carcinoma (C50._)M8315/3 Glycogen-rich carcinomaM8316/3 Cyst-associated renal cell carcinoma (C64.9)M8317/3 Renal cell carcinoma, chromophobe type (C64.9)Chromophobe cell renal carcinomaM8318/3 Renal cell carcinoma, sarcomatoid (C64.9)Renal cell carcinoma, spindle cellM8319/3 collecting duct carcinoma (C64.9)Bellini duct carcinomaRenal carcinoma, collecting duct typeM8320/3 Granular cell carcinomaGranular cell adenocarcinomaM8321/0 Chief cell adenoma (C75.0)M8322/0 Water-clear cell adenoma (C75.0)M8322/3 Water-clear cell adenocarcinoma (C75.0)Water-celar cell carcinomaM8323/0 Mixed cell adenomaM8323/3 Mixed cell adenocarcinomaM8324/0 LipoadenomaAdenolipomaM8325/0 Metanephric adenoma (C64.9)M8330/0 Follicular adenoma (C73.9)M8330/1 Atypical follicular adenoma (C73.9)M8330/3 Follicular adenocarcinoma, NOS (C73.9)Follicular carcinoma, NOSM8331/3 Follicular adenocarcinoma, well differentiated (C73.9)Follicular carcinoma, well differentiatedM8332/3 Follicular adenocarcinoma, trabecular (C73.9)Follicular carcinoma, trabecularFollicular adenocarcinoma, moderately differentiatedFOlloicular carcinoma, moderatedly differentiatedM8333/0 Microfollicular adenoma, NOS (C73.9)Fetal adenomaM8333/3 Fetal adenocarcinomaM8334/0 Macrofollicular adenoma (C73.9)Colloid adenomaM8335/3 Follicular carcinoma, minimally invasive (C73.9)Follicular carcinoma, encapsulatedM8336/0 Hyalinizing trabecular adenoma (C73.9)(M8337/3)Insular carcinoma (C73.9)M8340/3 Papillary carcinoma, follicular variant (C73.9)Papillary adenocarcinoma, follicular variantPapillary and follicular adenocarcinomaPapillary and follicular carcinomaM8341/3 Papillary microcarcinoma (C73.9)M8342/3 Papillary carcinoma, oxyphilic cell (C73.9)M8343/3 Papillary carcinoma, encapsulated (C73.9)M8344/3 Papillary carcinoma, columnar cell (C73.9)Papillary carcinoma, tall cellM8345/3 Medullary carcinoma with amyloid stroma (C73.9)Parafollicular cell carcinomaC cell carcinomaM8346/3 Mixed medullary-follicular carcinoma (C73.9)M8347/3 Mixed medullary-papillary carcinoma (C73.9)M8350/3 Nonencapsulated sclerosing carcinoma (c73.9)Nonencapsulated sclerosing adenocarcinomaNonencapsulated sclerosing tumorPapillary carcinoma, diffuse sclerosingM8360/1 Multiple endocrine adenomasEndocrine adenomatosisM8361/0 Juxtaglomerular tumor (C64.9)ReninomaM8370/0 Adrenal cortical adenoma, NOS (C74.0)Adrenal cortical tumor, benignAdrenal cortical tumor, NOSM8370/3 Adrenal cortical carcinoma (C74.0)Adrenal cortical adenocarcinomaAdrenal cortical tumor, malignantM8371/0 Adrenal cortical adenoma, compact cell (C74.0)M8372/0 Adrenal cortical adenoma, pigmented (C74.0)Black adenomaPigmented adenomaM8373/0 Adrenal cortical adenoma, clear cell (C74.0)M8374/0 Adrenal cortical adenoma, glomerulosa cell (C74.0)M8375/0 Adrenal cortical adenoma, mixed cell (C74.0)(M8380/0) Endometrioid adenoma, NOSEndometrioid cystadenoma, NOSM8380/1 Endometrioid adenoma, borderline malignancyEndometrioid cystadenoma, borderline malignancyEndometrioid tumor of low malignant potentialAtypical proliferative endometrioid tumorM8380/3 Endometrioid adenocarcinoma, NOSEndometrioid carcinoma, NOSEndometrioid cystadenocarcinomaM8381/0 Endometrioid adenofibroma, NOSEndometrioid cystadenofibroma, NOSM8381/1 Endometrioid adenofibroma, borderline malignancyEndometrioid cystadenofibroma, borderline malignancyM8381/3 Endometriod adenofibroma, malignantEndometrioid cystadenofibroma, malignantM8382/3 Endometrioid adenocarcinoma, secretory variantM8383/3 Endometrioid adenocarcinoma, ciliated cell variantM8384/3 Adenocarcinoma, endocervical type839–842 Adnexal And Skin appendage Neoplasms
M8390/0 Skin appendage adenoma (C44._)
Skin appendage tumor, benignAdnexal tumor, benignM8390/3 Skin appendage carcinoma (C44._)
Adnexal carcinomaM8391/0 Follicular fibroma (C44._)
TrichodiscomaFibrofolliculomaPerifollicular fibromaM8392/0 Syringofibroadenoma (C44._)
M8400/0 Sweat gland adenoma (C44._)
Sweat gland tumor, benignHidradenoma, NOSSyringadenoma, NOSM8400/1 Sweat gland tumor, NOS (C44._)
M8400/3 Sweat gland adenocarcinoma (C44._)
Sweat gland carcinomaSweat gland tumor, malignantM8401/0 Apocrine adenoma
Apocrine cystadenomaM8401/3 Apocrine adenocarcinoma
M8402/0 Nodular hidradenoma (C44._)
Eccrine acrospiromaClear cell hidradenomaM8402/3 Nodular hidradenoma, malignant (C44._)
HidradenocarcinomaM8403/0 Eccrine spiradenoma (C44._)
Spiradenoma, NOSM8403/3 Malignant eccrine spiradenoma (C44._) M8404/0 Hidrocystoma (C44._)
Eccrine cystadenomaM8405/0 Papillary hidradenoma
Hidradenoma papilliferumM8406/0 Papillary syringadenoma (C44._)
Papillary syringocystadenomaSyringocystadenoma papilliferumM8407/0 Syringoma, NOS (C44._)
M8407/3 Sclerosing sweat duct carcinoma (C44._)
Syringomatous carcinomaMicrocystic adnexal carcinomaM8408/0 Eccrine papillary adenoma (C44._)
M8408/1 Aggressive digital papillary adenoma (C44._)
M8408/3 Eccrine papillary adenocarcinoma (C44._)
Digital papillary adenocarcinomaM8409/0 Eccrine poroma (C44._)
M8410/0 Sebaceous adnoma (C44._)
M8410/3 Sebaceous adenocarcinoma (C44._)
Sebaceous carcinomaM8413/3 Eccrine adenocarcinoma (C44._)
M8420/0 Ceruminous adenoma (C44.2)
M8420/3 Ceruminous adenocarcinioma (C44.2)
Ceruminous carcinomaM8430/1 Mucoepidermoid tumor
M8430/3 Mucoepidermoid carcinoma
844–849 Cystic, Mucinous And Serous Neoplasms
M8440/0 Cystadenoma, NOS
Cystoma, NOSM8440/3 Cystadenocarcinoma, NOS
M8441/0 Serous cystadenoma, NOS
Serous cystomaSerous microcystic adenomaM8441/3 Serous cystadenocarcinoma, NOS (C56.9)
Serous adenocarcinoma, NOSSerous carcinoma, NOSM8442/1 Serous cystadenoma, borderline malignancy (C56.9)
Serous tumor, NOS, of low malignant potentialAtypical proliferating serous tumorM8443/0 Clear cell cystadenoma (C56.9)
M8444/1 Clear cell cystic tumor of borderline malignancy (C56.9)
Atypical proliferating clear cell tumorM8450/0 Papillary cystadenoma, NOS (C56.9)
M8450/3 Papillary cystadenocarcinoma, NOS (C56.9)
Papillocystic adenocarcinomaM8451/1 Papillary cystadenoma, borderline malignancy (C56.9)
M8452/1 Solid pseudo papillary tumor (C25._)
Papillary cystic tumorSolid and papillary epithelial neoplasmSolid and cystic tumorM8452/3 Solid pseudopapillary carcinoma (C25._)
M8453/0 Intraductal papillary-mucinous adenoma (C25._)
M8453/1 Intraductal papillary-mucinous tumor with moderate dysplasia (C25._)
M8453/2 Intraductal papillary-mucinous carcinoma, non-invasive (C25._)
M8453/3 Intraductal papillary-mucinous carcinoma invasive (C25._)
M8454/0 Cystic tumor of atrio-ventricular node (C38.0)
M8460/0 Papillary serous cystadenoma, NOS (C56.9)
M8460/3 Papillary serous cystadenocarcinoma (C56.9)
Papillary serous adenocarcinomaMicropapillary serous carcinomaM8461/0 Serous surface papilloma (C56.9)
M8461/3 Serous surface papillary carcinoma (C56.9)
Primary serous papillary carcinoma of peritoneum (C48.1)M8462/1 Serous papillary cystic tumor of borderline malignancy (C56.9)
Papillary serous cystadenoma, borderline malignancyPapillary serous tumor of low malignant potentialAtypical proliferative papillary serous tumorM8463/1 Serous surface papillary tumor of borderline malignancy (C56.9)
M8470/0 Mucinous cystadenoma, NOS (C56.9)
Mucinous cystomaPseudomucinous cystadenoma, NOSM8470/1 Mucinous cystic tumor with moderate dysplasia (C25._)
M8470/2 Mucinous cystadenocarcinoma, non-invasive (C25._)
M8470/3 Mucinous cystadenocarcinoma/ NOS (C56.9)
Pseudomucinous adenocarcinomaPseudomucinous cystadenocarcinoma, NOSM8471/0 Papillary mucinous cystadenoma, NOS (C56.9)
Papillary pseudomucinous cystadenoma, NOSM8471/3 papillary mucinous cystadenocarcinoma (C56.9)
Papillary pseudomucinous cystadenocarcinomaM8472/1 Mucinous cystic tumor of borderline malignancy (C56.9)
Mucinous cystadenoma, borderline malignancyPseudomucinous cystadenoma, borderline malignancyMucinous tumor, NOS, of low malignant potentialAtypical proliferative mucinous tumorM8473/1 Papillary mucinous cystadenoma, borderline malignancy (C56.9)
Papillary pseudomucinous cystadenoma borderline malignancyPapillary mucinous tumor of low malignant potentialM8480/0 Mucinous adenoma
M8480/3 Mucinous adenocarcinoma
Mucinous carcinomaColloid adenocarcinomaColloid carcinomaGelatinous adenocarcinomaGelatinous carcinomaMucoid adenocarcinomaMucoid carcinomaMucous adenocarcinomaMucous carcinomaPseudomyxoma peritonei with unknown primary site (C80.9)M8480/6 Pseudomyxoma peritonei
M8481/3 Mucin-producing adenocarcinoma
Mucin-producing carcinomaMucin-secreting adenocarcinomaMucin-secreting carcinomaM8482/3 Mucinous adenocarcinoma, endocervical type
M8490/3 Signet ring cell carcinoma
Signet ring cell adenocarcinomaM8490/6 Metastatic signet ring cell carcinoma
Krukenberg tumor850–854 Ductal, Lobular And Medullary Neoplasms
M8500/2 Intraductal carcinoma, noninfiltrating, NOS
Intraductal adenocarcinoma, noninfiltrating, NOSIntraductal carcinoma, NOSDuctal carcinoma in situ, NOS (C50._)DCIS, NOSDuctal intraepithelial neoplasia 3DIN 3M8500/3 Infiltrating duct carcinoma, NOS (C50._)
Infiltrating duct adenocarcinomaDuct adenocarcinoma, NOSDuct carcinoma, NOSDuct cell carcinomaDuctal carcinoma, NOSM8501/2 Comedocarcinoma, noninfiltrating (C50._)
Ductal carcinoma in situ, comedo typeDCIS, comedo typeM8501/3 Comedocarcinoma, NOS (C50._)
M8502/3 Secretory carcinoma of breast (C50._)
Juvenile carcinoma of breastM8503/0 Intraductal papilloma
Duct adenoma, NOSDuctal papillomaM8503/2 Noninfiltrating intraductal papillary adenocarcinoma (C50._)
Noninfiltrating intraductal papillary carcinomaIntraductal papillary adenocarcinoma, NOSIntraductal papillary carcinoma, NOSDuctal carcinoma in situ, papillaryDCIS, papillaryM8503/3 Intraductal papillary adenocarcinoma with invasion (C50._)
Infiltrating papillary adenocarcinomaInfiltrating and papillary adenocarcinomaM8504/0 Intracystic papillary adenoma
Intracystic papillomaM8504/2 Noninfiltrating intracystic carcinoma
M8504/3 Intracystic carcinoma, NOS
Intracystic papillary adenocarcinomaM8505/0 Intraductal papillomatosis, NOS
Diffuse intraductal papillomatosisM8506/0 Adenoma of nipple (C50._)
Subareolar duct papillomatosisM8507/2 Intraductal micropapillary carcinoma (C50._)
Ductal carcinoma in situ, micropapillaryIntraductal carcinoma, clingingM8508/3 Cystic hypersecretory carcinoma (C50._)
M8510/3 Medullary carcinoma, NOS
Medullary adenocarcinomaM8512/3 Medullary carcinoma with lymphoid stroma
M8513/3 Atypical medullary carcinoma (C50._)
M8514/3 Duct carcinoma, desmoplastic type
M8520/2 Lobular carcinoma in situ, NOS (C50._)
Lobular carcinoma, noninfiltratingLCIS, NOSM8520/3 Lobular carcinoma, NOS (C50._)
Lobular adenocarcinomaInfiltrating lobular carcinoma, NOSM8521/3 Infiltrating ductular carcinoma (C50._)
M8522/2 Intraductal carcinoma and lobular carcinoma in situ (C50._)
M8522/3 Infiltrating duct and lobular carcinoma (C50._)
Lobular and ductal carcinomaInfiltrating duct and lobular carcinoma in situIntraductal and lobular carcinomaInfiltrating lobular carcinoma and ductal carcinoma in situM8523/3 Infiltrating duct mixed with other types of carcinoma (C50._)
Infiltrating duct and cribiform carcinomaInfiltrating duct and mucinous carcinomaInfiltrating duct and tubular carcinomaInfiltrating duct and colloid carcinomaM8524/3 Infiltrating lobular mixed with other types of carcinoma (C50._)
M8525/3 Polymorphous low grade adenocarcinoma
Terminal duct adenocarcinomaM8530/3 Inflammatory carcinoma (C50._)
Inflammatory adenocarcinomaM8540/3 Paget disease, mammary (C50._)
Paget disease of breastM8541/3 Paget disease and infiltrating duct carcinoma of breast (C50._)
M8542/3 Paget disease, extramammary (except paget disease of bone)
M8543/3 Paget disease and intraductal carcinoma of breast (C50._)
M8550/0 Acinar cell adenoma
Acinar adenomaAcinic cell adenomaM8550/1 Acinar cell tumor
Acinic cell tumorM8550/3 Acinar cell carcinoma
Acinic cell adenocarcinomaAcinar adenocarcinomaAcinar carcinomaM8551/3 Acinar cell cystadenocarcinoma
M8560/0 Mixed squamous cell and glandular papilloma
M8560/3 Adenosquamous carcinoma
Mixed adenocarcinoma and squamous cell carcinomaMixed adenocarcionma and epidermoid carcinomaM8561/0 Adenolymphoma (C07._, C08._)
Warthin's tumorPapillary cystadenoma lymphomatosumM8562/3 Epithelial-myoepithelial carcinoma
M8570/3 Adenocarcinoma with squamous metaplasia
AdenoacanthomaM8571/3 Adenocarcinoma with cartilaginous and osseus metaplasia
Adenocarcinoma with cartilaginous metaplasiaAdenocarcinoma with osseous metaplasiaM8572/3 Adenocarcinoma with spindle cell metaplasia
M8573/3 Adenocarcinoma with apocrine metaplasia
Carcinoma with apocrine metaplasiaM8574/3 Adenocarcinoma with neuroendocrine differentiation
Carcinoma with neuroendocrine differentiationM8575/3 Metaplastic carcinoma, NOS
M8576/3 Hepatoid adenocarcinoma
Hepatoid carcinomaM8580/0 Thymoma, benign (C37.9)M8580/1 Thymoma, NOS (C37.9)M8580/3 Thymoma, malignant, NOS (C37.9)M8581/1 Thymoma, type A, NOS (C37.9)Thymoma, spindle cell, NOSThymoma, medullary, NOSM8581/3 Thymoma, type A, malignant (C37.9)
Thymoma, spindle cell, malignantThymoma, medullary, malignantM8582/1 Thymoma, type AB, NOS (C37.9)
Thymoma, mixed type, NOSM8582/3 thymoma, type AB, malignant (C37.9)
Thymoma, mixed type, malignantM8583/1 Thymoma, type B1, NOS (C37.9)
Thymoma, lymphocyte-rich, NOSThymoma, lymphocytic, NOSThymoma, predominantly cortical, NOSThymoma, organoid, NOSM8583/3 Thymoma, type B1, malignant (C37.9)
Thymoma, lymphocyte-rich, malignantThymoma, lymphocytic, malignantThymoma, predominantly cortical, malignantThymoma, organoid, malignantM8584/1 Thymoma, type B2, NOS (C37.9)
Thymoma, cortical, NOSM8584/3 Thymoma, type B2, malignant (C37.9)
Thymoma, cortical, malignantM8585/1 Thymoma, type B3, NOS (C37.9)
Thymoma, epithelial, NOSThymoma, atypical, NOSM8585/3 Thymoma, type B3, malignant (C37.9)
Thymoma, epithelial, malignantThymoma, atypical, malignantWell differentiated thymic carcinomaM8586/3 Thymic carcinoma, NOS (C37.9)
Thymoma, type CM8587/0 Ectopic hamartomatous thymoma
M8588/3 Spindle epithelial tumor with thymus-like element
Spindle epithelial tumor with thymus-like differentiationSETTLEM8589/3 Carcinoma showing thymus-like element
Carcinoma showing thymus-like differentiationCASTLEM8590/1 Sex cord-stromal tumor, NOS
Sex cord/gonadal stromal tumor, NOSTesticular/ovarian stromal tumorM8591/1 Sex cord-gonadal stromal tumor, incompletely differentiated
M8592/1 Sex cord-gonadal stromal tumor, mixed forms
M8593/1 Stromal tumor with minor sex cord elements
M8600/0 Thecoma, NOS
Theca cell tumorM8600/3 Thecoma, malignant
M8601/0 Thecoma, luteinized
M8602/0 Sclerosing stromal tumor
M8610/0 Luteoma, NOS
LuteinomaM8620/1) Granulosa cell tumor, NOS
, adult typeM8620/3 Granulosa cell tumor, malignant
Granulosa cell carcinomaGranulosa cell tumor, sarcomatoidM8621/1 Granulosa cell-theca cell tumor
Theca cell-granulosa cell tumorM8622/1 Granulosa cell tumor, juvenile
M8623/1 Sex cord tumor with annular tubules
M8630/1 Androblastoma/Arrhenoblastoma, benign
M8630/1 Androblastoma/Arrhenoblastoma, NOS
M8630/3 Androblastoma/Arrhenoblastoma, malignant
M8631/0 Sertoli-Leydig cell tumor, well differentiated
M8631/1 Sertoli-Leydig cell tumor of intermediate differentiation
Sertoli-Leydig cell tumor, NOSM8631/3 Sertoli-Leydig cell tumor, poorly differentiated
Sertoli-Leydig cell tumor, sarcomatoidM8632/1 Gynandroblastoma
M8633/1 Sertoli-Leydig cell tumor, retiform
M8634/1 Sertoli-Leydig cell tumor, intermediate differentiation, with heterologous elements
retiform, with heterologous elementsM8634/3 Sertoli-Leydig cell tumor, poorly differentiated, with heterologous elements
M8640/1 Sertoli tumor, NOS
Pick tubular adenomaSertoli cell adenomaTubular androblastoma, NOSTesticular adenomaM8640/3 Sertoli cell carcinoma (C62._)
M8641/0 Sertoli cell tumor with lipid storage
Folliculome lipidique (C56.9)Tubular androblastoma with lipid storageLipid-rich Sertoli cell tumorM8642/1 large cell calcifying Sertoli cell tumor
M8650/0 Leydig cell tumor, bening (C62._)
M8650/3 Leydig cell tumor, malignant
Interstitial cell tumor, malignantM8660/0 Hilus cell tumor (C56.9)
Hilar cell tumorM8670/0 Lipid cell tumor of ovary (C56.9)
Lipoid cell tumor of ovarySteroid cell tumor, NOSMasculinovoblastomaM8670/3 Steroid cell tumor, malignant
M8641/0 Adrenal rest tumor
868–871 Paragangliomas And Glomus tumors
M8680/0 Paraganglioma, benign
M8680/1 Paraganglioma, NOS
M8680/3 paraganglioma, malignant
M8681/1 Sympathetic paraganglioma
M8682/1 Parasympathetic paraganglioma
M8683/0 Gangliocytic paraganglioma (C17.0)
M8690/1 Glomus jugulare tumor, NOS (C75.5)
Jugular/jugulotympanic parangliomaM8691/1 Aortic body tumor (C75.5)
Aortic/aorticopulmonary paragangliomaM8692/1 Carotid body tumor/paraganglioma (C75.4)
M8693/1 Extra-adrenal paraganglioma, NOS
Nonchromaffin paraganglioma, NOSChemodectomaM8693/3 Extra-adrenal paraganglioma, malignant
Nonchromaffin paraganglioma, malignantM8700/0 Pheochromocytoma, NOS (C74.1)
Adrenal medullary/chromaffin paragangliomaChromaffin tumorChromaffinomaM8700/3 Pheochromocytoma, malignant (C74.1)
Adrenal medullary paraganglioma, malignantPheochromoblastomaM8710/3 Glomangiosarcoma
Glomoid sarcomaM8711/0 Glomus tumor, NOS
M8711/3 Glomus tumor, Malignant
M8712/0 Glomangioma
M8713/0 Glomangiomyoma
872–879 Nevi And Melanomas
M8720/0 Pigmented nevus, NOS
Melanocytic nevusNevus, NOSHairy nevusM8720/2 Melanoma in situ
M8720/3 Malignant melanoma, NOS (except juvenile melanoma M8770/0)
Melanoma, NOSM8721/3 Nodular melanoma
M8722/0 Balloon cell nevus
M8722/3 Balloon cell melanoma
M8723/0 Halo nevus
Regressing nevusM8723/3 Malignant melanoma, regressing
M8725/0 Neuronevus
M8726/0 Magnocellular nevus (C69.4)
Melanocytoma, eyeballMelanocytoma, NOSM8727/0 Dysplastic nevus
M8727/0 dysplastic nevus
M8728/0 Diffuse melanocytosis
M8728/1 Meningeal melanocytoma (C70.9)
M8728/3 Meningeal melanomatosis (C70.9)
M8730/0 Nonpigmented nevus
Achromic nevusM8740/0 Junctional nevus, NOS
Intraepidermal nevusM8740/3 Malignant melanoma in junctional nevus
M8741/2 Precancerous melanosis, NOS
M8741/3 Malignant melanoma in precancerous melanosis
M8742/3 Lentigo maligna melanoma
Hutchinson melanotic freckleM8743/3 Superficial spreading melanoma
M8744/3 Acral lentiginous melanoma, malignant
M8745/3 * Desmoplastic melanoma, malignant
Neurotropic melanoma, malignantMelanoma, desmoplastic, amelanoticM8746/3 Mucosal lentiginous melanoma
M8750/0 Intradermal nevus
Dermal nevusM8760/0 compound nevus
Dermal and epidermal nevusM8761/0 Small congenital nevus
M8761/1 Giant pigmented nevus, NOS
Intermediate and giant congenital nevusM8761/3 Malignant melanoma in giant pigmented nevus/congenital melanocytic nevus
M78762/1 Proliferative dermal lesion in congenital nevus
M8770/0 Epithelioid and spindle cell nevus
Juvenile nevusJuvenile melanomaSpitz nevusPigmented spindle cell nevus of ReedM8770/3 Mixed epithelioid and spindle cell melanoma
M8771/0 Epithelioid cell nevus
M8771/3 Epithelioid cell melanoma
M8772/0 spindle cell nevus, NOS
M8772/3 Spindle cell melanoma, NOS
M8773/3 Spindle cell melanoma, type A
M8774/3 Spindle cell melanoma, type B
M8780/0 Blue nevus, NOS
Jadassohn blue nevusM8780/3 blue nevus, malignant
M8790/0 Cellular blue nevus
880 Soft tissue Tumors And Sarcomas, NOS
M8800/0 Soft tissue tumor, benign
M8800/3 Sarcoma, NOS
Soft tissue sarcomaSoft tissue/mesenchymal tumor, malignantM8800/9 Sarcomatosis, NOS
M8801/3 Spindle cell sarcoma
M8802/3 Giant cell sarcoma (except of bone M9250/3)
Pleomorphic cell sarcomaM8803/3 Small cell sarcoma
Round cell sarcomaM8804/3 Epithelioid sarcoma
Epithelioid cell sarcomaM8805/3 Undifferentiated sarcoma
M8806/3 Desmoplastic small round cell tumor
M8810/0 Fibroma, NOS
M8810/1 Cellular fibroma (C56.9)
M8810/3 Fibrosarcoma, NOS
M8811/0 Fibromyxoma
Myxoid fibromaMyxofibroma, nosM8811/3 Fibromyxosarcoma
M8812/0 Periosteal fibroma (C40._, C41._)
Periosteal sarcoma, NOSM8813/0 Fascial fibroma
M8813/3 Fascial fibrosarcoma
M8814/3 Infantile fibrosarcoma
Congenital fibrosarcomaM8815/0 Solitary fibrous tumor
Localized fibrous tumorM8815/3 Solitary fibrous tumor, malignant
M8820/0 Elastofibroma
M8821/1 Aggressive fibromatosis
Extra-abdominal desmoidDesmoid, NOSInvasive fibromaM8822/1 Abdominal fibromatosis
Abdominal desmoidMesenteric fibromatosis (C48.1)Retroperitoneal fibromatosis (C48.0)M8823/0 Desmoplastic fibroma
M8824/0 Myofibroma
M8824/1 Myofibromatosis
Congenital generalized fibromatosisInfantile myofibromatosisM8825/0 Myofibroblastoma
M8825/1 Myofibroblastic tumor, nos
Inflammatory myofibroblastic tumorM8826/0 Angiomyofibroblastoma
M8827/1 Myobfibroblastic tumor, peribronchial (C34._)
congenital peribronchial myofibroblastic tumorM8830/0 Benign fibrous histiocytoma
Fibrous histiocytoma, NOSFibroxanthoma, NOSXantofibromaM8830/1 Atypical fibrous histiocytoma
Atypical fibroxanthomaM8830/3 Malignant fibrous histiocytoma
Fibroxanthoma, malignantM8831/0 Histiocytoma, NOS
Deep histiocytomaJuvenile histiocytomaReticulohistiocytomaM8832/0 Dermatofibroma, NOS (C44._)
Sclerosing hemangiomaCutaneous histiocytomaSubepidermal nodular fibrosisDermatofibroma lenticulareM8832/3 Dermatofibrosarcoma, NOS (C44._)
Dermatofibrosarcoma protuberans, NOSM8833/3 Pigmented dermatofibrosarcoma protuberans
Bednar tumorM8834/1 Giant cell fibroblastoma
M8835/1 Plexiform fibrohistiocytic tumor
M8836/1 Angiomatoid fibrous histiocytoma
M8840/0 Myxoma, NOS
M8840/3 Myxosarcoma
M8841/1 Angiomyxoma
Aggressive angiomyxomaM8842/0 Ossifying fibromyxoid tumor
M8850/0 Lipoma, NOS
M8850/1 Atypical lipoma
Superficial well differentiated liposarcomaWell differentiated liposarcoma of superficial soft tissueM8850/3 Liposarcoma, NOS
FibroliposarcomaM8851/0 Fibrolipoma
M8851/3 Liposarcoma, well differentiated
Liposarcoma, differentiatedLipoma-like liposarcomaSclerosing liposarcomaInflammatory liposarcomaM8852/0 Fibromyxolipoma
MyxolipomaM8852/3 Myxoid liposarcoma
MyxoliposarcomaM8853/3 Round cell liposarcoma
M8854/0 Pleomorphic lipoma
M8854/3 Pleomorphic liposarcoma
M8855/3 Mixed liposarcoma
M8856/0 Intramuscular lipoma
Infiltrating lipoma/angiolipomaM8857/0 Spindle cell lipoma
M8857/3 Fibroblastic liposarcoma
M8858/3 Dedifferentiated liposarcoma
M8860/0 Angiomyolipoma
M8861/0 Angiolipoma, NOS
M8862/0 Chondroid lipoma
M8870/0 Myelolipoma
M8880/0 Hibernoma
Fetal fat cell lipomaBrown fat tumorM8881/0 Lipoblastomatosis
Fetal lipoma, NOSFetal lipomatosisLipoblastomaM8890/0 Leiomyoma, NOS
Fibroid uterus (C55.9)FibromyomaLeiomyofibromaPlexiform leiomyomaLipoleiomyomaM8890/1 Leiomyomatosis, NOS
Intravascular leiomyomatosisM8890/3 Leiomyosarcoma, NOS
M8891/0 Epithelioid leiomyoma
LeiomyoblastomaM8891/3 Epithelioid leiomyosarcoma
M8892/0 Cellular leiomyoma
M8893/0 Bizarre leiomyoma
Symplastic/atypical/pleomorphic leiomyomaM8894/0 Angiomyoma
Vascular leiomyomaAngioleiomyomaM8894/3 Angiomyosarcoma
M8895/0 Myoma
M8895/3 Myosarcoma
M8896/3 Myxoid leiomyosarcoma
M8897/1 Smooth muscle tumor of uncertain malignant potential
Smooth muscle tumor, NOSM8898/1 Metastasizing leiomyoma
M8900/0 Rhabdomyoma, NOS
M8900/3 Rhabdomyosarcoma, NOS
RhabdosarcomaM8901/3 Pleomorphic rhabdomyosarcoma, adult type
Pleomorphic rhabdomyosarcoma, NOSM8902/3 Mixed type rhabdomyosarcoma
Mixed embryonal rhabdomyosarcoma and alveolar rhabdomyosarcomaM8903/0 Fetal rhabdomyoma
M8904/0 Adult rhabdomyoma
Glycogenic rhabdomyomaM8905/0 Genital rhabdomyoma
M8910/3 Embryonal rhabdomyosarcoma, NOS
Embryonal rhabdomyosarcoma, pleomorphicSarcoma botryoidesBotryoid sarcomaM8912/3 Spindle cell rhabdomyosarcoma
M8920/3 Alveolar rhabdomyosarcoma
M8921/3 Rhabdomyosarcoma with ganglionic differentiation
Ectomesenchymoma893–899 Complex Mixed And Stromal Neoplasms
M8930/0 Endometrial stromal nodule
M8930/3 Endometrial stromal sarcoma, NOS
Endometrial sarcoma, NOSEndometrial stromal sarcoma, high gradeM8931/3 Endometrial stromal sarcoma, low grade
Endolymphatic stromal myosisEndometrial stromatosisStromal endometriosisStromal myosis, NOSM8932/0 Adenomyoma
Atypical polypoid adenomyomaM8933/3 Adenosarcoma
M8934/3 Carcinofibroma
M8935/0 Stromal tumor, benign
M9835/1 Stromal tumor, NOS
M8935/3 Stromal sarcoma, NOS
M8936/0 Gastrointestinal stromal tumor, benign
GIST, benignM8936/1 Gastrointestinal stromal tumor, NOS
GIST, NOS/uncertain malignant potentialGastrointestinal autonomic nerve tumor (GANT)Gastrointestinal pacemaker cell tumorM8936/3 Gastrointestinal stromal sarcoma
GIST, malignantM8940/0 Pleomorphic adenoma
Mixed tumor, NOSMixed tumor, salivary gland type, NOSChondroid syringomaM8940/3 Mixed tumor, malignant, NOS
Mixed tumor, malignant, NOSMixed tumor, salivary gland type, malignantMalignant chondroid syringomaM8941/3 Carcinoma in pleomorphic adenoma
M8950/3 Mullerian mixed tumor
M8951/3 Mesodermal mixed tumor
M8959/0 Benign cystic nephroma
M8959/1 Cystic partially differentiated nephroblastoma
M8959/3 Malignant cystic nephroma
Malignant multilocular cystic nephromaM8960/1 Mesoblastic nephroma
M8960/3 Nephroblastoma, NOS
Wilms's tumorNephroma, NOSM8963/3 malignant rhabdoid tumor
Rhabdoid sarcomaRhabdoid tumor, NOSM8964/3 Clear cell sarcoma of kidney
M8965/0 Nephrogenic adenofibroma
M8966/0 Renomedullary interstitial cell tumor
Renomedullary fibromaM8967/0 Ossifying renal tumor
M8970/3 Hepatoblastoma
Embryonal hepatomaM8971/3 Pancreatoblastoma
M8972/3 Pulmonary blastoma
PneumoblastomaM8973/3 Pleuropulmonary blastoma
M8974/1 Sialoblastoma
M8980/3 Carcinosarcoma, NOS
M8981/3 Carcinosarcoma, embryonal
M8982/0 Myoepithelioma
Myoepithelial tumorMyoepithelial adenomaM8982/3 Malignant myoepithelioma
Myoepithelial carcinomaM8983/0 Adenomyoepithelioma
M8990/0 Mesencymoma, benign
M8990/1 Mesenchymoma, NOS
Mixed mesenchymal tumorM8990/3 Mesenchymoma, malignant
Mixed mesenchymal sarcomaM8991/3 Embryonal sarcoma
M9000/0 Brenner tumor, NOS
M9000/1 Brenner tumor, borderline malignancy
Brenner tumor, proliferatingM9000/3 Brenner tumor, malignant
M9010/0 Fibroadenoma, NOS
M9011/0 Intracanalicular fibroadenoma
M9012/0 Pericanalicular fibroadenoma
M9013/0 Adenofibroma, NOS
Cystadenofibroma, NOSPapillary adenofibromaM9014/0 Serous adenofibroma, NOS
Serous cystadenofibroma, NOSM9014/1 Serous adenofibroma of borderline malignancy
Serous cystadenofibroma of borderline malignancyM9014/3 Serous adenocarcinofibroma
Malignant serous adenofibromaSerous cystadenocarcinofibromaMalignant serous cystadenofibromaM9015/0 Mucinous adenofibroma, NOS
Mucinous cystadenofibroma, NOSM9015/1 Mucinous adenofibroma of borderline malignancy
Mucinous cystadenofibroma of borderline malignancyM9015/3 Mucinous adenocarcinofibroma
Malignant mucinous adenofibromaMucinous cystadenocarcinofibromaMalignant mucinous cystadenofibromaM9016/0 Gian fibroadenoma
M9020/0 Phyllodes tumor, benign
Cystosarcoma phyllodes, benignM9020/1 Phyllodes tumor, borderline
Cystosarcoma phyllodes, NOSPhyllodes tumor, NOSM9020/3 Phyllodes tumor, malignant
Cystosarcoma phyllodes, malignantM9030/0 Juvenile fibroadenoma
M9040/0 Synovioma, benign
M9040/3 Synovial sarcoma, NOS
Synovioma, NOSSynovioma, malignantM9041/3 Synovial sarcoma, spindle cell
Synovial sarcoma, monophasic fibrousM9042/3 Synovial sarcoma, epithelioid cell
M9043/3 Synovial sarcoma, biphasic
M9044/3 Clear cell sarcoma, NOS (except of kiney M9864/3)
Clear cell sarcoma, of tendons and aponeurosesMelanoma, malignant, of soft partsM9050/0 Mesothelioma, benign
M9050/3 Mesothelioma, malignant or NOS
M9051/0 Fibrous mesothelioma, benign
M9051/3 Fibrous mesothelioma, malignant or NOS
Spindled mesotheliomaSarcomatoid mesotheliomaDesmoplastic mesotheliomaM9052/0 Epithelioid mesothelioma, benign
Well differentiated papillary mesothelioma, benignmesothelial papillomaM9052/3 Epithelioid mesothelioma, malignant or NOS
M9053/3 Mesothelioma, biphasic, malignant or NOS
M9054/0 Adenomatoid tumor, NOS
M9055/0 Multicystic mesothelioma, benign
Cystic mesothelioma, benignM9055/1 cystic mesothelioma, NOS
M9060/3 Dysgerminoma
M9061/3 Seminoma, NOS
M9062/3 Seminoma, anaplastic
Seminoma with high mitotic indexM9063/3 Spermatocytic seminoma
SpermatocytomaM9064/2 Intratubular malignant germ cells
Intratubular germ cell neoplasiaM9064/3 Germinoma
Germ cell tumor, NOSM9065/3 Germ cell tumor, nonseminomatous
M9070/3 Embryonal carcinoma, NOS
Embryonal adenocarcinomaM9071/3 Yolk sac tumor
Endodermal sinus tumorPolyvesicular vitelline tumorOrchioblastomaEmbryonal carcinoma, infantileHepatoid yolk sac tumorM9072/3 Polyembryoma
Embryonal carcinoma, polyembryonal typeM9073/1 Gonadoblastoma
GonocytomaM9080/0 Teratoma, benign
Adult cystic teratomaAdult/cystic teratoma, NOSTeratoma, differentiatedMature teratomaM9080/1 Teratoma, NOS
Solid teratomaM9080/3 Teratoma, malignant, NOS
Embryonal teratomaTeratoblastoma, malignantImmature teratoma, malignant or NOSM9081/3 Teratocarcinoma
Mixed embryonal carcinoma and teratomaM9082/3 malignant teratoma, undifferentiated
Malignant teratoma, anaplasticM9083/3 Malignant teratoma, intermediate
M9084/0 Dermoid cyst, NOS
Dermoid, NOSM9084/3 Teratoma with malignant transformation
Dermoid cyst with malignant transformation or with secondary tumorM9085/3 mixed germ cell tumor
Mixed teratoma and seminomaM9090/0 Struma ovarii, NOS
M9090/3 Struma ovarii, malignant
M9091/1 Strumal carcinoid
Struma ovarii and carcinoidM9100/0 Hydatidifrom mole, NOS
Hydatid moleComplete hydatidiform moleM9100/1 Invasive hydatidiform mole
Chorioadenoma /destruensChorioadenomaInvasive mole, NOSMalignant hydatidiform moleM9100/3 Choriocarcinoma, NOS
ChorionepitheliomaChorioepitheliomaM9101/3 Choriocarcinoma combined with other germ cell elements
combined with teratomacombined with embryonal carcinomaM9102/3 Malignant teratoma, trophoblastic
M9103/0 Partial hydatidiform mole
M9104/1 Placental site trophoblastic tumor
M9105/3 Trophoblastic tumor, epithelioid
M9110/0 Mesonephroma, benign
Mesonephric adenomaWolffian duct adenomaM9110/1 Mesonephric tumor, NOS
Wolffian duct tumorM9110/3 Mesonephroma, malignant
Mesonephric adenocarcinomaMesonephroma, NOSWolffian duct carcinomaM9120/0 Hemangioma, NOS
Angioma, NOSChorioangiomaM9120/3 Hemangiosarcoma
AngiosarcomaM9121/0 Cavernous hemangioma
M9122/0 Venous hemangioma
M9123/0 Racemose hemangioma
Arteriovenous hemangiomaM9124/3 Kupffer cell sarcoma
M9125/0 Epithelioid hemangioma
Histiocytoid hemangiomaM9130/0 Hemangioendothelioma, benign
M9130/1 Hemangioendothelioma, NOS
AngioendotheliomaKaposiform hemangioendotheliomaM9130/3 Hemangioendothelioma, malignant
Hemangioendothelial sarcomaM9131/0 Capillary hemangioma
Hemangioma simplexInfantile/plexiform/juvenile hemangiomaM9132/0 Intramuscular hemangioma
M9133/1 Epithelioid hemangioendothelioma, NOS
M9133/3 Epithelioid hemangioendothelioma, malignant
Intravascular bronchial alveolar tumorM9135/1 Endovascular papillary angioendothelioma
Dabska tumorM9136/1 Spindle cell hemangioendothelioma
Spindle cell angioendotheliomaM9140/3 Kaposi's sarcoma
Multiple hemorrhagic sarcomaM9141/0 Angiokeratoma
M9142/0 Verrucous keratotic hemangioma
M9150/0 Hemangiopericytoma, benign
M9150/1 Hemangiopericytoma, NOS
Hemangiopericytic meningiomaM9150/3 Hemangiopericytoma, malignant
M9160/0 angiofibroma, NOS
Juvenile angiofibromaFibrous papule of noseInvoluting nevusGiant cell or cellular angiofibromaM9161/0 Acquired tufted hemangioma
M9161/1 Hemangioblastoma
AngioblastomaM9150/0 Hemangiopericytoma, benign
M9150/1 Hemangiopericytoma, NOS
M9170/0 Lymphangioma, NOS
Lymphangioendothelioma, NOSM9170/3 Lymphangiosarcoma
Lymphangioendothelial sarcomaLymphangioendothelioma, malignantM9171/0 Capillary lymphangioma
M9172/0 Cavernous lymphangioma
M9173/0 Cystic lymphangioma
Hygroma, NOSCystic HygromaM9174/0 Lymphangiomyoma
M9174/1 Lymphangiomyomatosis
LymphangioleiomyomatosisM9175/0 Hemolymphangioma
918–924 Osseous And Chondromatous neoplasms
M9180/0 Osteoma, NOS
M9180/3 Osteosarcoma, NOS
Osteogenic sarcoma, NOSOsteochondrosarcomaOsteoblastic sarcomaM9181/3 Chondroblastic osteosarcoma
M9182/3 Fibroblastic osteosarcoma
OsteofibrosarcomaM9183/3 Telangeictatic osteosarcoma
M9184/3 Osteosarcoma in Paget disease of bone
M9185/3 Small cell osteosarcoma
Round cell osteosarcomaM9186/3 Central osteosarcoma
Conventional central osteosarcomaMedullary osteo sarcomaM9187/3 Intraosseous well differentiated osteosarcoma
Intraosseous low grade osteosarcomaM9191/0 Osteoid osteoma, NOS
M9192/3 Parosteal osteosarcoma
Juxtacortical osteosarcomaM9193/3 Periosteal osteosarcoma
M9194/3 High grade surface osteosarcoma
M9195/3 Intracortical osteosarcoma
M9200/0 Osteoblastmoa, NOS
Giant osteoid ostemoaM9200/1 Aggressive osetoblastoma
M9210/0 Osteochondroma
Cartilagionus exostosisCartilaginous exostosisEcchondromaM9210/1 Osteochondromatosis, NOS
EcchondrosisM9220/0 Chondroma, NOS
EnchondromaM9220/1 Condromatosis, NOS
M9220/3 Chondrosarcoma, NOS
FibrochondrosarcomaM9221/0 Juxtacortical chondroma
Periosteal chondromaM9221/3 Juxtacortical chondrosarcoma
Periosteal chondrosarcomaM9230/0 Chondroblastoma, NOS
Chondromatous giant cell tumorCodman tumorM9230/3 Chondroblastoma, malignant
M9231/3 Myxoid chondrosarcoma
M9240/3 Mesenchymal chondrosarcoma
M9241/0 Chondromyxoid fibroma
M9242/3 Clear cell chondrosarcoma
M9243/3 Dedifferentiated chondrosarcoma
M9250/1 giant cell tumor of bone, NOS
Osteoclastoma, NOSM9250/3 Giant cell tumor of bone, malignant
Osteoclastoma, malignantGiant cell sarcoma of boneM9251/1 Giant cell tumor of soft parts, NOS
M9251/3 Malignant giant cell tumor of soft parts
M9252/0 Tenosynovial giant cell tumor
Fibrous histiocytoma of tendon sheathGiant cell tumor of tendon sheathM9252/3 Malignant tenosynovial giant cell tumoe
Giant cell tumor of tendon sheath, malignantM9260/3 Ewing's sarcoma/tumor
M9261/3 Adamantinoma of long bones
M9262/0 Ossifying fibroma
Fibro-osteomaOsteofibromaM9270/0 Odontogenic tumor, benign
M9270/1 Odontogenic tumor, NOS
M9270/3 Odontogenic tumor, malignant
Odontogenic carcinoma/sarcomaPrimary intraosseus or ameloblastic carcinomaM9271/0 Ameloblastic fibrodentinoma
DentinomaM9272/0 Cementoma, NOS
Periapical cemental dysplasia or cemento-osseus dysplasiaM9273/0 Cementoblastoma, benign
M9274/0 Cementifying fibroma
Cemento-ossifying fibromaM9275/0 Gigantiform cementoma
Florid osseus dysplasiaM9280/0 Odontoma, NOS
M9281/0 Compound odontoma
M9282/0 Complex odontoma
M9290/0 Ameloblastic fibro-odontoma
Fibroameloblastic odontomaM9290/3 Ameloblastic odontosarcoma
Ameloblastic fibrodentinosarcoma or fibro-odontosarcomaM9300/0 Adenomatoid odontogenic tumor
AdenomeloblastomaM9301/0 Calcifying odontogenic cyst
M9302/0 Odontogenic ghost cell tumor
M9310/0 Ameloblastoma, NOS
Adamantinoma, NOS (except of long bones M9261/3)M9310/3 Ameloblastoma, malignant
Adamantinoma, NOS (except of long bones M9261/3)M9311/0 Odontoameloblastoma
M9312/0 Squamous odontogenic tumor
M9320/0 Odontogenic myxoma
Odontogenic myxofibromaM9321/0 Central odontogenic fibroma
Odontogenic fibroma, NOSM9322/0 Peripheral odontogenic fibroma
M9330/0 Ameloblastic fibroma
M9330/3 Ameloblastic fibrosarcoma
Ameloblastic sarcomaOdontogenic fibrosarcomaM9340/0 Calcifying epithelial odontogenic tumor
Pindbord gumorM9341/1 clear cell odontogenic tumor
M9342/3 Odontogenic carcinosarcoma
M9350/1 Craniopharyngioma
Rathke pouch tumorM9351/1 Craniopharyngioma, adamantinomatous
M9352/1 Craniopharyngioma, papillary
M9360/1 Pinealoma
M9361/1 Pineocytoma
M9362/3 Pineoblastoma
Mixed pineal tumorMixed pineocytoma-pineoblastomaPineal parenchymal tumor of intermediate differentiationTransitional pineal tumorM9363/0 Melanotic neuroectodermal tumor
Retinal anlage tumorMelanoameloblastomaMelanotic progonomaM9364/3 Peripheral neuroectodermal tumor
Neuroectodermal tumor, NOSPeripheral primitive neuroectodermal tumor, NOS (PPNET)
M9365/3 Askin Tumor
M9370/3 Chordoma, NOS
M9371/3 Chondroid chordoma
M9372/3 Dedifferentiated chorcoma
M9373/0 Parachordoma
M9380/3 Glioma, malignant
Glioma, NOS (except nasal glioma, not neoplastic)M9381/3 Gliomatosis cerebri
M9382/3 Mixed glioma
oligoastrocytomaAnaplastic oligoastrocytomaM9383/1 Subepyndymoma
Subependymal gliomaSubependymal astrocytoma, NOSMixed subendymoma-ependymomaM9384/1 Subependymal giant cell astrocytoma
M9390/0 Choroid plexus papilloma, NOS
M9390/1 Atypical choroid plexus papilloma
M9390/3 Choroid plexus carcinoma
Choroid plexus papilloma, anaplastic or malignantM9391/3 Ependymoma, NOS
Epithelial / cellular / clear cell / tanycytic ependymomaM9392/3 Ependymoma, anaplastic
EpendymoblastomaM9393/3 Papillary ependymoma
M9394/1 Myxopapillary ependymoma
M9400/3 Astrocytoma, NOS
Astrocytic gliomaAstrogliomaDiffuse astrocytomaAstrocytoma, low gradeDiffuse astocytoma, low gradeCystic astrocytomaM9401/3 Astrocytoma, anaplastic
M9410/3 Protoplasmic astrocytoma
M9411/3 Gemistocytic astrocytoma
GemistocytomaM9412/1 Desmoplastic infantile astrocytoma or ganglioglioma
M9413/0 dysembryoplastic neuroepithelial tumor
M9420/3 Fibrillary astrocytoma
Fibrous astrocytomaM9421/1 Pilocytic astrocytoma
Piloid or Juvenile astrocytomaSpongioblastoma, NOSM9423/3 Polar spongioblastoma
Spongioblastoma polarePrimitive polar spongioblastomaM9424/3 Pleomorphic xanthoastrocytoma
M9430/3 Astroblastoma
M9440/3 Glioblastoma, NOS
Glioblastoma multiformeSpongioblastoma multiformeM9441/3 Giant cell glioblastoma
Monstrocellular sarcomaM9442/1 gliofibroma
M9442/3 gliosarcoma
Glioblastoma with sarcomatous componentM9444/1 Chordoid glioma
Chordoid glioma of third ventricleM9450/3 Oligodendroglioma, NOS
M9451/3 Oligodendroglioma, anaplastic
M9460/3 Oligodendroblastoma
M9470/3 Medullablastoma, NOS
Melanotic medulloblastomaM9471/3 Desmoplastic nodular medulloblastoma
Desmoplastic medulloblastomaCircumscribed arachnoidal cerebellar sarcomaM9472/3 Medullomyoblastoma
M9473/3 Primitive neuroectodermal tumor, NOS
PNET, NOSCentral primitive neuroectodermal tumor, NOS (CPNET)Supratentorial PNETM9474/3 large cell medulloblastoma
M9480/3 Cerebellar sarcoma, NOS
M9490/0 Ganglioneuroma
M9490/3 Ganglioneuroblastoma
M9491/0 Ganglioneuromatosis
M9492/0 Gangliocytoma
M9493/0 Dysplastic gangliocytoma of cerebellum (Lhermitte-Duclos)
M9500/3 Neuroblastoma, NOS
SympathicoblastomaCentral neuroblastomaM9501/0 Medulloepithelioma, benign
Diktyoma, benignM9501/3 Medulloepithelioma, NOS
Diktyoma, malignantM9502/0 Teratoid medulloepithelioma, benign
M9502/3 Teratoid medulloepithelioma
M9503/3 Neuroepithelioma, NOS
M9504/3 Spongioneuroblastoma
M9505/1 Ganglioglioma, NOS
M9505/3 Ganglioglioma, anaplastic
M9506/1 Central neurocytoma
NeurocytomaCerebellar liponeurocytomaLipomatous medulloblastomaNeurolipocytomaMedullocytomaM9507/0 Pacinian tumor
M9508/3 Atypical teratoid/rhabdoid tumor
M9510/0 Retinocytoma
M9510/3 Retinoblastoma, NOS
M9511/3 Retinoblastoma, differentiated
M9512/3 Retinoblastoma, undifferentiated
M9513/3 Retinoblastoma, diffuse
M9514/1 Retinoblastoma, spontaneously regressed
M9520/3 Olfactory neurogenic tumor
M9521/3 Olfactory neurocytoma
EsthesioneurocytomaM9522/3 Olfactory neuroblastoma
EsthesioneuroblastomaM9523/3 Olfactory neuroepithelioma
Esthesio neuroepitheliomaM9530/0 Meningioma, NOS
MicrocysticSecretoryLymphoplasmacyte-richMetaplasticM9530/1 Meningiomatosis, NOS
DiffuseMultiple meningiomasM9530/3 Meningioma, malignant
AnaplasticLeptomeningeal sarcomaMeningeal sarcomaMeningothelial sarcomaM9531/0 Meningothelial meningioma
Endotheliomatous meningiomaSyncytial meningiomaM9532/0 Fibrous meningioma
Fibroblastic meningiomaM9533/0 Psammomatous meningioma
M9534/0 Angiomatous meningioma
M9537/0 Transitional meningioma
M9538/1 Clear cell meningioma
ChordoidM9538/3 Papillary meningioma
RhabdoidM9539/1 Atypical meningioma
M9539/3 Meningeal sarcomatosis
M9540/0 Neurofibroma, NOS
M9540/1 Neurofibromatosis, NOS
Multiple neurofibromatosisVon Recklinghausen disease (except of bone)M9540/3 Malignant peripheral nerve sheath tumor
MPNST, NOSMPNST with glandular differentiationEpithelioidwith mesenchymal differentiationMelanoticMelanotic psammomatousM9541/0 Melanotic neurofibroma
M9550/0 Plexiform neurofibroma
Plexiform neuromaM9560/0 Neurilemoma, NOS
Schwannoma, NOSNeurinomaAcoustic neuromaPigmented or melanotic schwannomaPlexiform / cellular / degenerated / ancient / psammomatousM9560/1 Neurinomatosis
M9561/3 Malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation
MPNST with rhabdomyoblastic differentiationTriton tumor, malignantMalignant schwannoma with rhabdomyoblastic differentiationM9562/0 Neurothekeoma
Nerve sheath myxomaM9570/0 Neuroma, NOS
M9571/0 Perineurioma, NOS
Intraneural perineuriomaSoft tissue perineuriomaM9571/3 Perineurioma, malignant
Perineural MPNSTM9560/0 Schwannoma, NOS
M9560/0 Neurinoma
M9560/0 Acoustic neuroma
M9570/0 Neuroma, NOS
958 Granular cell tumors and Alveolar soft part sarcoma
M9580/0 Granular cell tumor/myoblastoma, NOS
M9580/3 Granular cell tumor/myoblastoma, malignant
M9581/3 Alveolar soft part sarcoma
M9582/0 Granular cell tumor of the sellar region (C75.1)
M9590/3 Malignant Lymphoma, NOS
Lymphoma, NOSMicroglioma (C71._)M9591/3 Malignant lymphoma, non-Hodgkin, NOS
Non-Hodgkin's lymphoma, NOSB cell lymphoma, NOSMalignant lymphoma, non-cleaved cell, NOSMalignant lymphoma, diffuse, NOSMalignant lymphoma, lymphocytic, intermediate differentiation, nodularMalignant lymphoma, small cell, noncleaved, diffuseMalignant lymphoma, undifferentiated cell, non-BurkittMalignant lymphoma, undifferentiated cell type, NOSLymphosarcoma, NOSLymphosarcoma, diffuseReticulum cell sarcoma, NOSReticulum cell sarcoma, diffuseReticulosarcoma, NOSReticulosarcoma, diffuseMalignant lymphoma, small cleaved cell, diffuseMalignant lymphoma, lymphocytic, poorly differentiated, diffuseMalignant lymphoma, small cleaved cell, NOSMalignant lymphoma, cleaved cell, NOSM9596/3 Composite Hodgkin and non-Hodgkin lymphoma
M9650/3 Hodgkin lymphoma, NOS
Hodgkin's disease, NOSMalignant lymphoma, HodgkinM9651/3 Hodgkin lymphoma, lymphocyte rich
Lymphocyte-rich classical Hodgkin lymphomaHodgkin disease, lymphocyte predominance, NOSHodgkin disease, lymphocytic-histiocytic predominanceHodgkin disease, lymphocyte predominance, diffuseM9652/3 Mixed cellularity classical Hodgkin lymphoma, NOS
Hodgkin lymphoma, mixed cellularity, NOSM9653/3 Lymphocyte-depleted classical Hodgkin lymphoma, NOS
M9654/3 Hodgkin lymphoma, lymphocyte depletion, diffuse fibrosis
M9655/3 Hodgkin lymphoma, lymphocyte depletion, reticular
M9659/3 Nodular lymphocyte predominant Hodgkin lymphoma
Hodgkin lymphoma, lymphocyte predominance, nodularHodgkin paragranuloma, NOSHodgkin paragranuloma, nodularM9661/3 Hodgkin granuloma
M9662/3 Hodgkin sarcoma
M9663/3 Nodular sclerosis classical Hodgkin lymphoma
Hodgkin lymphoma, nodular sclerosis, NOSM9664/3 Hodgkin lymphoma, nodular sclerosis, cellular phase
Classical Hodgkin lymphoma, nodular sclerosis, cellular phaseM9665/3 Hodgkin lymphoma, nodular sclerosis, grade 1
Classical Hodgkin lymphoma, nodular sclerosis grade 1Hodgkin disease, nodular sclerosis, lymphocyte predominanceHodgkin disease, nodular sclerosis, mixed cellularityM9667/3 Hodgkin lymphoma, nodular sclerosis, grade 2
Classical Hodgkin lymphoma, nodular sclerosis, grade 2Hodgkin disease, nodular sclerosis, lymphocyte depletionHodgkin disease, nodular sclerosis, syncytial variantM9670/3 Malignant lymphoma, small B lymphocytic, NOS (see also M9823/3)
Small lymphocytic lymphomaMalignant lymphoma, small lymphocytic, NOSMalignant lymphoma, lymphocytic, well differentiated, diffuseMalignant lymphoma, lymphocytic, NOSMalignant lymphoma, lymphocytic, diffuse, NOSMalignant lymphoma, small cell, NOSMalignant lymphoma, small lymphocytic, diffuseMalignant lymphoma, small cell diffuseM9671/3 Malignant lymphoma, lymphoplasmacytic (see also M9761/3)
Lymphoplasmacytic lymphomaMalignant lymphoma, lymphoplasmacytoidImmunocytomaMalignant lymphoma, plasmacytoidPlasmacytic lymphomaM9673/3 Mantle cell lymphoma
Includes all variants: blastic, pleomorphic, small cellMantle zone lymphomaMalignant zone lymphomaMalignant lymphoma, lymphocytic, intermediate differentiation, diffuseMalignant lymphoma, centrocyticMalignant lymphomatous polyposisM9675/3 Malignant lymphoma, mixed small and large cell, diffuse (see also M9690/3)
Malignant lymphoma, mixed lymphocytic-histiocytic, diffuseMalignant lymphoma, mixed cell type, diffuseMalignant lymphoma, centroblastic-centrocytic,NOSMalignant lymphoma, centroblastic-centrocytic, diffuseM9678/3 Primary effusion lymphoma
M9679/3 Mediastinal large B-cell lymphoma (C38.3)
Mediastinal (thymic) large cell lymphomaM9680/3 Malignant lymphoma, large B-cell, diffuse, NOS
Diffuse large B-cell lymphoma, NOSMalignant lymphoma, large cell, NOSMalignant lymphoma, large B-cell, NOSMalignant lymphoma, histiocytic, NOSMalignant lymphoma, histiocytic, diffuseMalignant lymphoma, large cell, cleaved and noncleavedMalignant lymphoma, large cell, diffuse, NOSMalignant lymphoma, large cleaved cell, NOSMalignant lymphoma, large cell, cleaved, NOSMalignant lymphoma, large cell, noncleaved, diffuse or NOSMalignant lymphoma, large B-cell, diffuse, centroblastic, NOSMalignant lymphoma, large B-cell, centroblastic, NOS or diffuseIntravascular large B-cell lymphomaAngioendotheliomatosisAngiotropic lymphomaT-cell rich large B-cell lymphomaHistiocyte-rich large B-cell lymphomaAnaplastic large B-cell lymphomaM9684/3 Malignant lymphoma, large B-cell, diffuse, immunoblastic, NOS
Malignant lymphoma, immunoblastic, NOSImmunoblastic sarcomaMalignant lymphoma, large cell, immunoblasticPlasmablastic lymphomaM9687/3 Burkitt lymphoma, NOS (see also M9826/3)
Includes all variantsMalignant lymphoma, undifferentiatedMalignant lymphoma, small noncleavedBurkitt-like lymphomaM9689/3 Splenic marginal zone lymphoma
Splenic marginal zone B-cell lymphomaSplenic lymphoma with villous lymphocytesM9690/3 Follicular lymphoma, NOS (see also M9675/3)
Malignant lymphoma, follicular/follicle center, NOSM9691/3 Follicular lymphoma, grade 2
Follicular lymphoma, small cleaved cellM9698/3 Follicular lymphoma, grade 3
Malignant lymphoma, large cell/centroblastic, follicular, NOSM9699/3 Marginal zone B-cell lymphoma, NOS
Marginal zone lymphoma, NOSExtranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue (MALT-lymphoma)BALT lymphomaSALT lymphomaMonocytoid b-cell lymphomaNodal marginal zone lymphomaNodal marginal zone B-cell lymphoma970–971 Mature T- and NK-cell Lymphomas
M9700/3 Mycosis fungoides
Pagetoid reticulosisM9701/3 Sezary syndrome
Sezary diseaseM9702/3 Mature T-cell lymphoma, NOS
Peripheral T-cell lymphoma, NOST-cell lymphoma, NOSPeripheral T-cell lymphoma, pleomorphic small/medium/large cell/T-zone lymphomaLymphoepithelioid lymphomaLennert lymphomaM9705/3 Angioimmunoblastic T-cell lymphoma
Peripheral T-cell lymphoma, AILD (Angioimmunoblastic lymphadenopathy with dysproteinemia)M9708/3 Subcutaneous panniculitis-like T-cell lymphoma
M9709/3 Cutaneous T-cell lymphoma, NOS (C44._)
Cutaneous lymphoma, NOSM9714/3 Anaplastic large cell lymphoma, T cell and Null cell type
Anaplastic large cell lymphoma, CD30+/NOSM9716/3 Hepatosplenic (gamma-delta) cell lymphoma
Hepatosplenic T-cell lymphomaM9717/3 Intestinal T-cell lymphoma
Enteropathy type T-cell lymphomaM9718/3 Primary cutaneous CD 30+ T-cell lymphoproliferative disorder (C44._)
Lymphomatoid papulosisPrimary cutaneous anaplastic large cell lymphomaPrimary cutaneous CD30+ large T-cell lymphomaM9719/3 NK/T-cell lymphoma, nasal and nasal type
Extranodal NK/T cell lymphoma, nasal typeT/NK-cell lymphomaM9727/3 Precursor cell lymphoblastic lymphoma, NOS (see also M9835/3)
Blastic NK cell lymphomaMalignant lymphoma, lymphoblastic, NOSM9728/3 Precursor B-cell lymphoblastic Lymphoma (see also M9836/3)
M9729/3 Precursor T-cell lymphoblastic Lymphoma (see also M9837/3)
M9731/3 Plasmacytoma, NOS
Extramedullary plasmacytomaSolitary plasmacytoma of bone (C40._, C41._)Solitary myelomaSolitary plasmacytomaM9732/3 Multiple myeloma (C42.1)
Plasma cell myelomaMyeloma, NOSMyelomatosisM9733/3 Plasma cell leukemia (C42.1)
Plasmacytic leukemiaM9734/3 Plasmacytoma, extramedullary (not occurring in bone)
Extraosseous plasmacytomaM9740/1 Mastocytoma, NOS or Extracutaneous mastocytoma
Mast cell tumor, NOSM9740/3 Mast cell sarcoma
Malignant mast cell tumorMalignant mastocytomaM9741/3 Malignant mastocytosis
Systemic tissue mast cell diseaseAggressive systemic mastocytosis or Systemic mastocytosis with associated clonal, hematological non-mast cell lineage diseaseM9742/3 Mast cell leukemia (C42.1)
975 Neoplasms of Histiocytes and Accessory Lymphoid Cells
M9750/3 Malignant histiocytosis
M9751/1 Langerhans cell histiocytosis, NOS
M9752/1 Langerhans cell histiocytosis, unifocal
Langerhans cell granulomatosis, unifocalLangerhans cell histiocytosis, mono-ostoticEosinophilic granulomaM9753/1 Langerhans cell histiocytosis, multifocal
Langerhans cell histiocytosis, poly-ostoticM9754/3 Langerhans cell histiocytosis, disseminated
Langerhans cell histiocytosis, generalizedLetterer-Siwe diseaseAcute progressive histiocytosis XM9755/3 Histiocytic sarcoma
True histiocytic lymphomaM9756/3 Langerhans cell sarcoma
M9757/3 Dendritic cell sarcoma, NOS
Interdigitating dendritic cell sarcoma/tumorM9758/3 Follicular dendritic cell sarcoma/tumor
M9760/3 Immunoproliferative disease, NOS
M9761/3 Waldenstrom macroglobulinemia (C42.0) (see also M9671/3)
M9762/3 Heavy chain disease, NOS
Alpha heavy chain diseaseMu heavy chain diseaseGamma heavy chain diseaseFranklin diseaseM9764/3 Immunoproliferative small intestinal disease (C17._)
Mediterranean lymphomaM9765/1 Monoclonal gammopathy of undetermined significance
MGUSMonoclonal gammopathy, NOS(M9766/1) Angiocentric immunoproliferative lesion
LYmphoid granulomatosisLymphomatoid granulomatosisM9767/1 Angioimmunoblastic lymphadenopathy
M9768/1 T-gamma lymphoproliferative disease
M9769/1 Immunoglobulin deposition disease
Systemic light chain diseasePrimary amyloidosisM9800/3 Leukemia, NOS
M9801/3 Acute leukemia, NOS
Blast cell leukemiaUndifferentiated leukemiaStem cell leukemiaM9805/3 Acute biphenotypic leukemia
Acute leukemia of ambiguous lineageAcute mixed lineage leukemiaAcute bilineal leukemiaM9820/3 Lymphoid leukemia, NOS
Lymphocytic leukemia, NOSLymphatic leukemia, NOSM9823/3 B-cell chronic lymphocytic leukemia/small lymphocytic lymphoma (see also M9670/3)
Chronic lymphocytic leukemia, B-cell type (includes all variants of BCLL)Chronic lymphocytic leukemiaChronic lymphoid leukemiaChronic lymphatic leukemiaM9826/3 Burkitt cell Leukemia (see also M9687/3)
Acute lymphoblastic leukemia, mature B-cell typeM9827/3 Adult T-cell leukemia/lymphoma (HTLV-1 positive) includes all variants
Adult T-cell lymphoma/leukemiaM9831/1 T-cell large granular lymphocytic leukemia
T-cell large granular lymphocytosisNK-cell large granular lymphocytic leukemiaLarge granular lymphocytosis, NOSM9832/3 Prolymphocytic leukemia, NOS
M9833/3 B-cell prolymphocytic leukemia
M9834/3 T-cell prolymphocytic leukemia
M9835/3 Precursor cell lymphoblastic leukemia, NOS (see also M9727/3)
Precursor cell lymphoblastic leukemia, not phenotypedAcute lymphoblastic leukemia, NOS (see also M9727/3)Acute lymphoblastic leukemia, precursor-cell typeAcute lymphoblastic leukemia-lymphoma, NOSAcute lymphocytic leukemiaAcute lymphoid leukemiaAcute lymphatic leukemiaAcute lymphoblastic leukemia, L2 type, NOSFAB L2M9836/3 Precursor B lymphoblastic leukemia (see also M9728/3)
Pro-B ALLCommon precursor B ALLPre-B ALLPre-pre-B ALLCommon ALLc-ALLM9837/3 Precursor T lymphoblastic leukemia (see also M9729/3)
Pro-T ALLPre-T ALLCortical T ALLMature T ALL(9840–9849) Erythroleukemias (FAB-M6)
M9840/3 Acute myeloid leukemia, M6 type
Acute erythroid leukemiaErythroleukemiaFAB M6AML M6Erythremic myelosis, NOS(9850–9859) Lymphosarcoma cell leukemia (9860–9869) Myeloid (Granulocytic) Leukemias
M9860/3 Myeloid leukemia, NOS
Non-lymphocytic leukemia, NOSGranulocytic leukemia, NOSMyelogenous leukemia, NOSMyelomonocytic leukemia, NOSMyelocytic leukemia, NOSEosinophilic leukemiaMonocytic leukemia, NOSM9861/3 Acute myeloid leukemia, NOS (FAB or WHO type not specified (see also M9930/3)
Acute myelogenous leukemiaAcute non-lymphocytic leukemiaAcute granulocytic leukemiaAcute myelogenous leukemiaAcute myelocytic leukemiaM9863/3 Chronic myeloid leukemia, NOS
Chronic myelogenous leukemia, NOSChronic granulocytic leukemia, NOSChronic myelocytic leukemia, NOSM9866/3 Acute promyelocytic leukemia t(15;17)(q22;q11-12) * Acute promyelocytic leukemia, PML/RAR-alpha
Acute myeloid leukemia, t(15:17(q22;q11-12)Acute promyelocytic leukemia, NOSFAB-M3 (includes all variants)
Acute promyelocytic leukemia (AML with t(15;17)(q22;q12), PML-RARa and variants)M9867/3) Acute myelomonocytic leukemia
Acute myelomonocytic leukemiaFAB-M4M9870/3 Basophilic leukemia or Acute basophilic leukemia
M9871/3 Acute myeloid leukemia with abnormal marrow eosinophils (includes all variants)
AML with inv(16)(p13q22) or t(16;16)(p13;q22), CBFb/MYH11 (FAB M4Eo)M9872/3 Acute myeloid leukemia, minimally differentiated (FAB type M0)
Acute myeloblastic leukemia]M9873/3 Acute myeloid leukemia, without maturation (FAB type M1)
M9874/3 Acute myeloid leukemia, with maturation (FAB M2), NOS
M9875/3 Chronic myelogenous leukemia BCR/ABL positive
Philadelphia chromosome (Ph1 positive)t(9;22)(q34;q11)Chronic granulocytic leukemia (BCR/ABL positive)/(Ph1 positive)/t(9;22)(q34;q11)M9876/3 Atypical chronic myelogenous leukemia BCR/ABL negative
Atypical chronic myeloid leukemia (BCR/ABL negative)/(Ph1 negative)M9891/3 Acute monoblastic and monocytic leukemia
Monoblastic leukemia, NOSFAB M5 (includes all variants)M9895/3 Acute myeloid leukemia multilineage dysplasia
AML with/without prior myelodysplastic syndromeM9896/3 AML with t(8;21)(q22;q22), AML1/ETO
FAB M2 with t(8;21)(q22;q22), AML1/ETOM9897/3 AML with 11q23 (MLL) abnormalities
AML, MLLM9910/3 Acute megakaryoblastic leukemia, NOS
Megakaryocytic leukemia(FAB-M7)M9920/3 Acute myeloid leukemia and myelodysplastic syndrome, therapy related, NOS Therapy-related acute myeloid leukemia, alkylating agent/epipodophyllotoxin related
M9930/3 Chloroma or Myeloid sarcoma (see also M9861/3)
Granulocytic sarcomaM9931/3) Acute panmyelosis with myelofibrosis (C42.1)
Acute panmyelosis, NOSAcute myelofibrosisAcute myelosclerosis, NOSM9940/3 Hairy cell leukemia (C42.1)
Hairy cell leukemia variantLeukemic reticuloendotheliosisM9945/3 Chronic myelomonocytic, leukemia, NOS
Type 1Type 2M9946/3 Juvenile myelomonocytic leukemia
M9948/3 Aggressive NK cell leukemia
M9950/3 Polycythemia vera
Polycythemia rubra veraProliferative polycythemiaM9960/1 Chronic Myeloproliferative disease, NOS
M9961/3 Myelosclerosis with myeloid metaplasia
Chronic idiopathic myelofibrosisMyelofibrosis as a result of myeloproliferative diseaseAgnogenic myeloid metaplasiaMegakaryocytic myelosclerosisMyelofibrosis with myeloid metaplasiaM9962/3 Essential thrombocytemia
Idiopathic thrombocythemiaEssential/idiopathic hemorrhagic thrombocythemiaM9963/3 Chronic neutrophilic leukemia
M9964/3 Chronic eosinophilic leukemia / hypereosinophilic syndrome
M9970/1 Lymphoproliferative disease/disorder, NOS
Post-transplant lymphoproliferative disorder, pleomorphicM9775/1 Myeloproliferative disease, NOS
Chronic Myeloproliferative disease, unclassifiableMyelodysplastic / myeloproliferative diseases, unclassifiableM9980/3 Chronic myelomonocytic leukemia or Refractory anemia
M9982/3 Refractory anemia with ringed sideroblasts
with sideroblastsM9983/3 Refractory anemia with excess blasts
RAEBRAEB IRAEB IIM9985/3 Refractory cytopenia with multilineage dysplasia
M9986/3 Myelodysplastic syndrome associated with isolated del(5q) chromosome abnormality
M9989/3 Myelodysplastic syndrome, NOS