EC number 1.3.8.8 IntEnz IntEnz view ExPASy NiceZyme view | CAS number 59536-74-2 BRENDA BRENDA entry KEGG KEGG entry | |
Long-chain acyl-CoA dehydrogenase (EC 1.3.8.8, palmitoyl-CoA dehydrogenase, palmitoyl-coenzyme A dehydrogenase, long-chain acyl-coenzyme A dehydrogenase, long-chain-acyl-CoA:(acceptor) 2,3-oxidoreductase, ACADL (gene).) is an enzyme with systematic name long-chain acyl-CoA:electron-transfer flavoprotein 2,3-oxidoreductase. This enzyme catalyses the following chemical reaction
a long-chain acyl-CoA + electron-transfer flavoproteinThis enzyme contains FAD as prosthetic group and participates in fatty acid metabolism and PPAR signaling pathway. Mitochondrial mutations in this enzyme may be associated with some forms of dilated cardiomyopathy.
References
Long-chain acyl-CoA dehydrogenase Wikipedia(Text) CC BY-SA