Specialty endocrinology ICD-9-CM 277.3 DiseasesDB 33335 | ICD-10 E85.0 OMIM 105200 eMedicine med/3379 | |
Familial renal amyloidosis (or familial visceral amyloidosis, or hereditary amyloid nephropathy) is a form of amyloidosis primarily presenting in the kidney.
It is associated with fibrinogen alpha chain, apolipoprotein A1, and lysozyme.
It is also known as "Ostertag" type, after B. Ostertag, who characterized it in 1932 and 1950.
References
Familial renal amyloidosis Wikipedia(Text) CC BY-SA