| ACAA1, ACAA, PTHIO, THIO, acetyl-CoA acyltransferase 1|
MGI: 2148491 HomoloGene: 37497 GeneCards: ACAA1
3-Ketoacyl-CoA thiolase, peroxisomal also known as acetyl-Coenzyme A acyltransferase 1 is an enzyme that in humans is encoded by the ACAA1 gene.
Acetyl-Coenzyme A acyltransferase 1 is an acetyl-CoA C-acyltransferase enzyme.
This gene encodes an enzyme operative in the beta oxidation system of the peroxisomes.
Deficiency of this enzyme leads to pseudo-Zellweger syndrome.