The International Statistical Classification of Diseases and Related Health Problems 10th Revision (ICD-10) is a coding of diseases and signs, symptoms, abnormal findings, complaints, social circumstances and external causes of injury or diseases, as classified by the World Health Organization (WHO). This page contains ICD-10 Chapter III: Diseases of the blood and blood-forming organs, and certain disorders involving the immune mechanism.
(D50) Iron deficiency anaemia
(D50.0) Iron deficiency anaemia secondary to blood loss (chronic)
(D50.1) Sideropenic dysphagia
Kelly-Paterson syndrome
Plummer-Vinson syndrome
(D50.8) Other iron deficiency anaemias
(D50.9) Iron deficiency anaemia, unspecified
(D51) Vitamin B12 deficiency anaemia
(D51.0) Vitamin B12 deficiency anaemia due to intrinsic factor deficiency
Pernicious anemia
(D51.1) Vitamin B 12 deficiency anaemia due to selective vitamin B 12 malabsorption with proteinuria
Megaloblastic hereditary anaemia
(D51.2) Transcobalamin II deficiency
(D51.3) Other dietary vitamin B 12 deficiency anaemia
(D51.8) Other vitamin B 12 deficiency anaemias
(D51.9) Vitamin B 12 deficiency anaemia, unspecified
(D52) Folate deficiency anaemia
(D52.0) Dietary folate deficiency anaemia
Nutritional megaloblastic anaemia
(D52.1) Drug-induced folate deficiency anaemia
(D52.8) Other folate deficiency anaemias
(D52.9) Folate deficiency anaemia, unspecified
(D53) Other nutritional anaemias
(D53.0) Protein deficiency anaemia
(D53.1) Other megaloblastic anaemias, not elsewhere classified
(D53.2) Scorbutic anaemia
(D53.8) Other specified nutritional anaemias
(D53.9) Nutritional anaemia, unspecified
(D55) Anaemia due to enzyme disorders
(D55.0) Anaemia due to glucose-6-phosphate dehydrogenase (G6PD) deficiency
Favism
G6PD deficiency anaemia
(D55.1) Anaemia due to other disorders of glutathione metabolism
(D55.2) Anaemia due to disorders of glycolytic enzymes
hexokinase deficiency
pyruvate kinase deficiency
triose-phosphate isomerase deficiency
(D55.3) Anaemia due to disorders of nucleotide metabolism
(D55.8) Other anaemias due to enzyme disorders
(D55.9) Anaemia due to enzyme disorder, unspecified
(D56) Thalassaemia
(D56.0) Alpha thalassaemia
(D56.1) Beta thalassaemia
(D56.2) Delta-beta thalassaemia
(D56.3) Thalassaemia trait
(D56.4) Hereditary persistence of fetal haemoglobin (HPFH)
(D56.8) Other thalassaemias
(D56.9) Thalassaemia, unspecified
(D57) Sickle-cell disorders
(D57.0) Sickle-cell anaemia with crisis
(D57.1) Sickle-cell anaemia without crisis
(D57.2) Double heterozygous sickling disorders
(D57.3) Sickle-cell trait
(D57.8) Other sickle-cell disorders
(D58) Other hereditary haemolytic anaemias
(D58.0) Hereditary spherocytosis
Acholuric (familial) jaundice
Congenital (spherocytic) haemolytic icterus
Minkowski-Chauffard syndrome
(D58.1) Hereditary elliptocytosis
Elliptocytosis (congenital)
Ovalocytosis (congenital) (hereditary)
(D58.2) Other haemoglobinopathies
Abnormal haemoglobin NOS
Congenital Heinz body anaemia
Haemoglobinopathy NOS
Unstable haemoglobin haemolytic disease
(D58.8) Other specified hereditary haemolytic anaemias
Stomatocytosis
(D59) Acquired haemolytic anaemia
(D59.0) Drug-induced autoimmune haemolytic anaemia
(D59.1) Other autoimmune haemolytic anaemias
Warm autoimmune hemolytic anemia
(D59.2) Drug-induce nonautoimmune haemolytic anaemia
(D59.3) Haemolytic-uraemic syndrome
(D59.4) Other nonautoimmune haemolytic anaemias
Microangiopathic hemolytic anemia
(D59.5) Paroxysmal nocturnal haemoglobinuria (Marchiafava-Micheli)
(D59.6) Haemoglobinuria due to haemolysis from other external causes
paroxysmal cold haemoglobinuria
(D59.8) Other acquired haemolytic anaemias
(D59.9) Acquired haemolytic anaemia, unspecified
(D60–D64) Aplastic and other anaemias
(D60) Acquired pure red cell aplasia (erythroblastopenia)
(D61) Other aplastic anaemias
(D61.0) Constitutional aplastic anaemia
Blackfan-Diamond syndrome
Familial hypoplastic anaemia
Fanconi's anaemia
Pancytopenia with malformations
(D61.1) Drug-induced aplastic anaemia
(D61.2) Aplastic anaemia due to other external agents
(D61.3) Idiopathic aplastic anaemia
(D61.8) Other specified aplastic anaemias
(D61.9) Aplastic anaemia, unspecified
Hypoplastic anaemia NOS
Medullary hypoplasia
Panmyelophthisis
(D62) Acute posthaemorrhagic anaemia
(D63) Anaemia in chronic diseases classified elsewhere
(D64) Other anaemias
(D64.0) Hereditary sideroblastic anaemia
(D64.1) Secondary sideroblastic anaemia due to disease
(D64.2) Secondary sideroblastic anaemia due to drugs and toxins
(D64.3) Other sideroblastic anaemias
(D64.4) Congenital dyserythropoietic anaemia
(D64.8) Other specified anaemias
(D64.9) Anaemia, unspecified
(D65–D69) Coagulation defects, purpura and other haemorrhagic conditions
(D65) Disseminated intravascular coagulation (defibrination syndrome)
Afibrinogenaemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation (DIC)
Fibrinolytic haemorrhage, acquired
Fibrinolytic purpura
Purpura fulminans
(D66) Hereditary factor VIII deficiency
Haemophilia A
(D67) Hereditary factor IX deficiency
Christmas disease
Haemophilia B
(D68) Other coagulation defects
(D68.0) Von Willebrand's disease
(D68.1) Hereditary factor XI deficiency
Haemophilia C
(D68.2) Hereditary deficiency of other clotting factors
(D68.3) Haemorrhagic disorder due to circulating anticoagulants
(D68.4) Acquired coagulation factor deficiency
(D68.8) Other specified coagulation defects
(D68.9) Coagulation defect, unspecified
(D69) Purpura and other haemorrhagic conditions
(D69.0) Allergic purpura
anaphylactoid purpura
Henoch-Schönlein purpura
(D69.1) Qualitative platelet defects
Bernard-Soulier syndrome (giant platelet)
Glanzmann's disease
Grey platelet syndrome
Thromboasthenia (haemorrhagic)(hereditary)
Thrombocytopathy
(D69.2) Other nonthrombocytopenic purpura
(D69.3) Idiopathic thrombocytopenic purpura
Evans' syndrome
(D69.4) Other primary thrombocytopenia
(D69.5) Secondary thrombocytopenia
(D69.6) Thrombocytopenia, unspecified
(D69.8) Other specified haemorrhagic conditions
(D69.9) Haemorrhagic condition, unspecified
(D70) Agranulocytosis
Agranulocytic angina
Infantile genetic agranulocytosis
Kostmann's disease
Neutropenia, NOS
(D71) Functional disorders of polymorphonuclear neutrophils
Cell membrane receptor complex (CR3) defect
Chronic (childhood) granulomatous disease
Congenital dysphagocytosis
Progressive septic granulomatosis
(D72) Other disorders of white blood cells
(D72.0) Genetic anomalies of leukocytes
Alder anomaly
May-Hegglin anomaly
Pelger-Huët anomaly
(D72.1) Eosinophilia
(D72.8) Other specified disorders of white blood cells
Leukaemoid reaction: lymphocytic, monocytic, myelocytic
Leukocytosis
Lymphocytosis (symptomatic)
Lymphopenia
Monocytosis (symptomatic)
Plasmacytosis
(D72.9) Disorder of white blood cells, unspecified
(D73) Diseases of spleen
(D73.0) Hyposplenism
(D73.1) Hypersplenism
(D73.2) Chronic congestive splenomegaly
(D73.3) Abscess of spleen
(D73.4) Cyst of spleen
(D73.5) Infarction of spleen
(D73.8) Other diseases of spleen
(D73.9) Disease of spleen, unspecified
(D74) Methaemoglobinaemia
(D74.0) Congenital methaemoglobinaemia
Congenital NADH-methaemoglobin reductase deficiency
Haemoglobin-M (Hb-M) disease
Methaemoglobinaemia, hereditary
(D74.8) Other methaemoglobinaemias
Acquired methaemoglobinaemia (with sulfhaemoglobinaemia)
Toxic methaemoglobinaemia
(D74.9) Methaemoglobinaemia, unspecified
(D75) Other diseases of blood and blood-forming organs
(D75.0) Familial erythrocytosis
(D75.1) Secondary polycythaemia
(D75.2) Essential thrombocytosis
(D75.8) Other specified diseases of blood and blood-forming organs
Basophilia
(D75.9) Disease of blood and blood-forming organs, unspecified
(D76) Certain diseases involving lymphoreticular tissue and reticulohistiocytic system
(D76.0) Langerhans' cell histiocytosis, not elsewhere classified
Eosinophilic granuloma
Hand-Schüller-Christian disease
Histiocytosis X (chronic)
(D76.1) Haemophagocytic lymphohistiocytosis
Familial haemophagocytic reticulosis
(D76.2) Haemophagocytic syndrome, infection-associated
(D76.3) Other histiocytosis syndromes
Reticulohistiocytoma (giant-cell)
Sinus histiocytosis with massive lymphadenopathy
Xanthogranuloma
(D77) Other disorders of blood and blood-forming organs in diseases classified elsewhere
(D80) Immunodeficiency with predominantly antibody defects
(D80.0) Hereditary hypogammaglobulinaemia
Autosomal recessive agammaglobulinaemia (Swiss type)
X-linked agammaglobulinaemia (Bruton) (with growth hormone deficiency)
(D80.1) Nonfamilial hypogammaglobulinaemia
Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
Common variable agammaglobulinaemia (CVAgamma)
Hypogammaglobulinaemia NOS
(D80.2) Selective deficiency of immunoglobulin A (IgA)
(D80.3) Selective deficiency of immunoglobulin G (IgG) subclasses
(D80.4) Selective deficiency of immunoglobulin M (IgM)
(D80.5) Immunodeficiency with increased immunoglobulin M (IgM)
(D80.6) Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia
(D80.7) Transient hypogammaglobulinaemia of infancy
(D80.8) Other immunodeficiencies with predominantly antibody defects
Kappa light chain deficiency
(D80.9) Immunodeficiency with predominantly antibody defects, unspecified
(D81) Combined immunodeficiencies
(D81.0) Severe combined immunodeficiency (SCID) with reticular dysgenesis
(D81.1) Severe combined immunodeficiency (SCID) with low T-cell and B-cell numbers
(D81.2) Severe combined immunodeficiency (SCID) with low or normal B-cell numbers
(D81.3) Adenosine deaminase deficiency (ADA)
(D81.4) Nezelof's syndrome
(D81.5) Purine nucleoside phosphorylase deficiency (PNP)
(D81.6) Major histocompatibility complex class I deficiency
Bare lymphocyte syndrome
(D81.7) Major histocompatibility complex class II deficiency
(D81.8) Other combined immunodeficiencies
Biotin-dependent carboxylase deficiency
(D81.9) Combined immunodeficiency, unspecified
Severe combined immunodeficiency disorder (SCID) NOS
(D82) Immunodeficiency associated with other major defects
(D82.0) Wiskott-Aldrich syndrome
Immunodeficiency with thrombocytopenia and eczema
(D82.1) Di George's syndrome
(D82.2) Immunodeficiency with short-limbed stature
(D82.3) Immunodeficiency following hereditary defective response to Epstein-Barr virus
X-linked lymphoproliferative disease
(D82.4) Hyperimmunoglobulin E syndrome (IgE)
(D83) Common variable immunodeficiency
(D84) Other immunodeficiencies
(D84.0) Lymphocyte function antigen-1 (LFA-1) defect
(D84.1) Defects in the complement system
C1 esterase inhibitor deficiency (C1-INH)
(D84.8) Other specified immunodeficiencies
(D84.9) Immunodeficiency, unspecified
(D86) Sarcoidosis
(D86.0) Sarcoidosis of lung
(D86.1) Sarcoidosis of lymph nodes
(D86.2) Sarcoidosis of lung with sarcoidosis of lymph nodes
(D86.3) Sarcoidosis of skin
(D86.8) Sarcoidosis of other and combined sites
(D89) Other disorders involving the immune mechanism, not elsewhere classified
(D89.0) Polyclonal hypergammaglobulinaemia
Benign hypergammaglobulinaemic purpura
Polyclonal gammopathy NOS
(D89.1) Cryoglobulinaemia
(D89.2) Hypergammaglobulinaemia, unspecified
(D89.8) Other specified disorders involving the immune mechanism, not elsewhere classified
(D89.9) Disorder involving the immune mechanism, unspecified
Autoimmune disease (systemic) NOS (M35.9)
Certain conditions originating in the perinatal period (P00-P96)
Complications of pregnancy, childbirth and the puerperium (O00-O9A)
Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
Endocrine, nutritional, and metabolic diseases (E00-E88)
Human immunodeficiency virus [HIV] disease (B20)
Injury, poisoning and certain other consequences of external causes (S00-T88)
Neoplasms (C00-D49)
Symptoms, signs, and abnormal clinical and laboratory findings, NEC (R00-R94)
ICD-10 Chapter III: Diseases of the blood and blood-forming organs, and certain disorders involving the immune mechanism Wikipedia (Text) CC BY-SA