Kalpana Kalpana (Editor)

ICD 10 Chapter III: Diseases of the blood and blood forming organs, and certain disorders involving the immune mechanism

Updated on
Edit
Like
Comment
Share on FacebookTweet on TwitterShare on LinkedInShare on Reddit

The International Statistical Classification of Diseases and Related Health Problems 10th Revision (ICD-10) is a coding of diseases and signs, symptoms, abnormal findings, complaints, social circumstances and external causes of injury or diseases, as classified by the World Health Organization (WHO). This page contains ICD-10 Chapter III: Diseases of the blood and blood-forming organs, and certain disorders involving the immune mechanism.

Contents

(D50–D53) Nutritional anemias

  • (D50) Iron deficiency anaemia
  • (D50.0) Iron deficiency anaemia secondary to blood loss (chronic)
  • (D50.1) Sideropenic dysphagia
  • Kelly-Paterson syndrome
  • Plummer-Vinson syndrome
  • (D50.8) Other iron deficiency anaemias
  • (D50.9) Iron deficiency anaemia, unspecified
  • (D51) Vitamin B12 deficiency anaemia
  • (D51.0) Vitamin B12 deficiency anaemia due to intrinsic factor deficiency
  • Pernicious anemia
  • (D51.1) Vitamin B 12 deficiency anaemia due to selective vitamin B 12 malabsorption with proteinuria
  • Megaloblastic hereditary anaemia
  • (D51.2) Transcobalamin II deficiency
  • (D51.3) Other dietary vitamin B 12 deficiency anaemia
  • (D51.8) Other vitamin B 12 deficiency anaemias
  • (D51.9) Vitamin B 12 deficiency anaemia, unspecified
  • (D52) Folate deficiency anaemia
  • (D52.0) Dietary folate deficiency anaemia
  • Nutritional megaloblastic anaemia
  • (D52.1) Drug-induced folate deficiency anaemia
  • (D52.8) Other folate deficiency anaemias
  • (D52.9) Folate deficiency anaemia, unspecified
  • (D53) Other nutritional anaemias
  • (D53.0) Protein deficiency anaemia
  • (D53.1) Other megaloblastic anaemias, not elsewhere classified
  • (D53.2) Scorbutic anaemia
  • (D53.8) Other specified nutritional anaemias
  • (D53.9) Nutritional anaemia, unspecified
  • (D55–D59) Haemolytic anaemias

  • (D55) Anaemia due to enzyme disorders
  • (D55.0) Anaemia due to glucose-6-phosphate dehydrogenase (G6PD) deficiency
  • Favism
  • G6PD deficiency anaemia
  • (D55.1) Anaemia due to other disorders of glutathione metabolism
  • (D55.2) Anaemia due to disorders of glycolytic enzymes
  • hexokinase deficiency
  • pyruvate kinase deficiency
  • triose-phosphate isomerase deficiency
  • (D55.3) Anaemia due to disorders of nucleotide metabolism
  • (D55.8) Other anaemias due to enzyme disorders
  • (D55.9) Anaemia due to enzyme disorder, unspecified
  • (D56) Thalassaemia
  • (D56.0) Alpha thalassaemia
  • (D56.1) Beta thalassaemia
  • (D56.2) Delta-beta thalassaemia
  • (D56.3) Thalassaemia trait
  • (D56.4) Hereditary persistence of fetal haemoglobin (HPFH)
  • (D56.8) Other thalassaemias
  • (D56.9) Thalassaemia, unspecified
  • (D57) Sickle-cell disorders
  • (D57.0) Sickle-cell anaemia with crisis
  • (D57.1) Sickle-cell anaemia without crisis
  • (D57.2) Double heterozygous sickling disorders
  • (D57.3) Sickle-cell trait
  • (D57.8) Other sickle-cell disorders
  • (D58) Other hereditary haemolytic anaemias
  • (D58.0) Hereditary spherocytosis
  • Acholuric (familial) jaundice
  • Congenital (spherocytic) haemolytic icterus
  • Minkowski-Chauffard syndrome
  • (D58.1) Hereditary elliptocytosis
  • Elliptocytosis (congenital)
  • Ovalocytosis (congenital) (hereditary)
  • (D58.2) Other haemoglobinopathies
  • Abnormal haemoglobin NOS
  • Congenital Heinz body anaemia
  • Haemoglobinopathy NOS
  • Unstable haemoglobin haemolytic disease
  • (D58.8) Other specified hereditary haemolytic anaemias
  • Stomatocytosis
  • (D59) Acquired haemolytic anaemia
  • (D59.0) Drug-induced autoimmune haemolytic anaemia
  • (D59.1) Other autoimmune haemolytic anaemias
  • Warm autoimmune hemolytic anemia
  • (D59.2) Drug-induce nonautoimmune haemolytic anaemia
  • (D59.3) Haemolytic-uraemic syndrome
  • (D59.4) Other nonautoimmune haemolytic anaemias
  • Microangiopathic hemolytic anemia
  • (D59.5) Paroxysmal nocturnal haemoglobinuria (Marchiafava-Micheli)
  • (D59.6) Haemoglobinuria due to haemolysis from other external causes
  • paroxysmal cold haemoglobinuria
  • (D59.8) Other acquired haemolytic anaemias
  • (D59.9) Acquired haemolytic anaemia, unspecified
  • (D60–D64) Aplastic and other anaemias

  • (D60) Acquired pure red cell aplasia (erythroblastopenia)
  • (D61) Other aplastic anaemias
  • (D61.0) Constitutional aplastic anaemia
  • Blackfan-Diamond syndrome
  • Familial hypoplastic anaemia
  • Fanconi's anaemia
  • Pancytopenia with malformations
  • (D61.1) Drug-induced aplastic anaemia
  • (D61.2) Aplastic anaemia due to other external agents
  • (D61.3) Idiopathic aplastic anaemia
  • (D61.8) Other specified aplastic anaemias
  • (D61.9) Aplastic anaemia, unspecified
  • Hypoplastic anaemia NOS
  • Medullary hypoplasia
  • Panmyelophthisis
  • (D62) Acute posthaemorrhagic anaemia
  • (D63) Anaemia in chronic diseases classified elsewhere
  • (D64) Other anaemias
  • (D64.0) Hereditary sideroblastic anaemia
  • (D64.1) Secondary sideroblastic anaemia due to disease
  • (D64.2) Secondary sideroblastic anaemia due to drugs and toxins
  • (D64.3) Other sideroblastic anaemias
  • (D64.4) Congenital dyserythropoietic anaemia
  • (D64.8) Other specified anaemias
  • (D64.9) Anaemia, unspecified
  • (D65–D69) Coagulation defects, purpura and other haemorrhagic conditions

  • (D65) Disseminated intravascular coagulation (defibrination syndrome)
  • Afibrinogenaemia, acquired
  • Consumption coagulopathy
  • Diffuse or disseminated intravascular coagulation (DIC)
  • Fibrinolytic haemorrhage, acquired
  • Fibrinolytic purpura
  • Purpura fulminans
  • (D66) Hereditary factor VIII deficiency
  • Haemophilia A
  • (D67) Hereditary factor IX deficiency
  • Christmas disease
  • Haemophilia B
  • (D68) Other coagulation defects
  • (D68.0) Von Willebrand's disease
  • (D68.1) Hereditary factor XI deficiency
  • Haemophilia C
  • (D68.2) Hereditary deficiency of other clotting factors
  • (D68.3) Haemorrhagic disorder due to circulating anticoagulants
  • (D68.4) Acquired coagulation factor deficiency
  • (D68.8) Other specified coagulation defects
  • (D68.9) Coagulation defect, unspecified
  • (D69) Purpura and other haemorrhagic conditions
  • (D69.0) Allergic purpura
  • anaphylactoid purpura
  • Henoch-Schönlein purpura
  • (D69.1) Qualitative platelet defects
  • Bernard-Soulier syndrome (giant platelet)
  • Glanzmann's disease
  • Grey platelet syndrome
  • Thromboasthenia (haemorrhagic)(hereditary)
  • Thrombocytopathy
  • (D69.2) Other nonthrombocytopenic purpura
  • (D69.3) Idiopathic thrombocytopenic purpura
  • Evans' syndrome
  • (D69.4) Other primary thrombocytopenia
  • (D69.5) Secondary thrombocytopenia
  • (D69.6) Thrombocytopenia, unspecified
  • (D69.8) Other specified haemorrhagic conditions
  • (D69.9) Haemorrhagic condition, unspecified
  • (D70–D77) Other diseases of blood and blood-forming organs

  • (D70) Agranulocytosis
  • Agranulocytic angina
  • Infantile genetic agranulocytosis
  • Kostmann's disease
  • Neutropenia, NOS
  • (D71) Functional disorders of polymorphonuclear neutrophils
  • Cell membrane receptor complex (CR3) defect
  • Chronic (childhood) granulomatous disease
  • Congenital dysphagocytosis
  • Progressive septic granulomatosis
  • (D72) Other disorders of white blood cells
  • (D72.0) Genetic anomalies of leukocytes
  • Alder anomaly
  • May-Hegglin anomaly
  • Pelger-Huët anomaly
  • (D72.1) Eosinophilia
  • (D72.8) Other specified disorders of white blood cells
  • Leukaemoid reaction: lymphocytic, monocytic, myelocytic
  • Leukocytosis
  • Lymphocytosis (symptomatic)
  • Lymphopenia
  • Monocytosis (symptomatic)
  • Plasmacytosis
  • (D72.9) Disorder of white blood cells, unspecified
  • (D73) Diseases of spleen
  • (D73.0) Hyposplenism
  • (D73.1) Hypersplenism
  • (D73.2) Chronic congestive splenomegaly
  • (D73.3) Abscess of spleen
  • (D73.4) Cyst of spleen
  • (D73.5) Infarction of spleen
  • (D73.8) Other diseases of spleen
  • (D73.9) Disease of spleen, unspecified
  • (D74) Methaemoglobinaemia
  • (D74.0) Congenital methaemoglobinaemia
  • Congenital NADH-methaemoglobin reductase deficiency
  • Haemoglobin-M (Hb-M) disease
  • Methaemoglobinaemia, hereditary
  • (D74.8) Other methaemoglobinaemias
  • Acquired methaemoglobinaemia (with sulfhaemoglobinaemia)
  • Toxic methaemoglobinaemia
  • (D74.9) Methaemoglobinaemia, unspecified
  • (D75) Other diseases of blood and blood-forming organs
  • (D75.0) Familial erythrocytosis
  • (D75.1) Secondary polycythaemia
  • (D75.2) Essential thrombocytosis
  • (D75.8) Other specified diseases of blood and blood-forming organs
  • Basophilia
  • (D75.9) Disease of blood and blood-forming organs, unspecified
  • (D76) Certain diseases involving lymphoreticular tissue and reticulohistiocytic system
  • (D76.0) Langerhans' cell histiocytosis, not elsewhere classified
  • Eosinophilic granuloma
  • Hand-Schüller-Christian disease
  • Histiocytosis X (chronic)
  • (D76.1) Haemophagocytic lymphohistiocytosis
  • Familial haemophagocytic reticulosis
  • (D76.2) Haemophagocytic syndrome, infection-associated
  • (D76.3) Other histiocytosis syndromes
  • Reticulohistiocytoma (giant-cell)
  • Sinus histiocytosis with massive lymphadenopathy
  • Xanthogranuloma
  • (D77) Other disorders of blood and blood-forming organs in diseases classified elsewhere
  • (D80–D89) Certain disorders involving the immune mechanism

  • (D80) Immunodeficiency with predominantly antibody defects
  • (D80.0) Hereditary hypogammaglobulinaemia
  • Autosomal recessive agammaglobulinaemia (Swiss type)
  • X-linked agammaglobulinaemia (Bruton) (with growth hormone deficiency)
  • (D80.1) Nonfamilial hypogammaglobulinaemia
  • Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
  • Common variable agammaglobulinaemia (CVAgamma)
  • Hypogammaglobulinaemia NOS
  • (D80.2) Selective deficiency of immunoglobulin A (IgA)
  • (D80.3) Selective deficiency of immunoglobulin G (IgG) subclasses
  • (D80.4) Selective deficiency of immunoglobulin M (IgM)
  • (D80.5) Immunodeficiency with increased immunoglobulin M (IgM)
  • (D80.6) Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia
  • (D80.7) Transient hypogammaglobulinaemia of infancy
  • (D80.8) Other immunodeficiencies with predominantly antibody defects
  • Kappa light chain deficiency
  • (D80.9) Immunodeficiency with predominantly antibody defects, unspecified
  • (D81) Combined immunodeficiencies
  • (D81.0) Severe combined immunodeficiency (SCID) with reticular dysgenesis
  • (D81.1) Severe combined immunodeficiency (SCID) with low T-cell and B-cell numbers
  • (D81.2) Severe combined immunodeficiency (SCID) with low or normal B-cell numbers
  • (D81.3) Adenosine deaminase deficiency (ADA)
  • (D81.4) Nezelof's syndrome
  • (D81.5) Purine nucleoside phosphorylase deficiency (PNP)
  • (D81.6) Major histocompatibility complex class I deficiency
  • Bare lymphocyte syndrome
  • (D81.7) Major histocompatibility complex class II deficiency
  • (D81.8) Other combined immunodeficiencies
  • Biotin-dependent carboxylase deficiency
  • (D81.9) Combined immunodeficiency, unspecified
  • Severe combined immunodeficiency disorder (SCID) NOS
  • (D82) Immunodeficiency associated with other major defects
  • (D82.0) Wiskott-Aldrich syndrome
  • Immunodeficiency with thrombocytopenia and eczema
  • (D82.1) Di George's syndrome
  • (D82.2) Immunodeficiency with short-limbed stature
  • (D82.3) Immunodeficiency following hereditary defective response to Epstein-Barr virus
  • X-linked lymphoproliferative disease
  • (D82.4) Hyperimmunoglobulin E syndrome (IgE)
  • (D83) Common variable immunodeficiency
  • (D84) Other immunodeficiencies
  • (D84.0) Lymphocyte function antigen-1 (LFA-1) defect
  • (D84.1) Defects in the complement system
  • C1 esterase inhibitor deficiency (C1-INH)
  • (D84.8) Other specified immunodeficiencies
  • (D84.9) Immunodeficiency, unspecified
  • (D86) Sarcoidosis
  • (D86.0) Sarcoidosis of lung
  • (D86.1) Sarcoidosis of lymph nodes
  • (D86.2) Sarcoidosis of lung with sarcoidosis of lymph nodes
  • (D86.3) Sarcoidosis of skin
  • (D86.8) Sarcoidosis of other and combined sites
  • (D89) Other disorders involving the immune mechanism, not elsewhere classified
  • (D89.0) Polyclonal hypergammaglobulinaemia
  • Benign hypergammaglobulinaemic purpura
  • Polyclonal gammopathy NOS
  • (D89.1) Cryoglobulinaemia
  • (D89.2) Hypergammaglobulinaemia, unspecified
  • (D89.8) Other specified disorders involving the immune mechanism, not elsewhere classified
  • (D89.9) Disorder involving the immune mechanism, unspecified
  • Excludes

  • Autoimmune disease (systemic) NOS (M35.9)
  • Certain conditions originating in the perinatal period (P00-P96)
  • Complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • Endocrine, nutritional, and metabolic diseases (E00-E88)
  • Human immunodeficiency virus [HIV] disease (B20)
  • Injury, poisoning and certain other consequences of external causes (S00-T88)
  • Neoplasms (C00-D49)
  • Symptoms, signs, and abnormal clinical and laboratory findings, NEC (R00-R94)
  • References

    ICD-10 Chapter III: Diseases of the blood and blood-forming organs, and certain disorders involving the immune mechanism Wikipedia